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Wyszukujesz frazę ""Creutzfeldt-Jakob Syndrome"" wg kryterium: Temat


Tytuł:
Anti-prion drugs do not improve survival in novel knock-in models of inherited prion disease.
Autorzy:
Walsh DJ; Department of Biochemistry and Cell Biology Geisel School of Medicine at Dartmouth, Hanover, New Hampshire, United States of America.
Rees JR; Department of Epidemiology Geisel School of Medicine at Dartmouth, Hanover, New Hampshire, United States of America.; Department of Community and Family Medicine Geisel School of Medicine at Dartmouth, Hanover, New Hampshire, United States of America.
Mehra S; Tanz Centre for Research in Neurodegenerative Diseases, University of Toronto, Toronto, Ontario, Canada.
Bourkas MEC; Tanz Centre for Research in Neurodegenerative Diseases, University of Toronto, Toronto, Ontario, Canada.; Department of Biochemistry, University of Toronto, Toronto, Ontario, Canada.
Kaczmarczyk L; Wallenberg Center for Molecular Medicine, Department of Biomedical and Clinical Sciences, Linköping University, Linköping, Sweden.
Stuart E; Tanz Centre for Research in Neurodegenerative Diseases, University of Toronto, Toronto, Ontario, Canada.; Department of Biochemistry, University of Toronto, Toronto, Ontario, Canada.
Jackson WS; Wallenberg Center for Molecular Medicine, Department of Biomedical and Clinical Sciences, Linköping University, Linköping, Sweden.
Watts JC; Tanz Centre for Research in Neurodegenerative Diseases, University of Toronto, Toronto, Ontario, Canada.; Department of Biochemistry, University of Toronto, Toronto, Ontario, Canada.
Supattapone S; Department of Biochemistry and Cell Biology Geisel School of Medicine at Dartmouth, Hanover, New Hampshire, United States of America.; Department of Medicine, Geisel School of Medicine at Dartmouth, Hanover, New Hampshire, United States of America.
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Źródło:
PLoS pathogens [PLoS Pathog] 2024 Apr 01; Vol. 20 (4), pp. e1012087. Date of Electronic Publication: 2024 Apr 01 (Print Publication: 2024).
Typ publikacji:
Journal Article
MeSH Terms:
Prions*/metabolism
Prion Diseases*/drug therapy
Prion Diseases*/genetics
Prion Diseases*/metabolism
Creutzfeldt-Jakob Syndrome*/drug therapy
Creutzfeldt-Jakob Syndrome*/genetics
Creutzfeldt-Jakob Syndrome*/metabolism
Animals ; Mice ; Prion Proteins/genetics ; Prion Proteins/metabolism ; Brain/pathology ; Arvicolinae/metabolism
Czasopismo naukowe
Tytuł:
Detection of prions in matching post-mortem skin and cerebrospinal fluid samples using second-generation real-time quaking-induced conversion assay.
Autorzy:
Baranová S; Institute of Immunology and Microbiology, First Faculty of Medicine, Charles University, Prague, Czech Republic.
Moško T; Institute of Immunology and Microbiology, First Faculty of Medicine, Charles University, Prague, Czech Republic.
Brůžová M; Department of Pathology and Molecular Medicine, Third Faculty of Medicine, Charles University and Thomayer University Hospital, Prague, Czech Republic.
Haldiman T; Department of Pathology, Case Western Reserve University School of Medicine, Cleveland, OH, 44106, USA.; Department Neurology, Case Western Reserve University School of Medicine, Cleveland, OH, 44106, USA.
Kim C; Department of Pathology, Case Western Reserve University School of Medicine, Cleveland, OH, 44106, USA.; Department Neurology, Case Western Reserve University School of Medicine, Cleveland, OH, 44106, USA.
Safar JG; Department of Pathology, Case Western Reserve University School of Medicine, Cleveland, OH, 44106, USA.; Department Neurology, Case Western Reserve University School of Medicine, Cleveland, OH, 44106, USA.
Matěj R; Department of Pathology and Molecular Medicine, Third Faculty of Medicine, Charles University and Thomayer University Hospital, Prague, Czech Republic.; Department of Pathology, Third Faculty of Medicine, Charles University and University Hospital Kralovske Vinohrady, Prague, Czech Republic.; Department of Pathology, First Faculty of Medicine, Charles University and General University Hospital, Prague, Czech Republic.
Holada K; Institute of Immunology and Microbiology, First Faculty of Medicine, Charles University, Prague, Czech Republic. .
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Źródło:
Scientific reports [Sci Rep] 2024 Mar 15; Vol. 14 (1), pp. 6294. Date of Electronic Publication: 2024 Mar 15.
Typ publikacji:
Journal Article
MeSH Terms:
Prions*/metabolism
Prion Diseases*/diagnosis
Creutzfeldt-Jakob Syndrome*/diagnosis
Creutzfeldt-Jakob Syndrome*/cerebrospinal fluid
Humans ; Skin/metabolism ; Prion Proteins ; Biological Assay
Czasopismo naukowe
Tytuł:
Detection limitations of prion seeding activities in blood samples from patients with sporadic prion disease.
Autorzy:
Nonaka T; Division of Cellular and Molecular Biology, Nagasaki University Graduate School of Biomedical Sciences, Nagasaki City, 852-8501, Japan.
Iwasaki Y; Department of Neuropathology, Institute for Medical Science of Aging, Aichi Medical University, Nagakute City, 480-1195, Japan.
Horiuchi H; Laboratory of Immunobiology, Graduate School of Integrated Sciences for Life, Hiroshima University, Higashihiroshima City, Japan.
Satoh K; Department of Health Sciences, Unit of Medical and Dental Sciences, Nagasaki University Graduate School of Biomedical Sciences, Nagasaki City, Japan. .
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Źródło:
BMC neurology [BMC Neurol] 2024 Mar 11; Vol. 24 (1), pp. 92. Date of Electronic Publication: 2024 Mar 11.
Typ publikacji:
Journal Article
MeSH Terms:
Prions*/metabolism
Prion Diseases*/diagnosis
Prion Diseases*/metabolism
Creutzfeldt-Jakob Syndrome*/diagnosis
Humans ; Prion Proteins ; Brain/metabolism ; Plasma/metabolism
Czasopismo naukowe
Tytuł:
New Light on Prions: Putative Role of PrP in Pathophysiology of Mood Disorders.
Autorzy:
Chrobak AA; Department of Adult Psychiatry, Jagiellonian University Medical College, Kopernika 21A, 31-501 Kraków, Poland.
Pańczyszyn-Trzewik P; Department of Human Physiology, Institute of Medical Sciences, Medical College of Rzeszow University, Kopisto 2a, 35-959 Rzeszow, Poland.
Król P; Department of Adult Psychiatry, Jagiellonian University Medical College, Kopernika 21A, 31-501 Kraków, Poland.
Pawelec-Bąk M; Department of Affective Disorders, Jagiellonian University Medical College, Kopernika 21A, 31-501 Kraków, Poland.
Dudek D; Department of Adult Psychiatry, Jagiellonian University Medical College, Kopernika 21A, 31-501 Kraków, Poland.
Siwek M; Department of Affective Disorders, Jagiellonian University Medical College, Kopernika 21A, 31-501 Kraków, Poland.
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Źródło:
International journal of molecular sciences [Int J Mol Sci] 2024 Mar 04; Vol. 25 (5). Date of Electronic Publication: 2024 Mar 04.
Typ publikacji:
Journal Article; Review
MeSH Terms:
Creutzfeldt-Jakob Syndrome*/metabolism
Prions*/metabolism
PrPC Proteins*
Humans ; Mood Disorders ; Neuronal Plasticity ; Synaptic Transmission
Czasopismo naukowe
Tytuł:
Development of statistical auto-segmentation method for diffusion restriction gray matter lesions in patients with newly diagnosed sporadic Creutzfeldt-Jakob disease.
Autorzy:
Heo H; Department of Convergence Medicine, Asan Medical Center, University of Ulsan College of Medicine, Seoul, 05505, Republic of Korea.
Park HY; Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, 05505, Republic of Korea.
Suh CH; Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, 05505, Republic of Korea. .
Shim WH; Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, 05505, Republic of Korea.
Lim JS; Department of Neurology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Republic of Korea.
Lee JH; Department of Neurology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Republic of Korea.
Kim SJ; Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, 05505, Republic of Korea.
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Źródło:
Scientific reports [Sci Rep] 2024 Feb 20; Vol. 14 (1), pp. 4215. Date of Electronic Publication: 2024 Feb 20.
Typ publikacji:
Journal Article
MeSH Terms:
Gray Matter*/diagnostic imaging
Gray Matter*/pathology
Creutzfeldt-Jakob Syndrome*/pathology
Humans ; Diffusion Magnetic Resonance Imaging/methods ; Algorithms ; Magnetic Resonance Imaging/methods
SCR Disease Name:
Creutzfeldt-Jakob Disease, Sporadic
Czasopismo naukowe
Tytuł:
Personalized brain MRI revealed distinct functional and anatomical disruptions in Creutzfeldt-Jakob disease and Alzheimer's disease.
Autorzy:
Guo Y; Department of Neurology, Beijing Tongren Hospital, Capital Medical University, Beijing, China.
Ren J; Changping Laboratory, Beijing, China.
Cui W; School of Engineering Medicine, Beihang University, Beijing, China.
Dahmani L; Department of Radiology, Athinoula A. Martinos Center for Biomedical Imaging, Massachusetts General Hospital, Harvard Medical School, Charlestown, Massachusetts, USA.
Wang D; Department of Radiology, Athinoula A. Martinos Center for Biomedical Imaging, Massachusetts General Hospital, Harvard Medical School, Charlestown, Massachusetts, USA.
Fu X; Changping Laboratory, Beijing, China.
Li M; Changping Laboratory, Beijing, China.
Li S; Changping Laboratory, Beijing, China.
Zhang Y; Department of Radiology, Beijing Friendship Hospital, Capital Medical University, Beijing, China.
Lin X; Department of Neurology, Beijing Tongren Hospital, Capital Medical University, Beijing, China.
Zhen Z; Department of Neurology, Beijing Tongren Hospital, Capital Medical University, Beijing, China.
Xu Y; Department of Neurosurgery, Beijing Tiantan Hospital, Capital Medical University, Beijing, China.
Xie D; Department of Neurology, Beijing Friendship Hospital, Capital Medical University, Beijing, China.
Guan H; Department of Neurology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences, Beijing, China.
Yi F; Department of Neurology, Lishilu Outpatient, Jingzhong Medical District, Chinese PLA General Hospital, Beijing, China.
Wang J; Department of Neurology, Beijing Tongren Hospital, Capital Medical University, Beijing, China.
Shi Q; State Key Laboratory for Infectious Disease Prevention and Control, National Institute for Viral Disease Control and Prevention, Chinese Center for Disease Control and Prevention, Beijing, China.
Liu H; Changping Laboratory, Beijing, China.; Biomedical Pioneering Innovation Center, Peking University, Beijing, China.
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Źródło:
CNS neuroscience & therapeutics [CNS Neurosci Ther] 2024 Feb; Vol. 30 (2), pp. e14404. Date of Electronic Publication: 2023 Aug 14.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Alzheimer Disease*/pathology
Creutzfeldt-Jakob Syndrome*/diagnostic imaging
Creutzfeldt-Jakob Syndrome*/complications
Creutzfeldt-Jakob Syndrome*/pathology
Humans ; Cerebral Cortical Thinning/pathology ; Brain/pathology ; Magnetic Resonance Imaging ; Atrophy/complications ; Atrophy/pathology
Czasopismo naukowe
Tytuł:
Neural cell engraftment therapy for sporadic Creutzfeldt-Jakob disease restores neuroelectrophysiological parameters in a cerebral organoid model.
Autorzy:
Williams K; Laboratory of Neurological Infections and Immunity, National Institute of Allergy and Infectious Diseases, Division of Intramural Research, Rocky Mountain Laboratories, National Institutes of Health, 903 South 4Th Street, Hamilton, MT, 59840, USA.
Foliaki ST; Laboratory of Neurological Infections and Immunity, National Institute of Allergy and Infectious Diseases, Division of Intramural Research, Rocky Mountain Laboratories, National Institutes of Health, 903 South 4Th Street, Hamilton, MT, 59840, USA.
Race B; Laboratory of Neurological Infections and Immunity, National Institute of Allergy and Infectious Diseases, Division of Intramural Research, Rocky Mountain Laboratories, National Institutes of Health, 903 South 4Th Street, Hamilton, MT, 59840, USA.
Smith A; Laboratory of Neurological Infections and Immunity, National Institute of Allergy and Infectious Diseases, Division of Intramural Research, Rocky Mountain Laboratories, National Institutes of Health, 903 South 4Th Street, Hamilton, MT, 59840, USA.
Thomas T; Rocky Mountain Veterinary Branch, National Institute of Allergy and Infectious Diseases, Division of Intramural Research, Rocky Mountain Laboratories, National Institutes of Health, 903 South 4Th Street, Hamilton, MT, 59840, USA.
Groveman BR; Laboratory of Neurological Infections and Immunity, National Institute of Allergy and Infectious Diseases, Division of Intramural Research, Rocky Mountain Laboratories, National Institutes of Health, 903 South 4Th Street, Hamilton, MT, 59840, USA.
Haigh CL; Laboratory of Neurological Infections and Immunity, National Institute of Allergy and Infectious Diseases, Division of Intramural Research, Rocky Mountain Laboratories, National Institutes of Health, 903 South 4Th Street, Hamilton, MT, 59840, USA. .
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Źródło:
Stem cell research & therapy [Stem Cell Res Ther] 2023 Dec 05; Vol. 14 (1), pp. 348. Date of Electronic Publication: 2023 Dec 05.
Typ publikacji:
Journal Article
MeSH Terms:
Creutzfeldt-Jakob Syndrome*/therapy
Neurodegenerative Diseases*
Prions*
Prion Diseases*
Animals ; Humans ; Organoids
SCR Disease Name:
Creutzfeldt-Jakob Disease, Sporadic
Czasopismo naukowe
Tytuł:
Detection of prions in the urine of patients affected by sporadic Creutzfeldt-Jakob disease.
Autorzy:
Pritzkow S; Department of Neurology, Mitchell Center for Alzheimer's Disease and Related Brain Disorders, University of Texas McGovern Medical School at Houston, Houston, Texas, USA.
Ramirez F; Department of Neurology, Mitchell Center for Alzheimer's Disease and Related Brain Disorders, University of Texas McGovern Medical School at Houston, Houston, Texas, USA.
Lyon A; Department of Neurology, Mitchell Center for Alzheimer's Disease and Related Brain Disorders, University of Texas McGovern Medical School at Houston, Houston, Texas, USA.
Schulz PE; Department of Neurology, Mitchell Center for Alzheimer's Disease and Related Brain Disorders, University of Texas McGovern Medical School at Houston, Houston, Texas, USA.
Appleby B; Department of Pathology, Case Western Reserve University, Cleveland, Ohio, USA.
Moda F; Division of Neurology 5 - Neuropathology, Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy.
Ramirez S; Department of Neurology, Mitchell Center for Alzheimer's Disease and Related Brain Disorders, University of Texas McGovern Medical School at Houston, Houston, Texas, USA.
Notari S; Department of Pathology, Case Western Reserve University, Cleveland, Ohio, USA.
Gambetti P; Department of Pathology, Case Western Reserve University, Cleveland, Ohio, USA.
Soto C; Department of Neurology, Mitchell Center for Alzheimer's Disease and Related Brain Disorders, University of Texas McGovern Medical School at Houston, Houston, Texas, USA.
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Źródło:
Annals of clinical and translational neurology [Ann Clin Transl Neurol] 2023 Dec; Vol. 10 (12), pp. 2316-2323. Date of Electronic Publication: 2023 Oct 10.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't; Research Support, N.I.H., Extramural
MeSH Terms:
Creutzfeldt-Jakob Syndrome*/diagnosis
Prions*
Humans ; Brain/metabolism
SCR Disease Name:
Creutzfeldt-Jakob Disease, Sporadic
Czasopismo naukowe
Tytuł:
Development of a sensitive real-time quaking-induced conversion (RT-QuIC) assay for application in prion-infected blood.
Autorzy:
Thomas CM; The Roslin Institute, Royal (Dick) School of Veterinary Studies, University of Edinburgh, Easter Bush Campus, Midlothian, United Kingdom.
Salamat MKF; The Roslin Institute, Royal (Dick) School of Veterinary Studies, University of Edinburgh, Easter Bush Campus, Midlothian, United Kingdom.
de Wolf C; The Roslin Institute, Royal (Dick) School of Veterinary Studies, University of Edinburgh, Easter Bush Campus, Midlothian, United Kingdom.
McCutcheon S; The Roslin Institute, Royal (Dick) School of Veterinary Studies, University of Edinburgh, Easter Bush Campus, Midlothian, United Kingdom.
Blanco ARA; The Roslin Institute, Royal (Dick) School of Veterinary Studies, University of Edinburgh, Easter Bush Campus, Midlothian, United Kingdom.
Manson JC; The Roslin Institute, Royal (Dick) School of Veterinary Studies, University of Edinburgh, Easter Bush Campus, Midlothian, United Kingdom.
Hunter N; The Roslin Institute, Royal (Dick) School of Veterinary Studies, University of Edinburgh, Easter Bush Campus, Midlothian, United Kingdom.
Houston EF; The Roslin Institute, Royal (Dick) School of Veterinary Studies, University of Edinburgh, Easter Bush Campus, Midlothian, United Kingdom.
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Źródło:
PloS one [PLoS One] 2023 Nov 02; Vol. 18 (11), pp. e0293845. Date of Electronic Publication: 2023 Nov 02 (Print Publication: 2023).
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Prions*/metabolism
Creutzfeldt-Jakob Syndrome*/diagnosis
Creutzfeldt-Jakob Syndrome*/metabolism
Encephalopathy, Bovine Spongiform*/diagnosis
Encephalopathy, Bovine Spongiform*/metabolism
Cattle ; Mice ; Humans ; Animals ; Sheep ; Brain/metabolism ; Prion Proteins/metabolism
Czasopismo naukowe
Tytuł:
The rapid progression of Creutzfeldt-Jakob disease with concomitant COVID-19 infection: a case report.
Autorzy:
McGrath A; University Hospitals of Derby and Burton NHS Foundation Trust.
Pai H; University Hospitals of Derby and Burton NHS Foundation Trust.
Clack A; University Hospitals of Derby and Burton NHS Foundation Trust.
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Źródło:
Clinical medicine (London, England) [Clin Med (Lond)] 2023 Nov; Vol. 23 Suppl 6, pp. 21-22.
Typ publikacji:
Case Reports; Journal Article
MeSH Terms:
Creutzfeldt-Jakob Syndrome*/complications
Creutzfeldt-Jakob Syndrome*/diagnosis
COVID-19*
Humans
Czasopismo naukowe
Tytuł:
Elevated E200K Somatic Mutation of the Prion Protein Gene ( PRNP ) in the Brain Tissues of Patients with Sporadic Creutzfeldt-Jakob Disease (CJD).
Autorzy:
Won SY; Korea Zoonosis Research Institute, Jeonbuk National University, 820-120, Hana-ro, Iksan 54531, Republic of Korea.; Department of Bioactive Material Sciences, Institute for Molecular Biology and Genetics, Jeonbuk National University, Jeonju 54896, Republic of Korea.
Kim YC; Department of Biological Sciences, Andong National University, Andong 36729, Republic of Korea.
Jeong BH; Korea Zoonosis Research Institute, Jeonbuk National University, 820-120, Hana-ro, Iksan 54531, Republic of Korea.; Department of Bioactive Material Sciences, Institute for Molecular Biology and Genetics, Jeonbuk National University, Jeonju 54896, Republic of Korea.
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Źródło:
International journal of molecular sciences [Int J Mol Sci] 2023 Oct 02; Vol. 24 (19). Date of Electronic Publication: 2023 Oct 02.
Typ publikacji:
Journal Article
MeSH Terms:
Prions*/genetics
Prions*/metabolism
Creutzfeldt-Jakob Syndrome*/genetics
Creutzfeldt-Jakob Syndrome*/metabolism
Neurodegenerative Diseases*
Humans ; Prion Proteins/genetics ; Prion Proteins/metabolism ; Brain/metabolism ; Mutation
SCR Disease Name:
Acquired CJD; Creutzfeldt-Jakob Disease, Sporadic
Czasopismo naukowe
Tytuł:
Diagnostic challenge of Creutzfeldt-Jakob disease in a patient with multimorbidity: a case-report.
Autorzy:
Yaqub A; Department of Epidemiology, Erasmus University Medical Center, Rotterdam, the Netherlands.
Ikram MK; Department of Epidemiology, Erasmus University Medical Center, Rotterdam, the Netherlands.; Department of Neurology, Erasmus University Medical Center, Rotterdam, the Netherlands.
Blankevoort J; Department of Neurology, Flevoziekenhuis, Almere, the Netherlands.
Ikram MA; Department of Epidemiology, Erasmus University Medical Center, Rotterdam, the Netherlands. .
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Źródło:
BMC neurology [BMC Neurol] 2023 Oct 02; Vol. 23 (1), pp. 346. Date of Electronic Publication: 2023 Oct 02.
Typ publikacji:
Case Reports; Journal Article
MeSH Terms:
Creutzfeldt-Jakob Syndrome*/complications
Creutzfeldt-Jakob Syndrome*/diagnosis
Akinetic Mutism*/complications
Churg-Strauss Syndrome*/complications
Myoclonus*/complications
Situs Inversus*/complications
Humans ; Male ; Multimorbidity
Czasopismo naukowe
Tytuł:
High diagnostic performance of plasma and cerebrospinal fluid beta-synuclein for sporadic Creutzfeldt-Jakob disease.
Autorzy:
Abu-Rumeileh S; Department of Neurology, Martin-Luther-University Halle-Wittenberg, Halle (Saale), Germany.
Halbgebauer S; Department of Neurology, Ulm University Hospital, Ulm, Germany.; German Center for Neurodegenerative Diseases (DZNE e.V.), Ulm, Germany.
Bentivenga GM; Department of Biomedical and Neuromotor Sciences (DIBINEM), University of Bologna, Bologna, Italy.
Barba L; Department of Neurology, Martin-Luther-University Halle-Wittenberg, Halle (Saale), Germany.
Baiardi S; Department of Biomedical and Neuromotor Sciences (DIBINEM), University of Bologna, Bologna, Italy.; IRCCS Istituto delle Scienze Neurologiche di Bologna, Bologna, Italy.
Mastrangelo A; Department of Biomedical and Neuromotor Sciences (DIBINEM), University of Bologna, Bologna, Italy.
Oeckl P; Department of Neurology, Ulm University Hospital, Ulm, Germany.; German Center for Neurodegenerative Diseases (DZNE e.V.), Ulm, Germany.
Steinacker P; Department of Neurology, Martin-Luther-University Halle-Wittenberg, Halle (Saale), Germany.
Mammana A; Department of Biomedical and Neuromotor Sciences (DIBINEM), University of Bologna, Bologna, Italy.; IRCCS Istituto delle Scienze Neurologiche di Bologna, Bologna, Italy.
Capellari S; Department of Biomedical and Neuromotor Sciences (DIBINEM), University of Bologna, Bologna, Italy.; IRCCS Istituto delle Scienze Neurologiche di Bologna, Bologna, Italy.
Otto M; Department of Neurology, Martin-Luther-University Halle-Wittenberg, Halle (Saale), Germany.
Parchi P; Department of Biomedical and Neuromotor Sciences (DIBINEM), University of Bologna, Bologna, Italy.; IRCCS Istituto delle Scienze Neurologiche di Bologna, Bologna, Italy.
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Źródło:
Annals of clinical and translational neurology [Ann Clin Transl Neurol] 2023 Oct; Vol. 10 (10), pp. 1904-1909. Date of Electronic Publication: 2023 Aug 08.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Creutzfeldt-Jakob Syndrome*/diagnosis
Creutzfeldt-Jakob Syndrome*/cerebrospinal fluid
Humans ; beta-Synuclein ; 14-3-3 Proteins/cerebrospinal fluid ; Biomarkers/cerebrospinal fluid
SCR Disease Name:
Creutzfeldt-Jakob Disease, Sporadic
Czasopismo naukowe
Tytuł:
Diagnostic and prognostic value of cerebrospinal fluid SNAP-25 and neurogranin in Creutzfeldt-Jakob disease in a clinical setting cohort of rapidly progressive dementias.
Autorzy:
Bentivenga GM; Department of Biomedical and Neuromotor Sciences (DiBiNeM), University of Bologna, Bologna, Italy.
Baiardi S; Department of Biomedical and Neuromotor Sciences (DiBiNeM), University of Bologna, Bologna, Italy.
Mastrangelo A; Department of Biomedical and Neuromotor Sciences (DiBiNeM), University of Bologna, Bologna, Italy.
Zenesini C; IRCCS, Istituto delle Scienze Neurologiche di Bologna, Programma Neuropatologia delle Malattie Neurodegenerative, Bologna, Italy.
Mammana A; IRCCS, Istituto delle Scienze Neurologiche di Bologna, Programma Neuropatologia delle Malattie Neurodegenerative, Bologna, Italy.
Polischi B; IRCCS, Istituto delle Scienze Neurologiche di Bologna, Programma Neuropatologia delle Malattie Neurodegenerative, Bologna, Italy.
Capellari S; Department of Biomedical and Neuromotor Sciences (DiBiNeM), University of Bologna, Bologna, Italy.; IRCCS, Istituto delle Scienze Neurologiche di Bologna, Programma Neuropatologia delle Malattie Neurodegenerative, Bologna, Italy.
Parchi P; Department of Biomedical and Neuromotor Sciences (DiBiNeM), University of Bologna, Bologna, Italy. .; IRCCS, Istituto delle Scienze Neurologiche di Bologna, Programma Neuropatologia delle Malattie Neurodegenerative, Bologna, Italy. .
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Źródło:
Alzheimer's research & therapy [Alzheimers Res Ther] 2023 Sep 08; Vol. 15 (1), pp. 150. Date of Electronic Publication: 2023 Sep 08.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Creutzfeldt-Jakob Syndrome*/diagnosis
Prions*
Humans ; Neurogranin ; Prognosis ; Synaptosomal-Associated Protein 25 ; Retrospective Studies
Czasopismo naukowe
Tytuł:
Understanding the key features of the spontaneous formation of bona fide prions through a novel methodology that enables their swift and consistent generation.
Autorzy:
Eraña H; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.; ATLAS Molecular Pharma S. L. Bizkaia Technology Park, 48160, Derio, Spain.; Centro de Investigación Biomédica en Red de Enfermedades Infecciosas (CIBERINFEC), Carlos III National Health Institute, 28029, Madrid, Spain.
Díaz-Domínguez CM; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.; Centro de Investigación Biomédica en Red de Enfermedades Infecciosas (CIBERINFEC), Carlos III National Health Institute, 28029, Madrid, Spain.
Charco JM; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.; ATLAS Molecular Pharma S. L. Bizkaia Technology Park, 48160, Derio, Spain.; Centro de Investigación Biomédica en Red de Enfermedades Infecciosas (CIBERINFEC), Carlos III National Health Institute, 28029, Madrid, Spain.
Vidal E; IRTA, Programa de Sanitat Animal, Centre de Recerca en Sanitat Animal (CReSA), Campus de la Universitat Autònoma de Barcelona (UAB), Bellaterra, Catalonia, Spain.
González-Miranda E; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
Pérez-Castro MA; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
Piñeiro P; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
López-Moreno R; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
Sampedro-Torres-Quevedo C; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
Fernández-Veiga L; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
Tasis-Galarza J; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
Lorenzo NL; CIMUS Biomedical Research Institute and Department of Medical Sciences, University of Santiago de Compostela-IDIS, 15782, Santiago de Compostela, Spain.
Santini-Santiago A; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
Lázaro M; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
García-Martínez S; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
Gonçalves-Anjo N; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
San-Juan-Ansoleaga M; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
Galarza-Ahumada J; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
Fernández-Muñoz E; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
Giler S; IRTA, Programa de Sanitat Animal, Centre de Recerca en Sanitat Animal (CReSA), Campus de la Universitat Autònoma de Barcelona (UAB), Bellaterra, Catalonia, Spain.
Valle M; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain.
Telling GC; Prion Research Center (PRC), Colorado State University, Fort Collins, CO, 80523, USA.
Geijó M; Animal Health Department, NEIKER-Basque Institute for Agricultural Research and Development, Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Spain.
Requena JR; CIMUS Biomedical Research Institute and Department of Medical Sciences, University of Santiago de Compostela-IDIS, 15782, Santiago de Compostela, Spain.
Castilla J; Center for Cooperative Research in Biosciences (CIC bioGUNE), Basque Research and Technology Alliance (BRTA), Bizkaia Technology Park, 48160, Derio, Bizkaia, Spain. .; Centro de Investigación Biomédica en Red de Enfermedades Infecciosas (CIBERINFEC), Carlos III National Health Institute, 28029, Madrid, Spain. .; IKERBASQUE, Basque Foundation for Science, 48011, Bilbao, Spain. .
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Źródło:
Acta neuropathologica communications [Acta Neuropathol Commun] 2023 Sep 07; Vol. 11 (1), pp. 145. Date of Electronic Publication: 2023 Sep 07.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Prions*
Creutzfeldt-Jakob Syndrome*
Humans ; Magnetic Resonance Imaging ; Tremor
Czasopismo naukowe
Tytuł:
Respıratuar Changes ın Creutzfeldt-Jakob Dısease: Bıot Lıke Respıratuar Pattern.
Autorzy:
Aysenur I; Neurology Department, Meram Medıcıne Faculty Hospıtal, Necmettın Erbakan Unıversıty, Konya, Turkey.
Huseyın KH; Neurology Department, Meram Medıcıne Faculty Hospıtal, Necmettın Erbakan Unıversıty, Konya, Turkey.
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Źródło:
Neurology India [Neurol India] 2023 Sep-Oct; Vol. 71 (5), pp. 1068-1069.
Typ publikacji:
Letter
MeSH Terms:
Creutzfeldt-Jakob Syndrome*
Humans ; Electroencephalography
Opinia redakcyjna
Tytuł:
Novel histotypes of sporadic Creutzfeldt-Jakob disease linked to 129MV genotype.
Autorzy:
Cracco L; Department of Pathology and Laboratory Medicine, School of Medicine, Indiana University, Indianapolis, IN, 46202, USA.
Puoti G; Division of Neurology, University of Campania 'Luigi Vanvitelli', Caserta, Italy.
Cornacchia A; Department of Pathology, School of Medicine, Case Western Reserve University, Cleveland, OH, 44106, USA.
Glisic K; National Prion Disease Pathology Surveillance Center, Cleveland, OH, 44106, USA.
Lee SK; Department of Physiology and Biophysics, School of Medicine, Case Western Reserve University, Cleveland, OH, 44106, USA.
Wang Z; Department of Pathology, School of Medicine, Case Western Reserve University, Cleveland, OH, 44106, USA.
Cohen ML; Department of Pathology, School of Medicine, Case Western Reserve University, Cleveland, OH, 44106, USA.; National Prion Disease Pathology Surveillance Center, Cleveland, OH, 44106, USA.
Appleby BS; Department of Pathology, School of Medicine, Case Western Reserve University, Cleveland, OH, 44106, USA.; National Prion Disease Pathology Surveillance Center, Cleveland, OH, 44106, USA.; Department of Neurology, School of Medicine, Case Western Reserve University, Cleveland, OH, 44106, USA.; Department of Psychiatry, School of Medicine, Case Western Reserve University, Cleveland, OH, 44106, USA.
Cali I; Department of Pathology, School of Medicine, Case Western Reserve University, Cleveland, OH, 44106, USA. .; National Prion Disease Pathology Surveillance Center, Cleveland, OH, 44106, USA. .
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Źródło:
Acta neuropathologica communications [Acta Neuropathol Commun] 2023 Aug 31; Vol. 11 (1), pp. 141. Date of Electronic Publication: 2023 Aug 31.
Typ publikacji:
Journal Article; Research Support, U.S. Gov't, P.H.S.; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
MeSH Terms:
Creutzfeldt-Jakob Syndrome*/genetics
Kuru*
Prions*
Humans ; Genotype ; Prion Proteins/genetics ; Plaque, Amyloid
SCR Disease Name:
Creutzfeldt-Jakob Disease, Sporadic
Czasopismo naukowe
Tytuł:
Efficacy of Wex-cide 128 disinfectant against multiple prion strains.
Autorzy:
Baune C; The Laboratory of Neurological Infections and Immunity, Rocky Mountain Laboratories, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Hamilton, Montana, United States of America.
Groveman BR; The Laboratory of Neurological Infections and Immunity, Rocky Mountain Laboratories, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Hamilton, Montana, United States of America.
Hughson AG; The Laboratory of Neurological Infections and Immunity, Rocky Mountain Laboratories, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Hamilton, Montana, United States of America.
Thomas T; Rocky Mountain Veterinary Branch, Rocky Mountain Laboratories, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Hamilton, Montana, United States of America.
Twardoski B; Office of Operations Management, Rocky Mountain Laboratories, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Hamilton, Montana, United States of America.
Priola S; The Laboratory of Neurological Infections and Immunity, Rocky Mountain Laboratories, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Hamilton, Montana, United States of America.
Chesebro B; The Laboratory of Neurological Infections and Immunity, Rocky Mountain Laboratories, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Hamilton, Montana, United States of America.
Race B; The Laboratory of Neurological Infections and Immunity, Rocky Mountain Laboratories, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Hamilton, Montana, United States of America.
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Źródło:
PloS one [PLoS One] 2023 Aug 24; Vol. 18 (8), pp. e0290325. Date of Electronic Publication: 2023 Aug 24 (Print Publication: 2023).
Typ publikacji:
Journal Article; Research Support, N.I.H., Intramural
MeSH Terms:
Prions*
Creutzfeldt-Jakob Syndrome*
Scrapie*
Deer*
Disinfectants*/pharmacology
Sprains and Strains*
Cricetinae ; Humans ; Animals ; Cattle ; Mice ; Sheep ; Brain ; Phenols
Czasopismo naukowe
Tytuł:
Metabolic Brain Changes Can Predict the Underlying Pathology in Neurodegenerative Brain Disorders: A Case Report of Sporadic Creutzfeldt-Jakob Disease with Concomitant Parkinson's Disease.
Autorzy:
Rus T; Department of Neurology, University Medical Center Ljubljana, Zaloška cesta 2a, 1000 Ljubljana, Slovenia.
Mlakar J; Institute of Pathology, Medical Faculty, University of Ljubljana, Korytkova ulica 2, 1000 Ljubljana, Slovenia.
Jamšek J; Department of Nuclear Medicine, University Medical Center Ljubljana, Zaloška cesta 7, 1000 Ljubljana, Slovenia.
Trošt M; Department of Neurology, University Medical Center Ljubljana, Zaloška cesta 2a, 1000 Ljubljana, Slovenia.; Department of Nuclear Medicine, University Medical Center Ljubljana, Zaloška cesta 7, 1000 Ljubljana, Slovenia.; Medical Faculty, University of Ljubljana, Vrazov trg 2, 1000 Ljubljana, Slovenia.
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Źródło:
International journal of molecular sciences [Int J Mol Sci] 2023 Aug 23; Vol. 24 (17). Date of Electronic Publication: 2023 Aug 23.
Typ publikacji:
Case Reports
MeSH Terms:
Creutzfeldt-Jakob Syndrome*/diagnosis
Creutzfeldt-Jakob Syndrome*/diagnostic imaging
Parkinson Disease*/complications
Parkinson Disease*/diagnostic imaging
Neurodegenerative Diseases*
Humans ; Aged ; Fluorodeoxyglucose F18 ; Brain/diagnostic imaging
SCR Disease Name:
Creutzfeldt-Jakob Disease, Sporadic
Raport

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