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Wyszukujesz frazę ""Anemia, Sickle Cell"" wg kryterium: Temat


Tytuł:
World Sickle Cell Day 2022: Progress & prospects.
Autorzy:
Steinberg MH; Department of Medicine, Division of Hematology & Medical Oncology, Center of Excellence for Sickle Cell Disease, Boston University School of Medicine & Boston Medical Center, Boston, MA, USA.
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Źródło:
The Indian journal of medical research [Indian J Med Res] 2022 Jul; Vol. 156 (1), pp. 10-13.
Typ publikacji:
Editorial
MeSH Terms:
Erythrocytes, Abnormal*
Anemia, Sickle Cell*/epidemiology
Anemia, Sickle Cell*/genetics
Anemia, Sickle Cell*/therapy
Humans
Opinia redakcyjna
Tytuł:
Integrating deep learning with microfluidics for biophysical classification of sickle red blood cells adhered to laminin.
Autorzy:
Praljak N; Department of Physics, Case Western Reserve University, Cleveland, Ohio, United States of America.; Department of Physics, Cleveland State University, Cleveland, Ohio, United States of America.
Iram S; Department of Physics, Case Western Reserve University, Cleveland, Ohio, United States of America.
Goreke U; Department of Mechanical and Aerospace Engineering, Case Western Reserve University, Cleveland, Ohio, United States of America.
Singh G; Department of Physics, Case Western Reserve University, Cleveland, Ohio, United States of America.
Hill A; Department of Mechanical and Aerospace Engineering, Case Western Reserve University, Cleveland, Ohio, United States of America.
Gurkan UA; Department of Mechanical and Aerospace Engineering, Case Western Reserve University, Cleveland, Ohio, United States of America.; Department of Biomedical Engineering, Case Western Reserve University, Cleveland, Ohio, United States of America.
Hinczewski M; Department of Physics, Case Western Reserve University, Cleveland, Ohio, United States of America.
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Źródło:
PLoS computational biology [PLoS Comput Biol] 2021 Nov 29; Vol. 17 (11), pp. e1008946. Date of Electronic Publication: 2021 Nov 29 (Print Publication: 2021).
Typ publikacji:
Journal Article; Research Support, N.I.H., Extramural; Research Support, U.S. Gov't, Non-P.H.S.
MeSH Terms:
Deep Learning*
Anemia, Sickle Cell/*blood
Erythrocytes, Abnormal/*classification
Microfluidics/*statistics & numerical data
Anemia, Sickle Cell/diagnostic imaging ; Biophysical Phenomena ; Computational Biology ; Diagnosis, Computer-Assisted/statistics & numerical data ; Erythrocyte Deformability/physiology ; Erythrocytes, Abnormal/pathology ; Erythrocytes, Abnormal/physiology ; Hemoglobin, Sickle/chemistry ; Hemoglobin, Sickle/metabolism ; High-Throughput Screening Assays/statistics & numerical data ; Humans ; Image Interpretation, Computer-Assisted/statistics & numerical data ; In Vitro Techniques ; Lab-On-A-Chip Devices/statistics & numerical data ; Laminin/metabolism ; Neural Networks, Computer ; Protein Multimerization
Czasopismo naukowe
Tytuł:
VZHE-039, a novel antisickling agent that prevents erythrocyte sickling under both hypoxic and anoxic conditions.
Autorzy:
Abdulmalik O; Division of Hematology, The Children's Hospital of Philadelphia, Philadelphia, PA, 19104, USA. .
Pagare PP; Department of Medicinal Chemistry, Virginia Commonwealth University, Richmond, VA, 23298, USA.
Huang B; Department of Medicinal Chemistry, Virginia Commonwealth University, Richmond, VA, 23298, USA.
Xu GG; Department of Medicinal Chemistry, Virginia Commonwealth University, Richmond, VA, 23298, USA.
Ghatge MS; Department of Medicinal Chemistry, Virginia Commonwealth University, Richmond, VA, 23298, USA.; The Institute for Structural Biology, Drug Discovery and Development, School of Pharmacy, Virginia Commonwealth University, Richmond, VA, 23298, USA.
Xu X; Department of Pharmaceutics, Virginia Commonwealth University, Richmond, VA, 23298, USA.
Chen Q; Division of Hematology, The Children's Hospital of Philadelphia, Philadelphia, PA, 19104, USA.
Anabaraonye N; Division of Hematology, The Children's Hospital of Philadelphia, Philadelphia, PA, 19104, USA.
Musayev FN; Department of Medicinal Chemistry, Virginia Commonwealth University, Richmond, VA, 23298, USA.; The Institute for Structural Biology, Drug Discovery and Development, School of Pharmacy, Virginia Commonwealth University, Richmond, VA, 23298, USA.
Omar AM; Department of Pharmaceutical Chemistry, Faculty of Pharmacy, King Abdulaziz University, Alsulaymanyah, 21589, Jeddah, Saudi Arabia.; Department of Pharmaceutical Chemistry, Faculty of Pharmacy, Al-Azhar University, Cairo, 11884, Egypt.
Venitz J; Department of Pharmaceutics, Virginia Commonwealth University, Richmond, VA, 23298, USA.
Zhang Y; Department of Medicinal Chemistry, Virginia Commonwealth University, Richmond, VA, 23298, USA.; The Institute for Structural Biology, Drug Discovery and Development, School of Pharmacy, Virginia Commonwealth University, Richmond, VA, 23298, USA.
Safo MK; Department of Medicinal Chemistry, Virginia Commonwealth University, Richmond, VA, 23298, USA. .; The Institute for Structural Biology, Drug Discovery and Development, School of Pharmacy, Virginia Commonwealth University, Richmond, VA, 23298, USA. .
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Źródło:
Scientific reports [Sci Rep] 2020 Nov 20; Vol. 10 (1), pp. 20277. Date of Electronic Publication: 2020 Nov 20.
Typ publikacji:
Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
MeSH Terms:
Anemia, Sickle Cell/*drug therapy
Antisickling Agents/*pharmacology
Erythrocytes, Abnormal/*drug effects
Hemoglobin, Sickle/*metabolism
Protein Multimerization/*drug effects
Adult ; Anemia, Sickle Cell/blood ; Antisickling Agents/therapeutic use ; Caco-2 Cells ; Cell Hypoxia ; Crystallography, X-Ray ; Drug Evaluation, Preclinical ; Erythrocytes, Abnormal/metabolism ; Hemoglobin, Sickle/genetics ; Humans ; Models, Molecular ; Oxygen/metabolism
Czasopismo naukowe
Tytuł:
Rheological properties of sickle erythrocytes in patients with sickle-cell anemia: The effect of hydroxyurea, fetal hemoglobin, and α-thalassemia.
Autorzy:
Ballas SK; Department of Medicine, Cardeza Foundation for Hematologic Research, Sidney Kimmel Medical College, Thomas Jefferson University, Philadelphia, Pennsylvania.
Connes P; Laboratoire LIBM EA7424, Equipe 'Biologie Vasculaire et du Globule Rouge', Université Claude Bernard Lyon 1, Villeurbanne, France.; Laboratoire d'Excellence du Globule Rouge (LABEX GR-Ex), PRES Sorbonne, Paris, France.; Institut Universitaire de France (IUF), Paris, France.
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Corporate Authors:
Investigators of the Multicenter Study of Hydroxyurea in Sickle Cell Anemia
Źródło:
European journal of haematology [Eur J Haematol] 2018 Dec; Vol. 101 (6), pp. 798-803. Date of Electronic Publication: 2018 Oct 09.
Typ publikacji:
Journal Article
MeSH Terms:
Anemia, Sickle Cell/*blood
Erythrocytes, Abnormal/*metabolism
Anemia, Sickle Cell/complications ; Anemia, Sickle Cell/drug therapy ; Biomarkers ; Erythrocyte Indices ; Erythrocytes, Abnormal/drug effects ; Fetal Hemoglobin/metabolism ; Genotype ; Hemorheology/drug effects ; Humans ; Hydroxyurea/therapeutic use ; Treatment Outcome ; alpha-Globins/genetics ; alpha-Thalassemia/blood ; alpha-Thalassemia/complications
Czasopismo naukowe
Tytuł:
Shape oscillations of single blood drops: applications to human blood and sickle cell disease.
Autorzy:
Hosseinzadeh VA; Department of Mechanical Engineering, Boston University, 110 Cummington Mall, Boston, MA, 02215, USA.
Brugnara C; Department of Laboratory Medicine, Boston Children's Hospital, Harvard Medical School, 300 Longwood Avenue, Boston, MA, 02115, USA.
Holt RG; Department of Mechanical Engineering, Boston University, 110 Cummington Mall, Boston, MA, 02215, USA. .
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Źródło:
Scientific reports [Sci Rep] 2018 Nov 14; Vol. 8 (1), pp. 16794. Date of Electronic Publication: 2018 Nov 14.
Typ publikacji:
Journal Article; Research Support, U.S. Gov't, Non-P.H.S.
MeSH Terms:
Blood Viscosity*/drug effects
Anemia, Sickle Cell/*blood
Erythrocytes, Abnormal/*pathology
Rheology/*methods
Anemia, Sickle Cell/diagnosis ; Fetal Hemoglobin/analysis ; Humans ; Hydroxyurea/pharmacology ; Rheology/standards ; Sound
Czasopismo naukowe
Tytuł:
Differential effects of adenylyl cyclase-protein kinase A cascade on shear-induced changes of sickle cell deformability.
Autorzy:
Ugurel E; Department of Physiology, Koç University School of Medicine, Sariyer, Istanbul, Turkey.
Connes P; Laboratoire Interuniversitaire de Biologie de la Motricité (LIBM) EA7424, Team « Vascular Biology and Red Blood Cell », Université Claude Bernard Lyon 1, Lyon, France.; Laboratoire d'Excellence du Globule Rouge (Labex GR-Ex), PRES Sorbonne, Paris, France.; Institut Universitaire de France (IUF), Paris, France.
Yavas G; Department of Physiology, Koç University School of Medicine, Sariyer, Istanbul, Turkey.
Eglenen B; Department of Physiology, Koç University School of Medicine, Sariyer, Istanbul, Turkey.
Turkay M; Department of Physiology, Koç University School of Medicine, Sariyer, Istanbul, Turkey.
Aksu AC; Department of Physiology, Koç University School of Medicine, Sariyer, Istanbul, Turkey.
Renoux C; Laboratoire Interuniversitaire de Biologie de la Motricité (LIBM) EA7424, Team « Vascular Biology and Red Blood Cell », Université Claude Bernard Lyon 1, Lyon, France.; Laboratoire d'Excellence du Globule Rouge (Labex GR-Ex), PRES Sorbonne, Paris, France.; UF de biochimie des pathologies érythrocytaires, Centre de Biologie Est, Hospices Civils de Lyon, Lyon, France.
Joly P; Laboratoire Interuniversitaire de Biologie de la Motricité (LIBM) EA7424, Team « Vascular Biology and Red Blood Cell », Université Claude Bernard Lyon 1, Lyon, France.; Laboratoire d'Excellence du Globule Rouge (Labex GR-Ex), PRES Sorbonne, Paris, France.; UF de biochimie des pathologies érythrocytaires, Centre de Biologie Est, Hospices Civils de Lyon, Lyon, France.
Gauthier A; Laboratoire Interuniversitaire de Biologie de la Motricité (LIBM) EA7424, Team « Vascular Biology and Red Blood Cell », Université Claude Bernard Lyon 1, Lyon, France.; Laboratoire d'Excellence du Globule Rouge (Labex GR-Ex), PRES Sorbonne, Paris, France.; Institut d'hématologie et d'oncologie pédiatrique (IHOP), Hospices Civils de Lyon, Lyon, France.
Hot A; Clinique de Médecine Ambulatoire/Hématologie Hôpital Edouard Herriot, Lyon, Lyon, France.
Bertrand Y; Institut d'hématologie et d'oncologie pédiatrique (IHOP), Hospices Civils de Lyon, Lyon, France.
Cannas G; Laboratoire Interuniversitaire de Biologie de la Motricité (LIBM) EA7424, Team « Vascular Biology and Red Blood Cell », Université Claude Bernard Lyon 1, Lyon, France.; Laboratoire d'Excellence du Globule Rouge (Labex GR-Ex), PRES Sorbonne, Paris, France.; Clinique de Médecine Ambulatoire/Hématologie Hôpital Edouard Herriot, Lyon, Lyon, France.
Yalcin O; Department of Physiology, Koç University School of Medicine, Sariyer, Istanbul, Turkey.
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Źródło:
Clinical hemorheology and microcirculation [Clin Hemorheol Microcirc] 2019; Vol. 73 (4), pp. 531-543.
Typ publikacji:
Journal Article
MeSH Terms:
Adenylyl Cyclases/*metabolism
Anemia, Sickle Cell/*blood
Cyclic AMP-Dependent Protein Kinases/*metabolism
Erythrocytes, Abnormal/*metabolism
Adult ; Erythrocytes/metabolism ; Female ; Humans ; Male ; Young Adult
Czasopismo naukowe
Tytuł:
LIN28A expression reduces sickling of cultured human erythrocytes.
Autorzy:
de Vasconcellos JF; Molecular Genomics and Therapeutics Section, Molecular Medicine Branch, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland, United States of America.
Fasano RM; Center for Cancer and Blood Disorders, Children's National Medical Center, Washington, District of Columbia, United States of America.
Lee YT; Molecular Genomics and Therapeutics Section, Molecular Medicine Branch, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland, United States of America.
Kaushal M; Molecular Genomics and Therapeutics Section, Molecular Medicine Branch, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland, United States of America; Center for Cancer and Blood Disorders, Children's National Medical Center, Washington, District of Columbia, United States of America.
Byrnes C; Molecular Genomics and Therapeutics Section, Molecular Medicine Branch, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland, United States of America.
Meier ER; Molecular Genomics and Therapeutics Section, Molecular Medicine Branch, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland, United States of America; Center for Cancer and Blood Disorders, Children's National Medical Center, Washington, District of Columbia, United States of America.
Anderson M; Molecular Genomics and Therapeutics Section, Molecular Medicine Branch, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland, United States of America.
Rabel A; Molecular Genomics and Therapeutics Section, Molecular Medicine Branch, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland, United States of America.
Braylan R; Department of Laboratory Medicine, Clinical Center, National Institutes of Health, Bethesda, Maryland, United States of America.
Stroncek DF; Cell Processing Section, Department of Transfusion Medicine, Clinical Center, National Institutes of Health, Bethesda, Maryland, United States of America.
Miller JL; Molecular Genomics and Therapeutics Section, Molecular Medicine Branch, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland, United States of America.
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Źródło:
PloS one [PLoS One] 2014 Sep 04; Vol. 9 (9), pp. e106924. Date of Electronic Publication: 2014 Sep 04 (Print Publication: 2014).
Typ publikacji:
Journal Article; Research Support, N.I.H., Intramural
MeSH Terms:
Anemia, Sickle Cell/*genetics
Erythrocytes, Abnormal/*metabolism
Fetal Hemoglobin/*genetics
MicroRNAs/*genetics
RNA-Binding Proteins/*genetics
beta-Globins/*genetics
Adolescent ; Anemia, Sickle Cell/metabolism ; Anemia, Sickle Cell/pathology ; Anemia, Sickle Cell/therapy ; Cell Differentiation ; Cell Shape ; Child ; Erythroblasts/metabolism ; Erythroblasts/pathology ; Erythrocyte Transfusion ; Erythrocytes, Abnormal/pathology ; Fetal Hemoglobin/metabolism ; Gene Expression Regulation ; Genetic Vectors ; Humans ; Lentivirus/genetics ; Lentivirus/metabolism ; Male ; MicroRNAs/metabolism ; Primary Cell Culture ; RNA-Binding Proteins/metabolism ; Signal Transduction ; Transfection ; beta-Globins/metabolism
Czasopismo naukowe
Tytuł:
GBT440 improves red blood cell deformability and reduces viscosity of sickle cell blood under deoxygenated conditions.
Autorzy:
Dufu K; Global Blood Therapeutics Inc., South San Francisco, CA, USA.
Patel M; Global Blood Therapeutics Inc., South San Francisco, CA, USA.
Oksenberg D; Global Blood Therapeutics Inc., South San Francisco, CA, USA.
Cabrales P; Department of Bioengineering, University of California, San Diego, La Jolla, CA, USA.
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Źródło:
Clinical hemorheology and microcirculation [Clin Hemorheol Microcirc] 2018; Vol. 70 (1), pp. 95-105.
Typ publikacji:
Journal Article
MeSH Terms:
Anemia, Sickle Cell/*blood
Blood Viscosity/*genetics
Erythrocyte Deformability/*physiology
Erythrocytes, Abnormal/*physiology
Humans
Czasopismo naukowe
Tytuł:
Patient-specific modeling of individual sickle cell behavior under transient hypoxia.
Autorzy:
Li X; Division of Applied Mathematics, Brown University, Providence, Rhode Island, United States of America.
Du E; Department of Materials Science and Engineering, Massachusetts Institute of Technology, Cambridge, Massachusetts, United States of America.; Department of Ocean and Mechanical Engineering, Florida Atlantic University, Boca Raton, Florida, United States of America.
Dao M; Department of Materials Science and Engineering, Massachusetts Institute of Technology, Cambridge, Massachusetts, United States of America.
Suresh S; Department of Biomedical Engineering, Computational Biology Department, and Department of Materials Science and Engineering, Carnegie Mellon University, Pittsburgh, Pennsylvania, United States of America.
Karniadakis GE; Division of Applied Mathematics, Brown University, Providence, Rhode Island, United States of America.
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Źródło:
PLoS computational biology [PLoS Comput Biol] 2017 Mar 13; Vol. 13 (3), pp. e1005426. Date of Electronic Publication: 2017 Mar 13 (Print Publication: 2017).
Typ publikacji:
Journal Article; Research Support, U.S. Gov't, Non-P.H.S.; Research Support, N.I.H., Extramural
MeSH Terms:
Models, Cardiovascular*
Patient-Specific Modeling*
Anemia, Sickle Cell/*pathology
Anemia, Sickle Cell/*physiopathology
Erythrocytes, Abnormal/*pathology
Erythrocytes, Abnormal/*physiology
Cell Hypoxia ; Cell Movement ; Cells, Cultured ; Computer Simulation ; Erythrocyte Membrane/pathology ; Erythrocyte Membrane/physiology ; Hemoglobins, Abnormal/metabolism ; Humans
Czasopismo naukowe
Tytuł:
Sickle red cell-endothelium interactions.
Autorzy:
Kaul DK; Department of Medicine, Albert Einstein College of Medicine, Bronx, New York 10461, USA. />Finnegan E
Barabino GA
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Źródło:
Microcirculation (New York, N.Y. : 1994) [Microcirculation] 2009 Jan; Vol. 16 (1), pp. 97-111.
Typ publikacji:
Journal Article; Research Support, N.I.H., Extramural; Review
MeSH Terms:
Cell Communication*
Anemia, Sickle Cell/*metabolism
Endothelium, Vascular/*metabolism
Erythrocytes, Abnormal/*metabolism
Anemia, Sickle Cell/genetics ; Anemia, Sickle Cell/pathology ; Anemia, Sickle Cell/physiopathology ; Animals ; Cell Adhesion/genetics ; Endothelium, Vascular/pathology ; Endothelium, Vascular/physiopathology ; Erythrocytes, Abnormal/pathology ; Humans ; Leukocytes/metabolism ; Leukocytes/pathology ; Mice ; Mice, Transgenic
Czasopismo naukowe
Tytuł:
Hyperhemolysis syndrome in a patient with sickle cell disease with erythrophagocytosis in peripheral blood.
Autorzy:
Islam MS; Department of Hematology, St George's Hospital, Blackshaw Road, Tooting SW17 0QT, London, UK. />Chia L
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Źródło:
European journal of haematology [Eur J Haematol] 2010 Feb 01; Vol. 84 (2), pp. 188. Date of Electronic Publication: 2009 Sep 10.
Typ publikacji:
Case Reports; Journal Article
MeSH Terms:
Hemolysis*
Phagocytosis*
Anemia, Sickle Cell/*pathology
Erythrocytes, Abnormal/*pathology
Adult ; Anemia, Sickle Cell/therapy ; Humans ; Male ; Syndrome
Czasopismo naukowe
Tytuł:
Importance of methodological standardization for the ektacytometric measures of red blood cell deformability in sickle cell anemia.
Autorzy:
Renoux C; Laboratoire CRIS EA647, Team 'Vascular Biology and Red Blood Cell', Université Lyon 1, Université de Lyon, Lyon, France.; Laboratoire de Biochimie et de Biologie Moléculatire, Hôpital Edouard Herriot, Lyon, France.; Laboratoired'Excellence GR-Ex « The red cell: from genesis to death », Paris, France.
Parrow N; National Institutes of Health, Washington, DC, USA.
Faes C; Laboratoire CRIS EA647, Team 'Vascular Biology and Red Blood Cell', Université Lyon 1, Université de Lyon, Lyon, France.; Laboratoired'Excellence GR-Ex « The red cell: from genesis to death », Paris, France.
Joly P; Laboratoire CRIS EA647, Team 'Vascular Biology and Red Blood Cell', Université Lyon 1, Université de Lyon, Lyon, France.; Laboratoire de Biochimie et de Biologie Moléculatire, Hôpital Edouard Herriot, Lyon, France.; Laboratoired'Excellence GR-Ex « The red cell: from genesis to death », Paris, France.
Hardeman M; Academic Medical Center, Amsterdam, The Netherlands.
Tisdale J; National Institutes of Health, Washington, DC, USA.
Levine M; National Institutes of Health, Washington, DC, USA.
Garnier N; Institut d'Hématologie et d'Oncologie Pédiatrique, Lyon, France.
Bertrand Y; Institut d'Hématologie et d'Oncologie Pédiatrique, Lyon, France.
Kebaili K; Institut d'Hématologie et d'Oncologie Pédiatrique, Lyon, France.
Cuzzubbo D; Institut d'Hématologie et d'Oncologie Pédiatrique, Lyon, France.
Cannas G; Service de Médecine Interne, Hôpital Edouard Herriot, Lyon, France.
Martin C; Laboratoire CRIS EA647, Team 'Vascular Biology and Red Blood Cell', Université Lyon 1, Université de Lyon, Lyon, France.; Laboratoired'Excellence GR-Ex « The red cell: from genesis to death », Paris, France.
Connes P; Laboratoire CRIS EA647, Team 'Vascular Biology and Red Blood Cell', Université Lyon 1, Université de Lyon, Lyon, France.; Laboratoired'Excellence GR-Ex « The red cell: from genesis to death », Paris, France.; Institut Universitaire de France, Paris, France.
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Źródło:
Clinical hemorheology and microcirculation [Clin Hemorheol Microcirc] 2016; Vol. 62 (2), pp. 173-9.
Typ publikacji:
Journal Article
MeSH Terms:
Anemia, Sickle Cell/*blood
Erythrocyte Deformability/*drug effects
Erythrocytes/*cytology
Erythrocytes, Abnormal/*cytology
Hematologic Tests/*standards
Hematologic Tests/methods ; Hemoglobin, Sickle/analysis ; Humans ; Stress, Mechanical
Czasopismo naukowe
Tytuł:
Evaluation of F cells in sickle cell disorders by flow cytometry -- comparison with the Kleihauer-Betke's slide method.
Autorzy:
Italia KY; Institute of Immunohaematology (ICMR), K.E.M. Hospital Campus, Parel, Mumbai, India.
Colah R
Mohanty D
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Źródło:
International journal of laboratory hematology [Int J Lab Hematol] 2007 Dec; Vol. 29 (6), pp. 409-14.
Typ publikacji:
Comparative Study; Journal Article
MeSH Terms:
Erythrocytes, Abnormal*/pathology
Flow Cytometry*
Anemia, Sickle Cell/*blood
Fetal Hemoglobin/*analysis
beta-Thalassemia/*blood
Adult ; Anemia, Sickle Cell/pathology ; Erythropoiesis ; Female ; Fetomaternal Transfusion/blood ; Fetomaternal Transfusion/pathology ; Humans ; Leukemia, Myeloid, Acute/blood ; Leukemia, Myeloid, Acute/pathology ; Male ; Pregnancy ; Sensitivity and Specificity ; beta-Thalassemia/pathology
Czasopismo naukowe
Tytuł:
The paradox of the serrated sickle erythrocyte: The importance of the red blood cell membrane topography.
Autorzy:
Ballas SK; Cardeza Foundation for hematologic Research, Department of Medicine, Jefferson Medical College, Thomas Jefferson University, Philadelphia, PA, USA.
Connes P; Laboratory CRIS-EA 647 -Section 'Vascular Biology and Red Blood Cell', University Claude Bernard Lyon 1, Villeurbanne, France.
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Źródło:
Clinical hemorheology and microcirculation [Clin Hemorheol Microcirc] 2015 Oct 16; Vol. 63 (2), pp. 149-52.
Typ publikacji:
Journal Article; Review
MeSH Terms:
Rheology*
Anemia, Sickle Cell/*blood
Erythrocyte Membrane/*metabolism
Erythrocytes/*metabolism
Erythrocytes, Abnormal/*metabolism
Humans
Czasopismo naukowe
Tytuł:
Biological parameters predictive of percent dense red blood cell decrease under hydroxyurea.
Autorzy:
Rakotoson MG; Institut Mondor de Recherche Biomédicale, Unité 955, Equipe 2: Transfusion et Maladies du Globule Rouge, Université Paris-Est Créteil, Créteil, France. .
Di Liberto G; Institut Mondor de Recherche Biomédicale, Unité 955, Equipe 2: Transfusion et Maladies du Globule Rouge, Université Paris-Est Créteil, Créteil, France. .; Etablissement Français du Sang, Île-de-France Mondor, Créteil, France. .
Audureau E; Service de Santé Publique, Hôpital Henri-Mondor, APHP, LIC EA4393, Université Paris-Est Créteil, Créteil, France. .
Habibi A; Centre de Référence des Syndromes Drépanocytaires Majeurs, Hôpital Henri-Mondor, APHP, Université Paris-Est Créteil, 51, avenue du Mal-de-Lattre-de-Tassigny, 94010, Créteil Cedex, France. .
Fauroux C; Centre de Référence des Syndromes Drépanocytaires Majeurs, Hôpital Henri-Mondor, APHP, Université Paris-Est Créteil, 51, avenue du Mal-de-Lattre-de-Tassigny, 94010, Créteil Cedex, France. .
Khorgami S; Institut Mondor de Recherche Biomédicale, Unité 955, Equipe 2: Transfusion et Maladies du Globule Rouge, Université Paris-Est Créteil, Créteil, France. sanam_.; Etablissement Français du Sang, Île-de-France Mondor, Créteil, France. sanam_.
Hulin A; Laboratoire de Pharmacologie, APHP, Hôpital Henri-Mondor, Université Paris Est-Créteil, Créteil, France. .
Loric S; Laboratoire de Biochimie et Génétique, Hôpital Henri-Mondor, Créteil, France. .
Noizat-Pirenne F; Institut Mondor de Recherche Biomédicale, Unité 955, Equipe 2: Transfusion et Maladies du Globule Rouge, Université Paris-Est Créteil, Créteil, France. .; Etablissement Français du Sang, Île-de-France Mondor, Créteil, France. .
Galacteros F; Institut Mondor de Recherche Biomédicale, Unité 955, Equipe 2: Transfusion et Maladies du Globule Rouge, Université Paris-Est Créteil, Créteil, France. .; Centre de Référence des Syndromes Drépanocytaires Majeurs, Hôpital Henri-Mondor, APHP, Université Paris-Est Créteil, 51, avenue du Mal-de-Lattre-de-Tassigny, 94010, Créteil Cedex, France. .
Bartolucci P; Institut Mondor de Recherche Biomédicale, Unité 955, Equipe 2: Transfusion et Maladies du Globule Rouge, Université Paris-Est Créteil, Créteil, France. .; Centre de Référence des Syndromes Drépanocytaires Majeurs, Hôpital Henri-Mondor, APHP, Université Paris-Est Créteil, 51, avenue du Mal-de-Lattre-de-Tassigny, 94010, Créteil Cedex, France. .
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Źródło:
Orphanet journal of rare diseases [Orphanet J Rare Dis] 2015 May 09; Vol. 10, pp. 57. Date of Electronic Publication: 2015 May 09.
Typ publikacji:
Clinical Study; Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Anemia, Sickle Cell/*drug therapy
Erythrocytes, Abnormal/*drug effects
Hydroxyurea/*therapeutic use
Adult ; Female ; Fetal Hemoglobin ; Humans ; Male
Czasopismo naukowe
Tytuł:
In vivo studies of sickle red blood cells.
Autorzy:
Kaul DK; Department of Medicine, Albert Einstein College of Medicine, Bronx, New York 10461, USA. />Fabry ME
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Źródło:
Microcirculation (New York, N.Y. : 1994) [Microcirculation] 2004 Mar; Vol. 11 (2), pp. 153-65.
Typ publikacji:
Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Review
MeSH Terms:
Hemodynamics*
Anemia, Sickle Cell/*metabolism
Erythrocytes, Abnormal/*metabolism
Vascular Diseases/*metabolism
Anemia, Sickle Cell/physiopathology ; Anemia, Sickle Cell/therapy ; Animals ; Cell Adhesion ; Humans ; Vascular Diseases/physiopathology ; Vascular Diseases/therapy ; Venules/metabolism ; Venules/physiopathology
Czasopismo naukowe
Tytuł:
Sickle cell vasoocclusion: heterotypic, multicellular aggregations driven by leukocyte adhesion.
Autorzy:
Frenette PS; Mount Sinai School of Medicine, Department of Medicine (Hematology), New York, New York 10029, USA.
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Źródło:
Microcirculation (New York, N.Y. : 1994) [Microcirculation] 2004 Mar; Vol. 11 (2), pp. 167-77.
Typ publikacji:
Journal Article; Research Support, N.I.H., Extramural; Review
MeSH Terms:
Anemia, Sickle Cell/*metabolism
Erythrocytes, Abnormal/*metabolism
Hemoglobin, Sickle/*metabolism
Ischemia/*metabolism
Leukocytes/*metabolism
Vascular Diseases/*metabolism
Anemia, Sickle Cell/pathology ; Anemia, Sickle Cell/physiopathology ; Anemia, Sickle Cell/therapy ; Animals ; Blood Flow Velocity ; Cell Adhesion ; Endothelium, Vascular ; Erythrocytes, Abnormal/pathology ; Humans ; Ischemia/pathology ; Ischemia/physiopathology ; Ischemia/therapy ; Leukocytes/pathology ; Vascular Diseases/pathology ; Vascular Diseases/physiopathology ; Vascular Diseases/therapy
Czasopismo naukowe
Tytuł:
Sickle red cell microrheology and sickle blood rheology.
Autorzy:
Ballas SK; Department of Medicine, Cardeza Foundation for Hematologic Research, Jefferson Medical College, Philadelphia, Pennsylvania, USA. />Mohandas N
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Źródło:
Microcirculation (New York, N.Y. : 1994) [Microcirculation] 2004 Mar; Vol. 11 (2), pp. 209-25.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't; Review
MeSH Terms:
Erythrocytes, Abnormal*/metabolism
Erythrocytes, Abnormal*/ultrastructure
Anemia, Sickle Cell/*physiopathology
Endothelium, Vascular/*physiopathology
Vascular Diseases/*physiopathology
Anemia, Sickle Cell/metabolism ; Anemia, Sickle Cell/pathology ; Animals ; Endothelium, Vascular/metabolism ; Endothelium, Vascular/pathology ; Hemoglobin, Sickle/metabolism ; Humans ; Inflammation/metabolism ; Inflammation/pathology ; Inflammation/physiopathology ; Rheology ; Vascular Diseases/metabolism ; Vascular Diseases/pathology
Czasopismo naukowe
Tytuł:
Polymerization and sickle cell disease: a molecular view.
Autorzy:
Ferrone FA; Department of Physics, Drexel University, Philadelphia, Pennsylvania 19104, USA.
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Źródło:
Microcirculation (New York, N.Y. : 1994) [Microcirculation] 2004 Mar; Vol. 11 (2), pp. 115-28.
Typ publikacji:
Journal Article; Research Support, N.I.H., Extramural; Review
MeSH Terms:
Anemia, Sickle Cell*/metabolism
Anemia, Sickle Cell*/physiopathology
Models, Chemical*
Erythrocytes, Abnormal/*chemistry
Hemoglobin, Sickle/*chemistry
Multiprotein Complexes/*chemistry
Erythrocytes, Abnormal/metabolism ; Hemoglobin, Sickle/metabolism ; Multiprotein Complexes/metabolism ; Polymers/chemistry ; Polymers/metabolism ; Thermodynamics
Czasopismo naukowe

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