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Wyszukujesz frazę ""Crosbie-Watson RH"" wg kryterium: Autor


Wyświetlanie 1-3 z 3
Tytuł:
Nanospan, an alternatively spliced isoform of sarcospan, localizes to the sarcoplasmic reticulum in skeletal muscle and is absent in limb girdle muscular dystrophy 2F.
Autorzy:
Peter AK; Department of Integrative Biology and Physiology, University of California, Los Angeles, 610 Charles E. Young Drive East, Terasaki Life Sciences Building, Los Angeles, CA, 90095, USA.; Present Address: Biofrontiers Institute, Department of Molecular, Cellular and Developmental Biology, University of Colorado, Boulder, CO, USA.
Miller G; Department of Integrative Biology and Physiology, University of California, Los Angeles, 610 Charles E. Young Drive East, Terasaki Life Sciences Building, Los Angeles, CA, 90095, USA.; Present Address: Department of Oncology and Metabolism, University of Sheffield, Sheffield, UK.
Capote J; Department of Neurology, David Geffen School of Medicine, University of California, Los Angeles, 610 Charles E. Young Drive East, Terasaki Life Sciences Building, Los Angeles, CA, 90095, USA.; Center for Duchenne Muscular Dystrophy, University of California, Los Angeles, Los Angeles, CA, USA.
DiFranco M; Center for Duchenne Muscular Dystrophy, University of California, Los Angeles, Los Angeles, CA, USA.; Department of Physiology, David Geffen School of Medicine, University of California, Los Angeles, Los Angeles, CA, USA.
Solares-Pérez A; Sección de Estudios de Posgrado e Investigación, Escuela Superior de Medicina, Instituto Politécnico Nacional, Mexico City, Mexico.
Wang EL; Department of Integrative Biology and Physiology, University of California, Los Angeles, 610 Charles E. Young Drive East, Terasaki Life Sciences Building, Los Angeles, CA, 90095, USA.
Heighway J; Cancer Communications and Consultancy Ltd, Knutsford, Cheshire, UK.
Coral-Vázquez RM; Sección de Estudios de Posgrado e Investigación, Escuela Superior de Medicina, Instituto Politécnico Nacional, Mexico City, Mexico.
Vergara J; Center for Duchenne Muscular Dystrophy, University of California, Los Angeles, Los Angeles, CA, USA.; Department of Physiology, David Geffen School of Medicine, University of California, Los Angeles, Los Angeles, CA, USA.
Crosbie-Watson RH; Department of Integrative Biology and Physiology, University of California, Los Angeles, 610 Charles E. Young Drive East, Terasaki Life Sciences Building, Los Angeles, CA, 90095, USA. .; Department of Neurology, David Geffen School of Medicine, University of California, Los Angeles, 610 Charles E. Young Drive East, Terasaki Life Sciences Building, Los Angeles, CA, 90095, USA. .; Center for Duchenne Muscular Dystrophy, University of California, Los Angeles, Los Angeles, CA, USA. .; Molecular Biology Institute, University of California, Los Angeles, Los Angeles, CA, USA. .
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Źródło:
Skeletal muscle [Skelet Muscle] 2017 Jun 06; Vol. 7 (1), pp. 11. Date of Electronic Publication: 2017 Jun 06.
Typ publikacji:
Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
MeSH Terms:
Alternative Splicing*
Carrier Proteins/*genetics
Membrane Proteins/*genetics
Neoplasm Proteins/*genetics
Sarcoglycanopathies/*metabolism
Sarcoplasmic Reticulum/*metabolism
Animals ; Carrier Proteins/metabolism ; Humans ; Membrane Proteins/metabolism ; Mice ; Mice, Inbred C57BL ; Neoplasm Proteins/metabolism ; Protein Isoforms/genetics ; Protein Isoforms/metabolism ; Protein Transport ; Sarcoglycanopathies/genetics ; Sarcoglycanopathies/pathology ; Sarcoglycans/genetics ; Sarcoplasmic Reticulum/ultrastructure
SCR Disease Name:
Limb-girdle muscular dystrophy type 2F
Czasopismo naukowe
Tytuł:
The potential of sarcospan in adhesion complex replacement therapeutics for the treatment of muscular dystrophy.
Autorzy:
Marshall JL; Department of Integrative Biology and Physiology, University of California, Los Angeles, CA 90095, USA.
Kwok Y
McMorran BJ
Baum LG
Crosbie-Watson RH
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Źródło:
The FEBS journal [FEBS J] 2013 Sep; Vol. 280 (17), pp. 4210-29. Date of Electronic Publication: 2013 May 13.
Typ publikacji:
Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Review
MeSH Terms:
Carrier Proteins/*metabolism
Dystrophin/*metabolism
Integrins/*metabolism
Membrane Proteins/*metabolism
Muscular Dystrophies/*therapy
Neoplasm Proteins/*metabolism
Sarcolemma/*metabolism
Utrophin/*metabolism
Animals ; Humans ; Muscular Dystrophies/metabolism ; Signal Transduction
Czasopismo naukowe
Tytuł:
Sarcospan: a small protein with large potential for Duchenne muscular dystrophy.
Autorzy:
Marshall JL; Department of Integrative Biology and Physiology, University of California Los Angeles, 610 Charles E, Young Drive East, Terasaki Life Sciences Building, Los Angeles, CA, 90095, USA. .
Crosbie-Watson RH
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Źródło:
Skeletal muscle [Skelet Muscle] 2013 Jan 03; Vol. 3 (1), pp. 1. Date of Electronic Publication: 2013 Jan 03.
Typ publikacji:
Journal Article
Czasopismo naukowe
    Wyświetlanie 1-3 z 3

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