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Wyszukujesz frazę ""Arrhythmogenic Right Ventricular Dysplasia"" wg kryterium: Temat


Tytuł:
Detection of gene mutation in the prognosis of a patient with arrhythmogenic right ventricular cardiomyopathy: a case report.
Autorzy:
Phan DP; Cardiac Electrocardiogram and Electrophysiology Laboratory, Vietnam National Heart Institute, Bach Mai Hospital, 78 Giai Phong St., Hai Ba Trung, Hanoi, Vietnam. .; Hanoi Medical University, 1 Ton That Tung St., Dong Da, Hanoi, Vietnam. .
Tran TV; Cardiac Electrocardiogram and Electrophysiology Laboratory, Vietnam National Heart Institute, Bach Mai Hospital, 78 Giai Phong St., Hai Ba Trung, Hanoi, Vietnam.; Hanoi Medical University, 1 Ton That Tung St., Dong Da, Hanoi, Vietnam.
Le VK; Cardiac Electrocardiogram and Electrophysiology Laboratory, Vietnam National Heart Institute, Bach Mai Hospital, 78 Giai Phong St., Hai Ba Trung, Hanoi, Vietnam.
Nguyen TV; Hanoi Medical University, 1 Ton That Tung St., Dong Da, Hanoi, Vietnam.
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Źródło:
Journal of medical case reports [J Med Case Rep] 2024 Feb 10; Vol. 18 (1), pp. 49. Date of Electronic Publication: 2024 Feb 10.
Typ publikacji:
Case Reports; Journal Article
MeSH Terms:
Arrhythmogenic Right Ventricular Dysplasia*/complications
Arrhythmogenic Right Ventricular Dysplasia*/diagnosis
Arrhythmogenic Right Ventricular Dysplasia*/genetics
Humans ; Male ; Adolescent ; Prognosis ; Death, Sudden, Cardiac/etiology ; Death, Sudden, Cardiac/prevention & control ; Electrocardiography ; Mutation
Czasopismo naukowe
Tytuł:
Arrhythmogenic Right Ventricular Cardiomyopathy Post-Mortem Assessment: A Systematic Review.
Autorzy:
Cianci V; Department of Biomedical and Dental Sciences and Morphofunctional Imaging, Section of Legal Medicine, University of Messina, Via Consolare Valeria, 1, 98125 Messina, Italy.
Forzese E; Department of Biomedical and Dental Sciences and Morphofunctional Imaging, Section of Legal Medicine, University of Messina, Via Consolare Valeria, 1, 98125 Messina, Italy.
Sapienza D; Department of Biomedical and Dental Sciences and Morphofunctional Imaging, Section of Legal Medicine, University of Messina, Via Consolare Valeria, 1, 98125 Messina, Italy.
Cianci A; Department of Cardiovascular Medicine, Fondazione Policlinico Universitario A. Gemelli-IRCCS, Largo A. Gemelli 8, 00168 Rome, Italy.
Ieni A; Department of Human Pathology in Adult and Developmental Age 'Gaetano Barresi', Section of Pathology, University of Messina, 98125 Messina, Italy.
Germanà A; Zebrafish Neuromorphology Lab, Department of Veterinary Sciences, Via Palatucci Snc, University of Messina, 98168 Messina, Italy.
Guerrera MC; Zebrafish Neuromorphology Lab, Department of Veterinary Sciences, Via Palatucci Snc, University of Messina, 98168 Messina, Italy.
Omero F; Medical Oncology Unit, Department of Human Pathology 'G.Barresi', University of Messina, 98125 Messina, Italy.
Speranza D; Medical Oncology Unit, Department of Human Pathology 'G.Barresi', University of Messina, 98125 Messina, Italy.
Cracò A; Department of Biomedical Sciences and Morphological and Functional Imaging, Diagnostic and Interventional Radiology Unit, University Hospital Messina, 98125 Messina, Italy.
Asmundo A; Department of Biomedical and Dental Sciences and Morphofunctional Imaging, Section of Legal Medicine, University of Messina, Via Consolare Valeria, 1, 98125 Messina, Italy.
Gualniera P; Department of Biomedical and Dental Sciences and Morphofunctional Imaging, Section of Legal Medicine, University of Messina, Via Consolare Valeria, 1, 98125 Messina, Italy.
Mondello C; Department of Biomedical and Dental Sciences and Morphofunctional Imaging, Section of Legal Medicine, University of Messina, Via Consolare Valeria, 1, 98125 Messina, Italy.
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Źródło:
International journal of molecular sciences [Int J Mol Sci] 2024 Feb 20; Vol. 25 (5). Date of Electronic Publication: 2024 Feb 20.
Typ publikacji:
Systematic Review; Journal Article; Review
MeSH Terms:
Arrhythmogenic Right Ventricular Dysplasia*
Humans ; Autopsy ; Myocardium ; Databases, Factual ; Death, Sudden, Cardiac
Czasopismo naukowe
Tytuł:
Single-cell RNA sequencing in donor and end-stage heart failure patients identifies NLRP3 as a therapeutic target for arrhythmogenic right ventricular cardiomyopathy.
Autorzy:
Fu M; Beijing Key Laboratory of Preclinical Research and Evaluation for Cardiovascular Implant Materials, Animal Experimental Centre, Fuwai Hospital, National Center for Cardiovascular Disease, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 100037, China.; Galactophore Department, Galactophore Center, Beijing Shijitan Hospital, Capital Medical University, Beijing, China.
Hua X; Beijing Key Laboratory of Preclinical Research and Evaluation for Cardiovascular Implant Materials, Animal Experimental Centre, Fuwai Hospital, National Center for Cardiovascular Disease, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 100037, China.; State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, 167A Beilishi Road, Xi Cheng District, Beijing, 10037, China.
Shu S; Beijing Key Laboratory of Preclinical Research and Evaluation for Cardiovascular Implant Materials, Animal Experimental Centre, Fuwai Hospital, National Center for Cardiovascular Disease, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 100037, China.; State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, 167A Beilishi Road, Xi Cheng District, Beijing, 10037, China.
Xu X; Beijing Key Laboratory of Preclinical Research and Evaluation for Cardiovascular Implant Materials, Animal Experimental Centre, Fuwai Hospital, National Center for Cardiovascular Disease, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 100037, China.; State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, 167A Beilishi Road, Xi Cheng District, Beijing, 10037, China.
Zhang H; Beijing Key Laboratory of Preclinical Research and Evaluation for Cardiovascular Implant Materials, Animal Experimental Centre, Fuwai Hospital, National Center for Cardiovascular Disease, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 100037, China.; State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, 167A Beilishi Road, Xi Cheng District, Beijing, 10037, China.
Peng Z; Department of Orthopedics, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, China.
Mo H; Shenzhen Key Laboratory of Cardiovascular Disease, Fuwai Hospital Chinese Academy of Medical Sciences, Shenzhen, 518057, China.
Liu Y; Engineering Research Center of Molecular and Neuro Imaging of Ministry of Education, School of Life Science and Technology, Xidian University, Shaanxi, 710126, China.
Chen X; State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, 167A Beilishi Road, Xi Cheng District, Beijing, 10037, China.
Yang Y; State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, 167A Beilishi Road, Xi Cheng District, Beijing, 10037, China.
Zhang N; State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, 167A Beilishi Road, Xi Cheng District, Beijing, 10037, China.
Wang X; State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, 167A Beilishi Road, Xi Cheng District, Beijing, 10037, China.
Liu Z; State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, 167A Beilishi Road, Xi Cheng District, Beijing, 10037, China.
Yue G; Beijing Key Laboratory of Preclinical Research and Evaluation for Cardiovascular Implant Materials, Animal Experimental Centre, Fuwai Hospital, National Center for Cardiovascular Disease, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 100037, China.
Hu S; Beijing Key Laboratory of Preclinical Research and Evaluation for Cardiovascular Implant Materials, Animal Experimental Centre, Fuwai Hospital, National Center for Cardiovascular Disease, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 100037, China. .; State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, 167A Beilishi Road, Xi Cheng District, Beijing, 10037, China. .; Shenzhen Key Laboratory of Cardiovascular Disease, Fuwai Hospital Chinese Academy of Medical Sciences, Shenzhen, 518057, China. .; Department of Cardiovascular Surgery, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 10037, China. .; The Cardiomyopathy Research Group, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 10037, China. .
Song J; Beijing Key Laboratory of Preclinical Research and Evaluation for Cardiovascular Implant Materials, Animal Experimental Centre, Fuwai Hospital, National Center for Cardiovascular Disease, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 100037, China. .; State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, 167A Beilishi Road, Xi Cheng District, Beijing, 10037, China. .; Shenzhen Key Laboratory of Cardiovascular Disease, Fuwai Hospital Chinese Academy of Medical Sciences, Shenzhen, 518057, China. .; Department of Cardiovascular Surgery, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 10037, China. .; The Cardiomyopathy Research Group, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 10037, China. .
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Źródło:
BMC medicine [BMC Med] 2024 Jan 08; Vol. 22 (1), pp. 11. Date of Electronic Publication: 2024 Jan 08.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Arrhythmogenic Right Ventricular Dysplasia*/genetics
Heart Failure*/genetics
Humans ; Animals ; Mice ; NLR Family, Pyrin Domain-Containing 3 Protein/genetics ; Genome-Wide Association Study ; Arrhythmias, Cardiac ; Sequence Analysis, RNA
Czasopismo naukowe
Tytuł:
Arrhythmogenic left ventricular cardiomyopathy caused by a novel likely pathogenic DSP mutation, p.K1165Rfs*8, in a family with sudden cardiac death.
Autorzy:
Azimi A; Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran University of Medical Sciences, Tehran, Iran.
Pourirahim M; Cardiogenetic Research Center, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran.
Houshmand G; Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran University of Medical Sciences, Tehran, Iran.
Adimi S; Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran University of Medical Sciences, Tehran, Iran.
Maleki M; Cardiogenetic Research Center, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran.
Kalayinia S; Cardiogenetic Research Center, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran. .
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Źródło:
BMC medical genomics [BMC Med Genomics] 2023 Oct 26; Vol. 16 (1), pp. 266. Date of Electronic Publication: 2023 Oct 26.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Arrhythmogenic Right Ventricular Dysplasia*/genetics
Arrhythmogenic Right Ventricular Dysplasia*/pathology
Cardiomyopathies*/genetics
Humans ; Iran ; Genetic Predisposition to Disease ; Death, Sudden, Cardiac/etiology ; Mutation
Czasopismo naukowe
Tytuł:
Ringlike late gadolinium enhancement provides incremental prognostic value in non-classical arrhythmogenic cardiomyopathy.
Autorzy:
Yang Y; Department of Radiology, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou, 510080, China.
Wei X; Department of Radiology, Sun Yat-Sen Memorial Hospital, Sun Yat-Sen University, Guangzhou, 510120, China.
Lu G; Department of Interventional Diagnosis and Therapy, Beijing Anzhen Hospital, Capital Medical University, Beijing, 100029, China.
Xie J; Department of Radiology, Guangzhou First People's Hospital, School of Medicine, South China University of Technology, Guangzhou, 510080, China.
Tan Z; Guangdong Cardiovascular Institute, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou, 510080, China.
Du Z; Department of Medical Statistics, School of Public Health, Sun Yat-Sen University, Guangzhou, 510080, China.
Ye W; Department of Radiology, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou, 510080, China.
Xu H; Department of Radiology, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou, 510080, China.
Li X; Department of Radiology, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou, 510080, China.
Liu E; WeiLun PET Center, Department of Nuclear Medicine, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou, 510080, China.
Zhang Q; Guangdong Cardiovascular Institute, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou, 510080, China.
Liu Y; Guangdong Cardiovascular Institute, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou, 510080, China.
Li J; Department of Radiology, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou, 510080, China. .
Liu H; Department of Radiology, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou, 510080, China. .; Guangdong Provincial Key Laboratory of Artificial Intelligence in Medical Image Analysis and Application, Guangdong Provincial People's Hospital, Guangdong Academy of Medical Sciences, Guangzhou, 510080, China. .
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Źródło:
Journal of cardiovascular magnetic resonance : official journal of the Society for Cardiovascular Magnetic Resonance [J Cardiovasc Magn Reson] 2023 Nov 30; Vol. 25 (1), pp. 72. Date of Electronic Publication: 2023 Nov 30.
Typ publikacji:
Journal Article
MeSH Terms:
Contrast Media*
Arrhythmogenic Right Ventricular Dysplasia*/diagnostic imaging
Humans ; Male ; Young Adult ; Adult ; Middle Aged ; Prognosis ; Gadolinium ; Retrospective Studies ; Predictive Value of Tests ; Arrhythmias, Cardiac ; Magnetic Resonance Imaging, Cine
Czasopismo naukowe
Tytuł:
Electrical storm in a middle-aged man.
Autorzy:
Ahadzi D; Department of Internal Medicine, Tamale Teaching Hospital, Tamale, Ghana.
Agyekum F; Department of Medicine, University of Ghana Medical School, Korle-Bu Teaching Hospital, Accra, Ghana.
Doku A; Department of Medicine, University of Ghana Medical School, Korle-Bu Teaching Hospital, Accra, Ghana.
Yakubu AS; Department of Internal Medicine, Tamale Teaching Hospital, Tamale, Ghana.
Hoedofia G; Department of Medicine, Korle-Bu Teaching Hospital, Accra, Ghana.
Ayetey H; Department of Internal Medicine and Therapeutics, University of Cape Coast School of Medical Sciences, Cape Coast, Ghana.
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Źródło:
Ghana medical journal [Ghana Med J] 2023 Jun; Vol. 57 (2), pp. 156-160.
Typ publikacji:
Case Reports
MeSH Terms:
Tachycardia, Ventricular*/therapy
Tachycardia, Ventricular*/complications
Defibrillators, Implantable*
Arrhythmogenic Right Ventricular Dysplasia*/complications
Arrhythmogenic Right Ventricular Dysplasia*/diagnosis
Arrhythmogenic Right Ventricular Dysplasia*/therapy
Male ; Middle Aged ; Humans ; Ventricular Fibrillation/therapy ; Ventricular Fibrillation/complications ; Anti-Arrhythmia Agents/therapeutic use ; Follow-Up Studies
Raport
Tytuł:
Computer-aided detection of arrhythmogenic sites in post-ischemic ventricular tachycardia.
Autorzy:
Baldazzi G; Medical Devices and Signal Processing (MeDSP) Lab, Department of Electrical and Electronic Engineering (DIEE), University of Cagliari, Cagliari, Italy. .; Department of Informatics, Bioengineering, Robotics and Systems Engineering (DIBRIS), University of Genoa, Genoa, Italy. .
Orrù M; Medical Devices and Signal Processing (MeDSP) Lab, Department of Electrical and Electronic Engineering (DIEE), University of Cagliari, Cagliari, Italy.; Department of Informatics, Bioengineering, Robotics and Systems Engineering (DIBRIS), University of Genoa, Genoa, Italy.
Viola G; Department of Cardiology, Santissima Annunziata Hospital, Sassari, Italy.
Pani D; Medical Devices and Signal Processing (MeDSP) Lab, Department of Electrical and Electronic Engineering (DIEE), University of Cagliari, Cagliari, Italy.
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Źródło:
Scientific reports [Sci Rep] 2023 Apr 27; Vol. 13 (1), pp. 6906. Date of Electronic Publication: 2023 Apr 27.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Arrhythmogenic Right Ventricular Dysplasia*
Tachycardia, Ventricular*/diagnosis
Tachycardia, Ventricular*/etiology
Catheter Ablation*/methods
Humans ; Treatment Outcome ; Time Factors ; Computers
Czasopismo naukowe
Tytuł:
A rapid adjunct to the postmortem diagnostic workup for right ventricular dysplasia.
Autorzy:
Aydin NE; Department of Pathology, Izmir Katip Celebi University, Ataturk Hospital, Izmir, Turkey.
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Źródło:
The Pan African medical journal [Pan Afr Med J] 2023 Apr 06; Vol. 44, pp. 164. Date of Electronic Publication: 2023 Apr 06 (Print Publication: 2023).
Typ publikacji:
Journal Article
MeSH Terms:
Arrhythmogenic Right Ventricular Dysplasia*/diagnosis
Humans ; Autopsy ; Death, Sudden, Cardiac
Czasopismo naukowe
Tytuł:
Right Ventricular Function in Arrhythmogenic Right Ventricular Cardiomyopathy: Potential Value of Strain Echocardiography.
Autorzy:
Bjerregaard, Caroline Løkke (AUTHOR)
Biering-Sørensen, Tor (AUTHOR)
Skaarup, Kristoffer Grundtvig (AUTHOR)
Sengeløv, Morten (AUTHOR)
Lassen, Mats Christian Højbjerg (AUTHOR)
Johansen, Niklas Dyrby (AUTHOR)
Olsen, Flemming Javier (AUTHOR)
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Źródło:
Journal of Clinical Medicine. Feb2024, Vol. 13 Issue 3, p717. 15p.
Czasopismo naukowe
Tytuł:
Enhancing Arrhythmogenic Right Ventricular Cardiomyopathy Detection and Risk Stratification: Insights from Advanced Echocardiographic Techniques.
Autorzy:
Olivetti, Natália (AUTHOR)
Sacilotto, Luciana (AUTHOR)
Moleta, Danilo Bora (AUTHOR)
França, Lucas Arraes de (AUTHOR)
Capeline, Lorena Squassante (AUTHOR)
Wulkan, Fanny (AUTHOR)
Wu, Tan Chen (AUTHOR)
Pessente, Gabriele D'Arezzo (AUTHOR)
Carvalho, Mariana Lombardi Peres de (AUTHOR)
Hachul, Denise Tessariol (AUTHOR)
Pereira, Alexandre da Costa (AUTHOR)
Krieger, José E. (AUTHOR)
Scanavacca, Mauricio Ibrahim (AUTHOR)
Vieira, Marcelo Luiz Campos (AUTHOR)
Darrieux, Francisco (AUTHOR)
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Źródło:
Diagnostics (2075-4418). Jan2024, Vol. 14 Issue 2, p150. 13p.
Czasopismo naukowe
Tytuł:
Arrhythmogenic Right Ventricular Cardiomyopathy in Children: A Systematic Review.
Autorzy:
Moisa, Stefana Maria (AUTHOR)
Spoiala, Elena Lia (AUTHOR)
Cinteza, Eliza (AUTHOR)
Vatasescu, Radu (AUTHOR)
Butnariu, Lacramioara Ionela (AUTHOR)
Brinza, Crischentian (AUTHOR)
Burlacu, Alexandru (AUTHOR)
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Źródło:
Diagnostics (2075-4418). Jan2024, Vol. 14 Issue 2, p175. 14p.
Czasopismo naukowe
Tytuł:
Clinical and echocardiographic evolution of patients with arrhythmogenic cardiomyopathy before heart transplantation.
Autorzy:
Rimac G; Department of Cardiology, Institut Universitaire de Cardiologie et Pneumologie de Québec, Québec, Canada.
Poulakos N; Faculty of Medicine, Université Laval, Québec, Canada.
Beaulieu-Shearer A; Faculty of Medicine, Université Laval, Québec, Canada.
Dupuis C; Department of Cardiology, Institut Universitaire de Cardiologie et Pneumologie de Québec, Québec, Canada.
Beaudoin J; Department of Cardiology, Institut Universitaire de Cardiologie et Pneumologie de Québec, Québec, Canada.
Lemay S; Department of Cardiology, Institut Universitaire de Cardiologie et Pneumologie de Québec, Québec, Canada.
Lalancette JS; Department of Cardiology, Institut Universitaire de Cardiologie et Pneumologie de Québec, Québec, Canada.
Trahan S; Department of Pathology, Institut Universitaire de Cardiologie et Pneumologie de Québec, Québec, Canada.
Racine HP; Department of Cardiology, Institut Universitaire de Cardiologie et Pneumologie de Québec, Québec, Canada.
Steinberg C; Department of Cardiology, Institut Universitaire de Cardiologie et Pneumologie de Québec, Québec, Canada.
Sénéchal M; Department of Cardiology, Institut Universitaire de Cardiologie et Pneumologie de Québec, Québec, Canada.
Turgeon PY; Department of Cardiology, Institut Universitaire de Cardiologie et Pneumologie de Québec, Québec, Canada.
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Źródło:
Clinical transplantation [Clin Transplant] 2023 Feb; Vol. 37 (2), pp. e14869. Date of Electronic Publication: 2022 Dec 14.
Typ publikacji:
Journal Article
MeSH Terms:
Arrhythmogenic Right Ventricular Dysplasia*/diagnostic imaging
Arrhythmogenic Right Ventricular Dysplasia*/etiology
Heart Transplantation*/adverse effects
Humans ; Retrospective Studies ; Arrhythmias, Cardiac/etiology ; Echocardiography
Czasopismo naukowe
Tytuł:
Alterations in Calcium Handling Are a Common Feature in an Arrhythmogenic Cardiomyopathy Cell Model Triggered by Desmosome Genes Loss.
Autorzy:
Vallverdú-Prats M; Cardiovascular Genetics Center, Biomedical Research Institute of Girona, 17190 Salt, Spain.
Carreras D; Cardiovascular Genetics Center, Biomedical Research Institute of Girona, 17190 Salt, Spain.
Pérez GJ; Cardiovascular Genetics Center, Biomedical Research Institute of Girona, 17190 Salt, Spain.; Department of Medical Sciences, Universitat de Girona, 17003 Girona, Spain.; Centro de Investigación Biomédica en Red de Enfermedades Cardiovasculares (CIBERCV), 21005 Madrid, Spain.
Campuzano O; Cardiovascular Genetics Center, Biomedical Research Institute of Girona, 17190 Salt, Spain.; Department of Medical Sciences, Universitat de Girona, 17003 Girona, Spain.; Centro de Investigación Biomédica en Red de Enfermedades Cardiovasculares (CIBERCV), 21005 Madrid, Spain.
Brugada R; Cardiovascular Genetics Center, Biomedical Research Institute of Girona, 17190 Salt, Spain.; Department of Medical Sciences, Universitat de Girona, 17003 Girona, Spain.; Centro de Investigación Biomédica en Red de Enfermedades Cardiovasculares (CIBERCV), 21005 Madrid, Spain.; Hospital Josep Trueta, 17007 Girona, Spain.
Alcalde M; Cardiovascular Genetics Center, Biomedical Research Institute of Girona, 17190 Salt, Spain.
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Źródło:
International journal of molecular sciences [Int J Mol Sci] 2023 Jan 20; Vol. 24 (3). Date of Electronic Publication: 2023 Jan 20.
Typ publikacji:
Journal Article
MeSH Terms:
Calcium*
Arrhythmogenic Right Ventricular Dysplasia*/genetics
Arrhythmogenic Right Ventricular Dysplasia*/metabolism
Humans ; Desmosomes/genetics ; Desmosomes/metabolism ; Myocardium/metabolism ; Heart
Czasopismo naukowe
Tytuł:
Epicardial conduction abnormalities in patients with Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) and mutation positive healthy family members - A study using electrocardiographic imaging.
Autorzy:
Kommata V; Department of Medical Sciences, Uppsala University, Uppsala, Sweden.
Sciaraffia E; Department of Medical Sciences, Uppsala University, Uppsala, Sweden.
Blomström-Lundqvist C; Department of Medical Sciences, Uppsala University, Uppsala, Sweden.; Department of Cardiology, School of Medical Sciences, Faculty of Medicine and Health, Örebro University, Örebro, Sweden.
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Źródło:
PloS one [PLoS One] 2023 Jan 05; Vol. 18 (1), pp. e0280111. Date of Electronic Publication: 2023 Jan 05 (Print Publication: 2023).
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Arrhythmogenic Right Ventricular Dysplasia*/diagnostic imaging
Arrhythmogenic Right Ventricular Dysplasia*/genetics
Humans ; Electrocardiography/methods ; Echocardiography ; Heart Ventricles/diagnostic imaging ; Mutation
Czasopismo naukowe
Tytuł:
Evaluation of autoantibodies to desmoglein-2 in dogs with and without cardiac disease.
Autorzy:
Walker AL; William R. Pritchard Veterinary Medical Teaching Hospital, University of California, Davis, CA, USA.
Li RHL; Department of Surgical and Radiological Sciences, School of Veterinary Medicine, University of California, Davis, CA, USA.
Nguyen N; Department of Surgical and Radiological Sciences, School of Veterinary Medicine, University of California, Davis, CA, USA.
Jauregui CE; Department of Medicine and Epidemiology, School of Veterinary Medicine, University of California-Davis, 2108 Tupper Hall, Davis, CA, 95616-8732, USA.
Meurs KM; College of Veterinary Medicine, North Carolina State University, Raleigh, NC, 27604, USA.
Gagnon AL; Department of Medicine and Epidemiology, School of Veterinary Medicine, University of California-Davis, 2108 Tupper Hall, Davis, CA, 95616-8732, USA.
Stern JA; Department of Medicine and Epidemiology, School of Veterinary Medicine, University of California-Davis, 2108 Tupper Hall, Davis, CA, 95616-8732, USA. .
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Źródło:
Scientific reports [Sci Rep] 2023 Mar 28; Vol. 13 (1), pp. 5044. Date of Electronic Publication: 2023 Mar 28.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Arrhythmogenic Right Ventricular Dysplasia*
Dog Diseases*/metabolism
Animals ; Dogs ; Autoantibodies ; Heart Atria ; Prospective Studies ; Desmoglein 2/immunology
Czasopismo naukowe
Tytuł:
Using Zebrafish Animal Model to Study the Genetic Underpinning and Mechanism of Arrhythmogenic Cardiomyopathy.
Autorzy:
Niu Y; The Biomedical Sciences Institute of Qingdao University (Qingdao Branch of SJTU Bio-X Institutes), Qingdao University, Qingdao 266021, China.
Sun Y; The Biomedical Sciences Institute of Qingdao University (Qingdao Branch of SJTU Bio-X Institutes), Qingdao University, Qingdao 266021, China.
Liu Y; School of Public Health, Qingdao University, Qingdao 266021, China.
Du K; School of Public Health, Qingdao University, Qingdao 266021, China.
Xu X; Department of Biochemistry and Molecular Biology, Mayo Clinic, Rochester, MN 55902, USA.
Ding Y; The Biomedical Sciences Institute of Qingdao University (Qingdao Branch of SJTU Bio-X Institutes), Qingdao University, Qingdao 266021, China.; School of Public Health, Qingdao University, Qingdao 266021, China.; Department of Biochemistry and Molecular Biology, Mayo Clinic, Rochester, MN 55902, USA.
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Źródło:
International journal of molecular sciences [Int J Mol Sci] 2023 Feb 18; Vol. 24 (4). Date of Electronic Publication: 2023 Feb 18.
Typ publikacji:
Journal Article; Review
MeSH Terms:
Zebrafish*
Arrhythmogenic Right Ventricular Dysplasia*/genetics
Animals ; Models, Animal ; Arrhythmias, Cardiac ; Death, Sudden, Cardiac
Czasopismo naukowe
Tytuł:
Revisiting the Newly Modified Criteria for Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia (ARVC/D) and Reporting Newly Identified Genes.
Autorzy:
Chang E; Children's Hospital of Michigan, Detroit, MI, USA.
Daboul R; Children's Hospital of Michigan, Detroit, MI, USA.
Hanan A; Children's Hospital of Michigan, Detroit, MI, USA.
Abdo M; Children's Hospital of Michigan, Detroit, MI, USA.
Poulik J; Children's Hospital of Michigan, Detroit, MI, USA.
Eskarous H; Children's Hospital of Michigan, Detroit, MI, USA.
Hadjilambris AM; Children's Hospital of Michigan, Detroit, MI, USA.
Shehata BM; Children's Hospital of Michigan, Detroit, MI, USA.
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Źródło:
Fetal and pediatric pathology [Fetal Pediatr Pathol] 2022 Dec; Vol. 41 (6), pp. 909-918. Date of Electronic Publication: 2021 Dec 02.
Typ publikacji:
Journal Article
MeSH Terms:
Arrhythmogenic Right Ventricular Dysplasia*/diagnosis
Arrhythmogenic Right Ventricular Dysplasia*/genetics
Adult ; Child ; Humans ; Genetic Testing
Czasopismo naukowe
Tytuł:
Activation of PPARα Ameliorates Cardiac Fibrosis in Dsg2-Deficient Arrhythmogenic Cardiomyopathy.
Autorzy:
Qiu Z; Department of Physiology, School of Medicine, Jinan University, 601 Huangpu Avenue West, Tianhe District, Guangzhou 510632, China.
Zhao Y; Department of Physiology, School of Medicine, Jinan University, 601 Huangpu Avenue West, Tianhe District, Guangzhou 510632, China.
Tao T; Department of Physiology, School of Medicine, Jinan University, 601 Huangpu Avenue West, Tianhe District, Guangzhou 510632, China.
Guo W; Department of Physiology, School of Medicine, Jinan University, 601 Huangpu Avenue West, Tianhe District, Guangzhou 510632, China.
Liu R; Department of Physiology, School of Medicine, Jinan University, 601 Huangpu Avenue West, Tianhe District, Guangzhou 510632, China.
Huang J; Department of Physiology, School of Medicine, Jinan University, 601 Huangpu Avenue West, Tianhe District, Guangzhou 510632, China.
Xu G; Department of Physiology, School of Medicine, Jinan University, 601 Huangpu Avenue West, Tianhe District, Guangzhou 510632, China.; Center for Clinical Epidemiology and Methodology (CCEM), Guangdong Second Provincial General Hospital, Guangzhou 510317, China.
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Źródło:
Cells [Cells] 2022 Oct 11; Vol. 11 (20). Date of Electronic Publication: 2022 Oct 11.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Desmoglein 2*/genetics
Desmoglein 2*/metabolism
PPAR alpha*/genetics
PPAR alpha*/metabolism
Arrhythmogenic Right Ventricular Dysplasia*/genetics
Arrhythmogenic Right Ventricular Dysplasia*/pathology
Myocardium*/pathology
Animals ; Mice ; Biomarkers/metabolism ; Disease Models, Animal ; Fenofibrate/pharmacology ; Fibrosis ; Myocytes, Cardiac/metabolism ; Proto-Oncogene Proteins c-akt/metabolism ; RNA, Small Interfering/metabolism ; Collagen Type I/metabolism
Czasopismo naukowe
Tytuł:
致心律失常型右心室心肌病患者冠状动脉病变与心脏病理和 心肌代谢组学的关系
Autorzy:
陈凯
陈晓
张宁宁
常远
陈实
胡振良
宋伸
宋江平
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Alternatywny tytuł:
The relationship between coronary artery disease, cardiac pathology and myocardial metabolomics in patients with arrhythmogenic right ventricular cardiomyopathy.
Źródło:
Chinese Journal of Arteriosclerosis. Oct2023, Vol. 31 Issue 10, p841-848. 8p.
Czasopismo naukowe

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