A transgenic mice model of retinopathy of cblG-type inherited disorder of one-carbon metabolism highlights epigenome-wide alterations related to cone photoreceptor cells development and retinal metabolism.
Autorzy:
Matmat K; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. Conart JB; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France.; Department of Ophthalmology, University Regional Hospital Center of Nancy, 54000, Nancy, France. Graindorge PH; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. El Kouche S; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. Hassan Z; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. Siblini Y; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. Umoret R; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. Safar R; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. Baspinar O; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. Robert A; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. Alberto JM; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. Oussalah A; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. Coelho D; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France.; National Center of Inborn Errors of Metabolism, University Regional Hospital Center of Nancy, 54000, Nancy, France. Guéant JL; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. jean-louis.gueant@univ-lorraine.fr.; National Center of Inborn Errors of Metabolism, University Regional Hospital Center of Nancy, 54000, Nancy, France. jean-louis.gueant@univ-lorraine.fr.; Faculté de Médecine, Bâtiment C 2Ème Étage, 9 Avenue de La Forêt de Haye, 54505, Vandœuvre-lès-Nancy, France. jean-louis.gueant@univ-lorraine.fr. Guéant-RodriguezRM; Inserm UMRS 1256 NGERE - Nutrition, Genetics, and Environmental Risk Exposure, University of Lorraine, 54500, Vandoeuvre-lès-Nancy, France. Rosa-Maria.Gueant-Rodriguez@univ-lorraine.fr.; National Center of Inborn Errors of Metabolism, University Regional Hospital Center of Nancy, 54000, Nancy, France. Rosa-Maria.Gueant-Rodriguez@univ-lorraine.fr.; Faculté de Médecine, Bâtiment C 2Ème Étage, 9 Avenue de La Forêt de Haye, 54505, Vandœuvre-lès-Nancy, France. Rosa-Maria.Gueant-Rodriguez@univ-lorraine.fr.
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Źródło:
Clinical epigenetics [Clin Epigenetics] 2023 Oct 05; Vol. 15 (1), pp. 158. Date of Electronic Publication: 2023 Oct 05.
Causes and consequences of impaired methionine synthase activity in acquired and inherited disorders of vitamin B 12 metabolism.
Autorzy:
Guéant JL; UMR Inserm 1256 N-GERE (Nutrition, Génetique et Exposition aux Risques Environmentaux), Université de Lorraine, Vandoeuvre-lès-Nancy, France.; Departments of Digestive Diseases and Molecular Medicine and National Center of Inborn Errors of Metabolism, University Hospital Center, Université de Lorraine, Vandoeuvre-lès-Nancy, France. Guéant-RodriguezRM; UMR Inserm 1256 N-GERE (Nutrition, Génetique et Exposition aux Risques Environmentaux), Université de Lorraine, Vandoeuvre-lès-Nancy, France.; Departments of Digestive Diseases and Molecular Medicine and National Center of Inborn Errors of Metabolism, University Hospital Center, Université de Lorraine, Vandoeuvre-lès-Nancy, France. Kosgei VJ; UMR Inserm 1256 N-GERE (Nutrition, Génetique et Exposition aux Risques Environmentaux), Université de Lorraine, Vandoeuvre-lès-Nancy, France. Coelho D; UMR Inserm 1256 N-GERE (Nutrition, Génetique et Exposition aux Risques Environmentaux), Université de Lorraine, Vandoeuvre-lès-Nancy, France.
Sirt1-PPARS Cross-Talk in Complex Metabolic Diseases and Inherited Disorders of the One Carbon Metabolism.
Autorzy:
Kosgei VJ; UMR Inserm 1256 N-GERE (Nutrition, Génetique et Exposition aux Risques Environmentaux), Université de Lorraine, 54500 Vandoeuvre-lès-Nancy, France. Coelho D; UMR Inserm 1256 N-GERE (Nutrition, Génetique et Exposition aux Risques Environmentaux), Université de Lorraine, 54500 Vandoeuvre-lès-Nancy, France. Guéant-RodriguezRM; UMR Inserm 1256 N-GERE (Nutrition, Génetique et Exposition aux Risques Environmentaux), Université de Lorraine, 54500 Vandoeuvre-lès-Nancy, France.; Departments of Digestive Diseases, Nutrition and Endocrinology and Molecular Medicine and National Center of Inborn Errors of Metabolism, University Hospital Center, Université de Lorraine, 54500 Vandoeuvre-lès-Nancy, France. Guéant JL; UMR Inserm 1256 N-GERE (Nutrition, Génetique et Exposition aux Risques Environmentaux), Université de Lorraine, 54500 Vandoeuvre-lès-Nancy, France.; Departments of Digestive Diseases, Nutrition and Endocrinology and Molecular Medicine and National Center of Inborn Errors of Metabolism, University Hospital Center, Université de Lorraine, 54500 Vandoeuvre-lès-Nancy, France.
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Źródło:
Cells [Cells] 2020 Aug 11; Vol. 9 (8). Date of Electronic Publication: 2020 Aug 11.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't; Review
Foetal programming by methyl donor deficiency produces steato-hepatitis in rats exposed to high fat diet.
Autorzy:
Bison A; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Marchal-Bressenot A; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Li Z; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Elamouri I; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Feigerlova E; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Peng L; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Houlgatte R; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Beck B; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Pourié G; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Alberto JM; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Umoret R; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Conroy G; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Bronowicki JP; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Guéant JL; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France. Guéant-RodriguezRM; Inserm U954, Nutrition-Genetics-Environmental Risk Exposure (N-GERE), University of Lorraine, BP 184, 54511, Vandœuvre-lès-Nancy, France.
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Źródło:
Scientific reports [Sci Rep] 2016 Nov 17; Vol. 6, pp. 37207. Date of Electronic Publication: 2016 Nov 17.
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