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Starter badań:

Tytuł:
iCPET Calculator: A Web-Based Application to Standardize the Calculation of Alpha Distensibility in Patients With Pulmonary Arterial Hypertension.
Autorzy:
Elliott J; Division of Translational and Regenerative Medicine University of Arizona Tucson AZ USA.
Menakuru N; Division of Translational and Regenerative Medicine University of Arizona Tucson AZ USA.
Martin KJ; Division of Translational and Regenerative Medicine University of Arizona Tucson AZ USA.
Rahaghi FN; Pulmonary and Critical Care Brigham and Women's Hospital Boston MA USA.
Rischard FP; Division of Pulmonary, Allergy, Critical Care and Sleep Medicine University of Arizona Tucson AZ USA.
Vanderpool RR; Division of Translational and Regenerative Medicine University of Arizona Tucson AZ USA.; Division of Cardiovascular Medicine, College of Medicine The Ohio State University Columbus OH USA.
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Źródło:
Journal of the American Heart Association [J Am Heart Assoc] 2023 Oct 17; Vol. 12 (20), pp. e029667. Date of Electronic Publication: 2023 Oct 10.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Pulmonary Arterial Hypertension*
Hypertension, Pulmonary*/diagnostic imaging
Hypertension, Pulmonary*/complications
Ventricular Dysfunction, Right*
Humans ; Retrospective Studies ; Exercise Test/methods ; Familial Primary Pulmonary Hypertension ; Internet ; Ventricular Function, Right ; Pulmonary Artery/diagnostic imaging
Czasopismo naukowe
Tytuł:
The efficacy of the treat-repair-treat strategy for severe pulmonary arterial hypertension associated with congenital heart disease: a meta-analysis.
Autorzy:
Wang Z; Department of Cardiac Surgery, The First Hospital of Hebei Medical University, No. 89, Donggang Road, Yuhua District, Shijiazhuang City, Hebei Province, China.
Li X; Department of Cardiac Surgery, The First Hospital of Hebei Medical University, No. 89, Donggang Road, Yuhua District, Shijiazhuang City, Hebei Province, China.
Li M; Department of Cardiac Surgery, The First Hospital of Hebei Medical University, No. 89, Donggang Road, Yuhua District, Shijiazhuang City, Hebei Province, China.
Peng J; Department of Cardiac Surgery, The First Hospital of Hebei Medical University, No. 89, Donggang Road, Yuhua District, Shijiazhuang City, Hebei Province, China.
Zhang H; Department of Cardiac Surgery, The First Hospital of Hebei Medical University, No. 89, Donggang Road, Yuhua District, Shijiazhuang City, Hebei Province, China. .
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Źródło:
BMC cardiovascular disorders [BMC Cardiovasc Disord] 2023 Nov 20; Vol. 23 (1), pp. 569. Date of Electronic Publication: 2023 Nov 20.
Typ publikacji:
Meta-Analysis; Journal Article
MeSH Terms:
Pulmonary Arterial Hypertension*/diagnosis
Pulmonary Arterial Hypertension*/drug therapy
Pulmonary Arterial Hypertension*/complications
Hypertension, Pulmonary*/complications
Heart Defects, Congenital*/complications
Heart Defects, Congenital*/diagnosis
Humans ; Familial Primary Pulmonary Hypertension ; Arteries
Czasopismo naukowe
Tytuł:
Targeting IL-11 system as a treatment of pulmonary arterial hypertension.
Autorzy:
Milara J; CIBER de enfermedades respiratorias, Health Institute Carlos III, Valencia, Spain; Department of Pharmacology, Faculty of Medicine, University of Valencia, Spain; Pharmacy Unit, University General Hospital Consortium of Valencia, Spain. Electronic address: .
Roger I; CIBER de enfermedades respiratorias, Health Institute Carlos III, Valencia, Spain; Department of Pharmacology, Faculty of Medicine, University of Valencia, Spain.
Montero P; Department of Pharmacology, Faculty of Medicine, University of Valencia, Spain.
Artigues E; Surgery Unit, University General Hospital Consortium, Valencia, Spain.
Escrivá J; Thoracic Surgery Unit, University and Polytechnic Hospital La Fe, Valencia, Spain.
Perez-Vizcaino F; CIBER de enfermedades respiratorias, Health Institute Carlos III, Valencia, Spain; Dept of Pharmacology and Toxicology, School of Medicine, Universidad Complutense de Madrid, Madrid, Spain.
Cortijo J; CIBER de enfermedades respiratorias, Health Institute Carlos III, Valencia, Spain; Department of Pharmacology, Faculty of Medicine, University of Valencia, Spain; Research and Teaching Unit, University General Hospital Consortium, Valencia, Spain.
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Źródło:
Pharmacological research [Pharmacol Res] 2023 Nov; Vol. 197, pp. 106985. Date of Electronic Publication: 2023 Nov 09.
Typ publikacji:
Journal Article
MeSH Terms:
Pulmonary Arterial Hypertension*
Hypertension, Pulmonary*/chemically induced
Hypertension, Pulmonary*/drug therapy
Humans ; Animals ; Rats ; Familial Primary Pulmonary Hypertension ; Interleukin-11 ; Monocrotaline ; Pulmonary Artery ; RNA, Small Interfering/genetics
Czasopismo naukowe
Tytuł:
Therapeutic Approaches in Pulmonary Arterial Hypertension with Beneficial Effects on Right Ventricular Function-Preclinical Studies.
Autorzy:
Balsa A; Cardiovascular R&D , Department of Surgery and Physiology, Faculty of Medicine, University of Porto, 4200-319 Porto, Portugal.
Adão R; Cardiovascular R&D , Department of Surgery and Physiology, Faculty of Medicine, University of Porto, 4200-319 Porto, Portugal.; Department of Pharmacology and Toxicology, School of Medicine, Complutense University of Madrid, 28040 Madrid, Spain.; CIBER of Respiratory Diseases (CIBERES), 28029 Madrid, Spain.
Brás-Silva C; Cardiovascular R&D , Department of Surgery and Physiology, Faculty of Medicine, University of Porto, 4200-319 Porto, Portugal.; Faculty of Nutrition and Food Sciences, University of Porto, 4150-180 Porto, Portugal.
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Źródło:
International journal of molecular sciences [Int J Mol Sci] 2023 Oct 24; Vol. 24 (21). Date of Electronic Publication: 2023 Oct 24.
Typ publikacji:
Journal Article; Review
MeSH Terms:
Pulmonary Arterial Hypertension*/drug therapy
Hypertension, Pulmonary*/drug therapy
Humans ; Mice ; Rats ; Animals ; Ventricular Function, Right ; Pulmonary Artery ; Familial Primary Pulmonary Hypertension ; Disease Models, Animal
Czasopismo naukowe
Tytuł:
Central diastolic blood pressure, plasma aldosterone and uric acid are associated with microalbuminuria in essential hypertension: a case-control study.
Autorzy:
Li J; Department of Hypertension, Clinical School of Cardiovascular Disease, Tianjin Medical University, Tianjin, 300457, China.; Department of Hypertension, TEDA International Cardiovascular Hospital, Tianjin, 300457, China.
Yang N; Department of Hypertension, TEDA International Cardiovascular Hospital, Tianjin, 300457, China.
Chou H; Department of Hypertension, TEDA International Cardiovascular Hospital, Tianjin, 300457, China.
Shi L; Department of Hypertension, TEDA International Cardiovascular Hospital, Tianjin, 300457, China.
Wei M; Center for Clinical Epidemiology, TEDA International Cardiovascular Hospital, Tianjin, 300457, China.
Li Y; Department of Hypertension, TEDA International Cardiovascular Hospital, Tianjin, 300457, China. .
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Źródło:
BMC cardiovascular disorders [BMC Cardiovasc Disord] 2023 Oct 17; Vol. 23 (1), pp. 511. Date of Electronic Publication: 2023 Oct 17.
Typ publikacji:
Journal Article
MeSH Terms:
Aldosterone*
Hypertension*/diagnosis
Hypertension*/epidemiology
Hypertension*/complications
Humans ; Blood Pressure ; Uric Acid ; Case-Control Studies ; Risk Factors ; Essential Hypertension/diagnosis ; Essential Hypertension/complications ; Albuminuria/diagnosis
Czasopismo naukowe
Tytuł:
Heritable Pulmonary Arterial Hypertension Diagnosed during the Postpartum Period: A Case Report and Literature Review.
Autorzy:
Çolak A; Department of Cardiology, Dokuz Eylül University Faculty of Medicine, İzmir, Türkiye.
Kumral Z; Department of Cardiology, Dokuz Eylül University Faculty of Medicine, İzmir, Türkiye.
Özpelit E; Department of Cardiology, Dokuz Eylül University Faculty of Medicine, İzmir, Türkiye.
Akdeniz B; Department of Cardiology, Dokuz Eylül University Faculty of Medicine, İzmir, Türkiye.
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Transliterated Title:
Postpartum Dönemde Tanı Konulan Kalıtsal Pulmoner Arteriyel Hipertansiyon: Bir Olgu Sunumu ve Literatür Taraması.
Źródło:
Turk Kardiyoloji Dernegi arsivi : Turk Kardiyoloji Derneginin yayin organidir [Turk Kardiyol Dern Ars] 2023 Oct; Vol. 51 (7), pp. 498-501.
Typ publikacji:
Review; Case Reports
MeSH Terms:
Hypertension, Pulmonary*/diagnosis
Hypertension, Pulmonary*/genetics
Pulmonary Arterial Hypertension*
Pregnancy ; Female ; Humans ; Adult ; Familial Primary Pulmonary Hypertension/diagnosis ; Familial Primary Pulmonary Hypertension/genetics ; Mutation ; Postpartum Period ; Bone Morphogenetic Protein Receptors, Type II/genetics ; Bone Morphogenetic Protein Receptors, Type II/metabolism
Recenzja
Tytuł:
Therapeutic effects of hypoxia-preconditioned bone marrow-derived mesenchymal stromal cells and their extracellular vesicles in experimental pulmonary arterial hypertension.
Autorzy:
Braga CL; Laboratory of Pulmonary Investigation, Carlos Chagas Filho Institute of Biophysics, Federal University of Rio de Janeiro, Rio de Janeiro, RJ, Brazil; National Institute of Science and Technology for Regenerative Medicine, Rio de Janeiro, Brazil.
Santos RT; Laboratory of Pulmonary Investigation, Carlos Chagas Filho Institute of Biophysics, Federal University of Rio de Janeiro, Rio de Janeiro, RJ, Brazil.
da Silva CM; Laboratory of Pulmonary Investigation, Carlos Chagas Filho Institute of Biophysics, Federal University of Rio de Janeiro, Rio de Janeiro, RJ, Brazil.
de Novaes Rocha N; Laboratory of Pulmonary Investigation, Carlos Chagas Filho Institute of Biophysics, Federal University of Rio de Janeiro, Rio de Janeiro, RJ, Brazil; National Institute of Science and Technology for Regenerative Medicine, Rio de Janeiro, Brazil; Department of Physiology and Pharmacology, Biomedical Institute, Fluminense Federal University, Niteroi, Brazil.
Felix NS; Laboratory of Pulmonary Investigation, Carlos Chagas Filho Institute of Biophysics, Federal University of Rio de Janeiro, Rio de Janeiro, RJ, Brazil.
Medeiros M; Laboratory of Pulmonary Investigation, Carlos Chagas Filho Institute of Biophysics, Federal University of Rio de Janeiro, Rio de Janeiro, RJ, Brazil.
Melo MM; Laboratory of Pulmonary Investigation, Carlos Chagas Filho Institute of Biophysics, Federal University of Rio de Janeiro, Rio de Janeiro, RJ, Brazil.
Silva JD; Laboratory of Pulmonary Investigation, Carlos Chagas Filho Institute of Biophysics, Federal University of Rio de Janeiro, Rio de Janeiro, RJ, Brazil; National Institute of Science and Technology for Regenerative Medicine, Rio de Janeiro, Brazil.
Teixeira DE; Laboratory of Biochemistry and Cell Signaling, Institute of Biophysics Carlos Chagas Filho, Federal University of Rio de Janeiro, RJ, Brazil.
Neves CC; National Institute of Science and Technology for Regenerative Medicine, Rio de Janeiro, Brazil; Laboratory of Biochemistry and Cell Signaling, Institute of Biophysics Carlos Chagas Filho, Federal University of Rio de Janeiro, RJ, Brazil.
Rocco PRM; Laboratory of Pulmonary Investigation, Carlos Chagas Filho Institute of Biophysics, Federal University of Rio de Janeiro, Rio de Janeiro, RJ, Brazil; National Institute of Science and Technology for Regenerative Medicine, Rio de Janeiro, Brazil.
Cruz FF; Laboratory of Pulmonary Investigation, Carlos Chagas Filho Institute of Biophysics, Federal University of Rio de Janeiro, Rio de Janeiro, RJ, Brazil; National Institute of Science and Technology for Regenerative Medicine, Rio de Janeiro, Brazil.
Silva PL; Laboratory of Pulmonary Investigation, Carlos Chagas Filho Institute of Biophysics, Federal University of Rio de Janeiro, Rio de Janeiro, RJ, Brazil; National Institute of Science and Technology for Regenerative Medicine, Rio de Janeiro, Brazil. Electronic address: .
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Źródło:
Life sciences [Life Sci] 2023 Sep 15; Vol. 329, pp. 121988. Date of Electronic Publication: 2023 Jul 29.
Typ publikacji:
Journal Article
MeSH Terms:
Hypertension, Pulmonary*
Pulmonary Arterial Hypertension*/therapy
Pulmonary Arterial Hypertension*/metabolism
Extracellular Vesicles*/metabolism
Mesenchymal Stem Cells*/metabolism
Rats ; Animals ; Male ; Hypertrophy, Right Ventricular ; Bone Marrow/metabolism ; Cells, Cultured ; Rats, Wistar ; Familial Primary Pulmonary Hypertension ; Collagen/metabolism ; Hypoxia/metabolism
Czasopismo naukowe
Tytuł:
A prognostic model for systemic lupus erythematosus-associated pulmonary arterial hypertension: CSTAR-PAH cohort study.
Autorzy:
Qu J; Department of Rheumatology, Peking Union Medical College Hospital (PUMCH), Peking Union Medical College & Chinese Academy of Medical Sciences, National Clinical Research Center for Dermatologic and Immunologic Diseases (NCRC-DID), Ministry of Science & Technology, Key Laboratory of Rheumatology and Clinical Immunology, Ministry of Education, State Key Laboratory of Complex Severe and Rare Diseases, Ministry of Science and Technology, No. 1 Shuaifuyuan, Wangfujing Ave, Beijing, 100730, China.; Department of Respiratory and Critical Care Medicine, Peking University Third Hospital, Beijing, China.
Li M; Department of Rheumatology, Peking Union Medical College Hospital (PUMCH), Peking Union Medical College & Chinese Academy of Medical Sciences, National Clinical Research Center for Dermatologic and Immunologic Diseases (NCRC-DID), Ministry of Science & Technology, Key Laboratory of Rheumatology and Clinical Immunology, Ministry of Education, State Key Laboratory of Complex Severe and Rare Diseases, Ministry of Science and Technology, No. 1 Shuaifuyuan, Wangfujing Ave, Beijing, 100730, China. .
Zhang X; Department of Rheumatology, Guangdong General Hospital, Guangzhou, China.
Zhang M; Department of Rheumatology, The First Affiliated Hospital of Nanjing Medical University, Nanjing, China.
Zuo X; Department of Rheumatology, Xiangya Hospital, Central South University, Changsha, China.
Zhu P; Department of Clinical Immunology, PLA Specialized Research Institute of Rheumatology and Immunology, Xijing Hospital, Fourth Military Medical University, Xi'an, China.
Ye S; Department of Rheumatology, School of Medicine, Shanghai Jiao Tong University, Ren Ji Hospital South Campus, Shanghai, China.
Zhang W; Department of Rheumatology, School of Medicine, Ren Ji Hospital, Shanghai Jiao Tong University, Shanghai, China.
Zheng Y; Department of Rheumatology, Beijing Chao-Yang Hospital, Capital Medical University, Beijing, China.
Qi W; Department of Rheumatology, The First Central Hospital, Tianjin, China.
Li Y; Department of Rheumatology, The Second Affiliated Hospital of Harbin Medical University, Harbin, China.
Zhang Z; Department of Rheumatology and Clinical Immunology, Peking University First Hospital, Beijing, China.
Ding F; Department of Rheumatology, Qilu Hospital of Shandong University, Jinan, China.
Gu J; Department of Rheumatology, The Third Affiliated Hospital of Sun Yat-Sen University, Guangzhou, China.
Liu Y; Department of Rheumatology and Immunology, West China Hospital, Sichuan University, Chengdu, China.
Qian J; Department of Rheumatology, Peking Union Medical College Hospital (PUMCH), Peking Union Medical College & Chinese Academy of Medical Sciences, National Clinical Research Center for Dermatologic and Immunologic Diseases (NCRC-DID), Ministry of Science & Technology, Key Laboratory of Rheumatology and Clinical Immunology, Ministry of Education, State Key Laboratory of Complex Severe and Rare Diseases, Ministry of Science and Technology, No. 1 Shuaifuyuan, Wangfujing Ave, Beijing, 100730, China.
Huang C; Department of Rheumatology, Peking Union Medical College Hospital (PUMCH), Peking Union Medical College & Chinese Academy of Medical Sciences, National Clinical Research Center for Dermatologic and Immunologic Diseases (NCRC-DID), Ministry of Science & Technology, Key Laboratory of Rheumatology and Clinical Immunology, Ministry of Education, State Key Laboratory of Complex Severe and Rare Diseases, Ministry of Science and Technology, No. 1 Shuaifuyuan, Wangfujing Ave, Beijing, 100730, China.
Zhao J; Department of Rheumatology, Peking Union Medical College Hospital (PUMCH), Peking Union Medical College & Chinese Academy of Medical Sciences, National Clinical Research Center for Dermatologic and Immunologic Diseases (NCRC-DID), Ministry of Science & Technology, Key Laboratory of Rheumatology and Clinical Immunology, Ministry of Education, State Key Laboratory of Complex Severe and Rare Diseases, Ministry of Science and Technology, No. 1 Shuaifuyuan, Wangfujing Ave, Beijing, 100730, China.
Wang Q; Department of Rheumatology, Peking Union Medical College Hospital (PUMCH), Peking Union Medical College & Chinese Academy of Medical Sciences, National Clinical Research Center for Dermatologic and Immunologic Diseases (NCRC-DID), Ministry of Science & Technology, Key Laboratory of Rheumatology and Clinical Immunology, Ministry of Education, State Key Laboratory of Complex Severe and Rare Diseases, Ministry of Science and Technology, No. 1 Shuaifuyuan, Wangfujing Ave, Beijing, 100730, China.
Liu Y; Department of Cardiology, Peking Union Medical College Hospital, Peking Union Medical College & Chinese Academy of Medical Sciences, State Key Laboratory of Complex Severe and Rare Diseases, Ministry of Science & Technology, Beijing, China.
Tian Z; Department of Cardiology, Peking Union Medical College Hospital, Peking Union Medical College & Chinese Academy of Medical Sciences, State Key Laboratory of Complex Severe and Rare Diseases, Ministry of Science & Technology, Beijing, China.
Wang Y; Department of Epidemiology and Bio-Statistics, Institute of Basic Medical Sciences, China Academy of Medical Sciences and Peking Union Medical College, Beijing, China.
Wei W; Department of Rheumatology, Tianjin Medical University General Hospital, No. 154 Anshan Street, Tianjin, 300052, China. .
Zeng X; Department of Rheumatology, Peking Union Medical College Hospital (PUMCH), Peking Union Medical College & Chinese Academy of Medical Sciences, National Clinical Research Center for Dermatologic and Immunologic Diseases (NCRC-DID), Ministry of Science & Technology, Key Laboratory of Rheumatology and Clinical Immunology, Ministry of Education, State Key Laboratory of Complex Severe and Rare Diseases, Ministry of Science and Technology, No. 1 Shuaifuyuan, Wangfujing Ave, Beijing, 100730, China. .
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Źródło:
Respiratory research [Respir Res] 2023 Sep 09; Vol. 24 (1), pp. 220. Date of Electronic Publication: 2023 Sep 09.
Typ publikacji:
Multicenter Study; Journal Article
MeSH Terms:
Pulmonary Arterial Hypertension*/diagnosis
Pulmonary Arterial Hypertension*/epidemiology
Pulmonary Arterial Hypertension*/etiology
Hypertension, Pulmonary*/diagnosis
Hypertension, Pulmonary*/epidemiology
Hypertension, Pulmonary*/etiology
Lupus Erythematosus, Systemic*/complications
Lupus Erythematosus, Systemic*/diagnosis
Lupus Erythematosus, Systemic*/epidemiology
Humans ; Cohort Studies ; Prognosis ; Familial Primary Pulmonary Hypertension
Czasopismo naukowe
Tytuł:
In the Search for Biomarkers of Pulmonary Arterial Hypertension, Are Cytokines IL-2, IL-4, IL-6, IL-10, and IFN-Gamma the Right Indicators to Use?
Autorzy:
Tomaszewski M; Department of Cardiology, Medical University of Lublin, Jaczewskiego 8, 20-954 Lublin, Poland.
Mertowska P; Department of Experimental Immunology, Medical University of Lublin, Chodzki 4a, 20-093 Lublin, Poland.
Janczewska M; Department of Cardiology, Medical University of Lublin, Jaczewskiego 8, 20-954 Lublin, Poland.
Styczeń A; Department of Cardiology, Medical University of Lublin, Jaczewskiego 8, 20-954 Lublin, Poland.
Mertowski S; Department of Experimental Immunology, Medical University of Lublin, Chodzki 4a, 20-093 Lublin, Poland.
Jonas K; Pulmonary Circulation Centre, Department of Cardiac and Vascular Diseases, Jagiellonian University Medical College, Centre for Rare Cardiovascular Diseases, John Paul II Hospital, ul. Pradnicka 80, 31-202 Krakow, Poland.
Grywalska E; Department of Experimental Immunology, Medical University of Lublin, Chodzki 4a, 20-093 Lublin, Poland.
Kopeć G; Pulmonary Circulation Centre, Department of Cardiac and Vascular Diseases, Jagiellonian University Medical College, Centre for Rare Cardiovascular Diseases, John Paul II Hospital, ul. Pradnicka 80, 31-202 Krakow, Poland.
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Źródło:
International journal of molecular sciences [Int J Mol Sci] 2023 Sep 05; Vol. 24 (18). Date of Electronic Publication: 2023 Sep 05.
Typ publikacji:
Journal Article
MeSH Terms:
Pulmonary Arterial Hypertension*
Hypertension, Pulmonary*/metabolism
Humans ; Cytokines/metabolism ; Interleukin-10 ; Interleukin-6 ; Interleukin-2 ; Interleukin-4 ; Familial Primary Pulmonary Hypertension ; Interferon-gamma ; Biomarkers
Czasopismo naukowe
Tytuł:
Seven Additional Patients with SOX17 Related Pulmonary Arterial Hypertension and Review of the Literature.
Autorzy:
Gallego-Zazo N; Instituto de Genética Médica y Molecular (INGEMM), Instituto de Investigación del Hospital Universitario La Paz (IdiPaz), Hospital Universitario La Paz, 28046 Madrid, Spain.; CIBERER, Centro de Investigación Biomédica de Enfermedades Raras en Red, Instituto de Salud Carlos III, 28029 Madrid, Spain.; ERN-ITHACA, European Reference Network on Rare Malformations Syndromes, Intellectual and Other Neuro-Developmental Disorders, 75019 Paris, France.
Miranda-Alcaraz L; Instituto de Genética Médica y Molecular (INGEMM), Instituto de Investigación del Hospital Universitario La Paz (IdiPaz), Hospital Universitario La Paz, 28046 Madrid, Spain.; CIBERER, Centro de Investigación Biomédica de Enfermedades Raras en Red, Instituto de Salud Carlos III, 28029 Madrid, Spain.; ERN-ITHACA, European Reference Network on Rare Malformations Syndromes, Intellectual and Other Neuro-Developmental Disorders, 75019 Paris, France.
Cruz-Utrilla A; Unidad Multidisciplinar de Hipertensión Pulmonar, Servicio de Cardiología, Hospital Universitario 12 de Octubre, 28041 Madrid, Spain.; ERN-LUNG, European Reference Network on Rare Lung Diseases (Pulmonary Hypertension), 60596 Frankfurt am Main, Germany.; CIBERCV, Centro de Investigación Biomédica en Red de Enfermedades Cardiovasculares, Instituto de Salud Carlos III, 28029 Madrid, Spain.
Del Cerro Marín MJ; Unidad de Hipertensión Pulmonar Pediátrica, Servicio de Cardiología Pediátrica, Hospital Universitario Ramón y Cajal, Instituto de Investigación Biomédica del Hospital Universitario Ramón y Cajal (Irycis), 28034 Madrid, Spain.
Álvarez-Fuente M; Unidad de Hipertensión Pulmonar Pediátrica, Servicio de Cardiología Pediátrica, Hospital Universitario Ramón y Cajal, Instituto de Investigación Biomédica del Hospital Universitario Ramón y Cajal (Irycis), 28034 Madrid, Spain.
Del Mar Rodríguez Vázquez Del Rey M; Unidad de Cardiología Pediátrica, Hospital Universitario Virgen de las Nieves, 18014 Granada, Spain.
Guillén Rodríguez I; Unidad de Cardiología Pediátrica, Hospital Universitario Virgen del Rocío, 41013 Sevilla, Spain.
Becerra-Munoz VM; CIBERCV, Centro de Investigación Biomédica en Red de Enfermedades Cardiovasculares, Instituto de Salud Carlos III, 28029 Madrid, Spain.; Unidad de Gestión Clínica Área del Corazón, Instituto de Investigación Biomédica de Málaga (IBIMA), Hospital Universitario Virgen de la Victoria, Universidad de Málaga, 29590 Málaga, Spain.
Moya-Bonora A; Unidad de Cardiología Pediátrica, Departamento de Pediatría, Hospital Universitario La Fe, 46026 Valencia, Spain.
Ochoa Parra N; Unidad Multidisciplinar de Hipertensión Pulmonar, Servicio de Cardiología, Hospital Universitario 12 de Octubre, 28041 Madrid, Spain.; ERN-LUNG, European Reference Network on Rare Lung Diseases (Pulmonary Hypertension), 60596 Frankfurt am Main, Germany.; CIBERCV, Centro de Investigación Biomédica en Red de Enfermedades Cardiovasculares, Instituto de Salud Carlos III, 28029 Madrid, Spain.
Parra A; Instituto de Genética Médica y Molecular (INGEMM), Instituto de Investigación del Hospital Universitario La Paz (IdiPaz), Hospital Universitario La Paz, 28046 Madrid, Spain.; CIBERER, Centro de Investigación Biomédica de Enfermedades Raras en Red, Instituto de Salud Carlos III, 28029 Madrid, Spain.; ERN-ITHACA, European Reference Network on Rare Malformations Syndromes, Intellectual and Other Neuro-Developmental Disorders, 75019 Paris, France.
Pascual P; Instituto de Genética Médica y Molecular (INGEMM), Instituto de Investigación del Hospital Universitario La Paz (IdiPaz), Hospital Universitario La Paz, 28046 Madrid, Spain.; CIBERER, Centro de Investigación Biomédica de Enfermedades Raras en Red, Instituto de Salud Carlos III, 28029 Madrid, Spain.; ERN-ITHACA, European Reference Network on Rare Malformations Syndromes, Intellectual and Other Neuro-Developmental Disorders, 75019 Paris, France.
Cazalla M; Instituto de Genética Médica y Molecular (INGEMM), Instituto de Investigación del Hospital Universitario La Paz (IdiPaz), Hospital Universitario La Paz, 28046 Madrid, Spain.; CIBERER, Centro de Investigación Biomédica de Enfermedades Raras en Red, Instituto de Salud Carlos III, 28029 Madrid, Spain.; ERN-ITHACA, European Reference Network on Rare Malformations Syndromes, Intellectual and Other Neuro-Developmental Disorders, 75019 Paris, France.
Silván C; Instituto de Genética Médica y Molecular (INGEMM), Instituto de Investigación del Hospital Universitario La Paz (IdiPaz), Hospital Universitario La Paz, 28046 Madrid, Spain.; CIBERER, Centro de Investigación Biomédica de Enfermedades Raras en Red, Instituto de Salud Carlos III, 28029 Madrid, Spain.; ERN-ITHACA, European Reference Network on Rare Malformations Syndromes, Intellectual and Other Neuro-Developmental Disorders, 75019 Paris, France.
Arias P; Instituto de Genética Médica y Molecular (INGEMM), Instituto de Investigación del Hospital Universitario La Paz (IdiPaz), Hospital Universitario La Paz, 28046 Madrid, Spain.; CIBERER, Centro de Investigación Biomédica de Enfermedades Raras en Red, Instituto de Salud Carlos III, 28029 Madrid, Spain.; ERN-ITHACA, European Reference Network on Rare Malformations Syndromes, Intellectual and Other Neuro-Developmental Disorders, 75019 Paris, France.
Valverde D; Centro de Investigación en Nonomateriais e Biomedicina (CINBIO), Universidad de Vigo, 36310 Vigo, Spain.; Instituto de Investigación Sanitaria Galicia Sur, Hospital Álvaro Cunqueiro, 36310 Vigo, Spain.; Centro de Investigaciones Biomédicas (CINBIO), 36310 Vigo, Spain.
de Jesús-Pérez V; Division of Pulmonary and Critical Care Medicine, Department of Medicine, Stanford University, Stanford, CA 94305, USA.
Lapunzina P; Instituto de Genética Médica y Molecular (INGEMM), Instituto de Investigación del Hospital Universitario La Paz (IdiPaz), Hospital Universitario La Paz, 28046 Madrid, Spain.; CIBERER, Centro de Investigación Biomédica de Enfermedades Raras en Red, Instituto de Salud Carlos III, 28029 Madrid, Spain.; ERN-ITHACA, European Reference Network on Rare Malformations Syndromes, Intellectual and Other Neuro-Developmental Disorders, 75019 Paris, France.
Escribano-Subías P; Unidad Multidisciplinar de Hipertensión Pulmonar, Servicio de Cardiología, Hospital Universitario 12 de Octubre, 28041 Madrid, Spain.; ERN-LUNG, European Reference Network on Rare Lung Diseases (Pulmonary Hypertension), 60596 Frankfurt am Main, Germany.; CIBERCV, Centro de Investigación Biomédica en Red de Enfermedades Cardiovasculares, Instituto de Salud Carlos III, 28029 Madrid, Spain.
Tenorio-Castano J; Instituto de Genética Médica y Molecular (INGEMM), Instituto de Investigación del Hospital Universitario La Paz (IdiPaz), Hospital Universitario La Paz, 28046 Madrid, Spain.; CIBERER, Centro de Investigación Biomédica de Enfermedades Raras en Red, Instituto de Salud Carlos III, 28029 Madrid, Spain.; ERN-ITHACA, European Reference Network on Rare Malformations Syndromes, Intellectual and Other Neuro-Developmental Disorders, 75019 Paris, France.
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Źródło:
Genes [Genes (Basel)] 2023 Oct 20; Vol. 14 (10). Date of Electronic Publication: 2023 Oct 20.
Typ publikacji:
Review; Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Pulmonary Arterial Hypertension*/genetics
Pulmonary Arterial Hypertension*/diagnosis
Heart Defects, Congenital*
Heart Septal Defects*
Humans ; Familial Primary Pulmonary Hypertension ; Pulmonary Artery ; SOXF Transcription Factors/genetics
Czasopismo naukowe
Tytuł:
RGS5 as a Biomarker of Pericytes, Involvement in Vascular Remodeling and Pulmonary Arterial Hypertension.
Autorzy:
Lu G; Department of Physiology and Pathophysiology, National Key Discipline of Cell Biology, Fourth Military Medical University, Xi'an, 710032, People's Republic of China.; State Key Laboratory of Holistic Integrative Management of Gastrointestinal Cancers and National Clinical Research Center for Digestive Diseases, Xijing Hospital of Digestive Diseases, Fourth Military Medical University, Xi'an, 710032, People's Republic of China.
Du R; Institute for Biomedical Sciences of Pain, Tangdu Hospital, Fourth Military Medical University, Xi'an, 710038, People's Republic of China.
Liu Y; Department of Physiology and Pathophysiology, National Key Discipline of Cell Biology, Fourth Military Medical University, Xi'an, 710032, People's Republic of China.
Zhang S; Department of Physiology and Pathophysiology, National Key Discipline of Cell Biology, Fourth Military Medical University, Xi'an, 710032, People's Republic of China.
Li J; Department of Physiology and Pathophysiology, National Key Discipline of Cell Biology, Fourth Military Medical University, Xi'an, 710032, People's Republic of China.
Pei J; Department of Physiology and Pathophysiology, National Key Discipline of Cell Biology, Fourth Military Medical University, Xi'an, 710032, People's Republic of China.
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Źródło:
Vascular health and risk management [Vasc Health Risk Manag] 2023 Oct 20; Vol. 19, pp. 673-688. Date of Electronic Publication: 2023 Oct 20 (Print Publication: 2023).
Typ publikacji:
Journal Article
MeSH Terms:
Pulmonary Arterial Hypertension*/genetics
Pulmonary Arterial Hypertension*/metabolism
RGS Proteins*/genetics
RGS Proteins*/metabolism
Mice ; Humans ; Animals ; Vascular Remodeling ; Pericytes/metabolism ; Muscle, Smooth, Vascular ; Familial Primary Pulmonary Hypertension ; Biomarkers ; Pulmonary Artery/metabolism ; Cell Proliferation
Czasopismo naukowe
Tytuł:
Distensibility, an Early Disease Marker of Pulmonary Vascular Health: Ready for Clinical Application.
Autorzy:
Raza F; Department of Medicine-Cardiovascular Division University of Wisconsin-Madison Madison WI USA.
Chesler NC; Edwards Lifesciences Foundation Cardiovascular Innovation and Research Center and Department of Biomedical Engineering University of California, Irvine Irvine CA USA.
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Źródło:
Journal of the American Heart Association [J Am Heart Assoc] 2023 Oct 17; Vol. 12 (20), pp. e031605. Date of Electronic Publication: 2023 Oct 10.
Typ publikacji:
Editorial; Comment
MeSH Terms:
Pulmonary Arterial Hypertension*/physiopathology
Hypertension, Pulmonary*/diagnosis
Hypertension, Pulmonary*/physiopathology
Humans ; Pulmonary Artery/physiopathology ; Familial Primary Pulmonary Hypertension/physiopathology ; Internet
Opinia redakcyjna
Tytuł:
Safety and efficacy of transitioning from selexipag to oral treprostinil in pulmonary arterial hypertension: Findings from the ADAPT registry.
Autorzy:
Lachant D; University of Rochester Medical Center, 601 Elmwood Ave, Rochester, NY, 14642, USA. Electronic address: daniel_.
Minkin R; New York-Presbyterian Brooklyn Methodist Hospital, 506 6th St, Brooklyn, NY, 11215, USA. Electronic address: .
Swisher J; Fort Sanders Regional Medical Center, 1901 Clinch Ave, Knoxville, TN, 37916, USA. Electronic address: .
Mogri M; Baylor Scott & White Health, 301 North Washington Avenue Dallas, TX, 75246, USA. Electronic address: .
Zolty R; University of Nebraska Medical Center, 42nd and Emile St, Omaha, NE, 68198, USA. Electronic address: .
Hwang S; United Therapeutics Corporation, 55 TW Alexander Dr, Durham, NC, 27709, USA. Electronic address: .
Seaman S; United Therapeutics Corporation, 55 TW Alexander Dr, Durham, NC, 27709, USA. Electronic address: .
Broderick M; United Therapeutics Corporation, 55 TW Alexander Dr, Durham, NC, 27709, USA. Electronic address: .
Sahay S; Houston Methodist Lung Center, 6445 Main St Floor 22, Houston, TX, 77030, USA. Electronic address: .
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Źródło:
Pulmonary pharmacology & therapeutics [Pulm Pharmacol Ther] 2023 Oct; Vol. 82, pp. 102232. Date of Electronic Publication: 2023 Jul 13.
Typ publikacji:
Multicenter Study; Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Pulmonary Arterial Hypertension*/drug therapy
Hypertension, Pulmonary*/drug therapy
Humans ; Antihypertensive Agents ; Prospective Studies ; Administration, Oral ; Epoprostenol/adverse effects ; Familial Primary Pulmonary Hypertension/drug therapy ; Registries
Czasopismo naukowe
Tytuł:
Risk factors of acute cerebral infarction in patients with primary hypertension.
Autorzy:
Zheng D; Department of Laboratory, People's Hospital of Honghuagang District, 134 Linjiapo Road, Zunyi City, 563000, Guizhou Province, China. .
Li X; Department of Laboratory, People's Hospital of Honghuagang District, 134 Linjiapo Road, Zunyi City, 563000, Guizhou Province, China.
Fu Y; Department of Laboratory, People's Hospital of Honghuagang District, 134 Linjiapo Road, Zunyi City, 563000, Guizhou Province, China.
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Źródło:
Irish journal of medical science [Ir J Med Sci] 2023 Oct; Vol. 192 (5), pp. 2441-2445. Date of Electronic Publication: 2022 Nov 19.
Typ publikacji:
Journal Article
MeSH Terms:
Stroke*/complications
Brain Ischemia*
Hypertension*/complications
Hypertension*/epidemiology
Diabetes Mellitus*/epidemiology
Humans ; Cerebral Infarction/diagnostic imaging ; Cerebral Infarction/epidemiology ; Cerebral Infarction/etiology ; Risk Factors ; Acute Disease ; Essential Hypertension
Czasopismo naukowe
Tytuł:
Severe Pulmonary Arterial Hypertension in Healthy Young Infants: Single Center Experience.
Autorzy:
Aroor S; Department of Paediatrics, Kasturba Medical College (Manipal Academy of Higher Education), Manipal, Karnataka.
Handattu K; Department of Paediatrics, Kasturba Medical College (Manipal Academy of Higher Education), Manipal, Karnataka. Correspondence to: Dr Koushik Handattu, Assosciate Professor, Department of Pediatrics, Kasturba Medical College (Manipal Academy of Higher Education), Manipal, Karnataka. .
Mundkur SC; Department of Paediatrics, Kasturba Medical College (Manipal Academy of Higher Education), Manipal, Karnataka.
Verma A; Department of Paediatrics, Kasturba Medical College (Manipal Academy of Higher Education), Manipal, Karnataka.
Samuel PC; Department of Paediatrics, Kasturba Medical College (Manipal Academy of Higher Education), Manipal, Karnataka.
Teli AS; Department of Cardiology, Kasturba Medical College (Manipal Academy of Higher Education), Manipal, Karnataka.
Banga G; Department of Cardiology, Kasturba Medical College (Manipal Academy of Higher Education), Manipal, Karnataka.
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Źródło:
Indian pediatrics [Indian Pediatr] 2023 Sep 15; Vol. 60 (9), pp. 748-751. Date of Electronic Publication: 2023 May 30.
Typ publikacji:
Journal Article
MeSH Terms:
Hypertension, Pulmonary*/diagnosis
Pulmonary Arterial Hypertension*/drug therapy
Ventricular Dysfunction*/drug therapy
Humans ; Infant ; Aged ; Retrospective Studies ; Familial Primary Pulmonary Hypertension/drug therapy ; Vasodilator Agents/therapeutic use ; Thiamine/therapeutic use
Czasopismo naukowe
Tytuł:
Predictors of the response to phosphodiesterase-5 inhibitors in pulmonary arterial hypertension: an analysis of the Spanish registry.
Autorzy:
Garcia AR; Department of Pulmonary Medicine, Hospital Clínic-IDIBAPS, University of Barcelona, Barcelona, Spain.; Biomedical Research Networking Center on Respiratory Diseases (CIBERES), Madrid, Spain.
Blanco I; Department of Pulmonary Medicine, Hospital Clínic-IDIBAPS, University of Barcelona, Barcelona, Spain.; Biomedical Research Networking Center on Respiratory Diseases (CIBERES), Madrid, Spain.
Ramon L; Department of Pulmonary Medicine, Hospital Clínic-IDIBAPS, University of Barcelona, Barcelona, Spain.; Biomedical Research Networking Center on Respiratory Diseases (CIBERES), Madrid, Spain.
Pérez-Sagredo J; Department of Pulmonary Medicine, Hospital El Bierzo, León, Spain.
Guerra-Ramos FJ; Department of Pulmonary Medicine, Complejo Hospitalario Universitario Insular-Materno Infantil, Las Palmas, Spain.
Martín-Ontiyuelo C; Department of Pulmonary Medicine, Hospital Clínic-IDIBAPS, University of Barcelona, Barcelona, Spain.; Biomedical Research Networking Center on Respiratory Diseases (CIBERES), Madrid, Spain.
Tura-Ceide O; Department of Pulmonary Medicine, Hospital Clínic-IDIBAPS, University of Barcelona, Barcelona, Spain.; Biomedical Research Networking Center on Respiratory Diseases (CIBERES), Madrid, Spain.
Pastor-Pérez F; Cardiology Department, Hospital Clínico Universitario Virgen de la Arrixaca, Murcia, Spain.
Escribano-Subías P; Pulmonary Hypertension Unit, Cardiology Department, Hospital Universitario 12 de Octubre, Madrid, Spain.; Biomedical Research Networking Center on Cardiovascular Diseases (CIBERCV), Madrid, Spain.
Barberà JA; Department of Pulmonary Medicine, Hospital Clínic-IDIBAPS, University of Barcelona, Barcelona, Spain. .; Biomedical Research Networking Center on Respiratory Diseases (CIBERES), Madrid, Spain. .
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Źródło:
Respiratory research [Respir Res] 2023 Sep 15; Vol. 24 (1), pp. 223. Date of Electronic Publication: 2023 Sep 15.
Typ publikacji:
Journal Article
MeSH Terms:
Pulmonary Arterial Hypertension*/diagnosis
Pulmonary Arterial Hypertension*/drug therapy
Pulmonary Arterial Hypertension*/epidemiology
HIV Infections*
Humans ; Male ; Cyclic Nucleotide Phosphodiesterases, Type 5 ; Phosphodiesterase 5 Inhibitors/therapeutic use ; Familial Primary Pulmonary Hypertension ; Registries
Czasopismo naukowe
Tytuł:
Plasma untargeted metabolomics with proteinase K discloses phospholipid signature associated with pulmonary arterial hypertension.
Autorzy:
Wawrzyniak R; Department of Biopharmaceutics and Pharmacodynamics, Medical University of Gdańsk, Hallera 107, 80-416, Gdańsk, Poland. .
Biesemans M; Department of Biopharmaceutics and Pharmacodynamics, Medical University of Gdańsk, Hallera 107, 80-416, Gdańsk, Poland.
Kugacka-Dąbrowska A; Department of Cardiology and Electrotherapy, Medical University of Gdansk, Debinki 7, 80-210, Gdańsk, Poland.
Lewicka E; Department of Cardiology and Electrotherapy, Medical University of Gdansk, Debinki 7, 80-210, Gdańsk, Poland.
Bartoszewski R; Department of Biophysics, Faculty of Biotechnology, University of Wroclaw, Ul. F. Joliot-Curie 14A, 50-383, Wrocław, Poland.
Markuszewski MJ; Department of Biopharmaceutics and Pharmacodynamics, Medical University of Gdańsk, Hallera 107, 80-416, Gdańsk, Poland.
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Źródło:
Scientific reports [Sci Rep] 2023 Sep 15; Vol. 13 (1), pp. 15280. Date of Electronic Publication: 2023 Sep 15.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Pulmonary Arterial Hypertension*
Hypertension, Pulmonary*
Humans ; Endopeptidase K ; Familial Primary Pulmonary Hypertension ; Metabolomics ; Pulmonary Artery
Czasopismo naukowe
Tytuł:
Sex-related differences for uric acid in the prediction of cardiovascular events in essential hypertension. A population prospective study.
Autorzy:
Perticone M; Department of Medical and Surgical Sciences, University Magna Græcia of Catanzaro, Viale Europa, 88100, Catanzaro, Italy.
Maio R; Geriatric Unit, Azienda Ospedaliero Universitaria R. Dulbecco, Catanzaro, Italy.
Shehaj E; Cardiology and CICU Unit, Giovanni Paolo II Hospital, Lamezia Terme, Catanzaro, Italy.
Gigliotti S; Department of Health Sciences, Magna Graecia University of Catanzaro, Catanzaro, Italy.
Caroleo B; Internal Medicine Unit, Basso Ionio Hospital, Soverato, Catanzaro, Italy.
Suraci E; Internal Medicine Unit, Azienda Ospedaliero Universitaria R. Dulbecco, Catanzaro, Italy.
Sciacqua A; Department of Medical and Surgical Sciences, University Magna Græcia of Catanzaro, Viale Europa, 88100, Catanzaro, Italy.
Andreozzi F; Department of Medical and Surgical Sciences, University Magna Græcia of Catanzaro, Viale Europa, 88100, Catanzaro, Italy.
Perticone F; Department of Medical and Surgical Sciences, University Magna Græcia of Catanzaro, Viale Europa, 88100, Catanzaro, Italy. .
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Źródło:
Cardiovascular diabetology [Cardiovasc Diabetol] 2023 Nov 01; Vol. 22 (1), pp. 298. Date of Electronic Publication: 2023 Nov 01.
Typ publikacji:
Journal Article
MeSH Terms:
Uric Acid*
Hypertension*
Humans ; Male ; Female ; Prospective Studies ; Risk Factors ; Sex Characteristics ; Essential Hypertension
Czasopismo naukowe
Tytuł:
Prostaglandin and prostaglandin receptors: present and future promising therapeutic targets for pulmonary arterial hypertension.
Autorzy:
Zeng C; Department of Cardiology, The Second Xiangya Hospital of Central South University, No.139, Middle Ren-min Road, Changsha, 410011, Hunan Province, People's Republic of China.
Liu J; Department of Cardiology, The Second Xiangya Hospital of Central South University, No.139, Middle Ren-min Road, Changsha, 410011, Hunan Province, People's Republic of China.
Zheng X; Department of Cardiology, The Second Xiangya Hospital of Central South University, No.139, Middle Ren-min Road, Changsha, 410011, Hunan Province, People's Republic of China.
Hu X; Department of Cardiology, The Second Xiangya Hospital of Central South University, No.139, Middle Ren-min Road, Changsha, 410011, Hunan Province, People's Republic of China. .
He Y; Department of Cardiology, The Second Xiangya Hospital of Central South University, No.139, Middle Ren-min Road, Changsha, 410011, Hunan Province, People's Republic of China. .
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Źródło:
Respiratory research [Respir Res] 2023 Nov 01; Vol. 24 (1), pp. 263. Date of Electronic Publication: 2023 Nov 01.
Typ publikacji:
Journal Article; Review
MeSH Terms:
Prostaglandins*
Pulmonary Arterial Hypertension*/drug therapy
Humans ; Receptors, Prostaglandin ; Vascular Remodeling ; Familial Primary Pulmonary Hypertension ; Epoprostenol/therapeutic use ; Prostaglandins I ; Inflammation/drug therapy ; Pulmonary Artery
Czasopismo naukowe
Tytuł:
Contribution of NOS3AS Variants to Susceptibility to Essential Hypertension: A Study in Kermanshah Province, Western Iran.
Autorzy:
Karami B; Department of Clinical Biochemistry, School of Medicine, Kermanshah University of Medical Sciences, Kermanshah, Iran.
Azimi A; Medical Genetics Laboratory, Kermanshah University of Medical Sciences, Kermanshah, Iran.
Rahimi Z; Department of Clinical Biochemistry, School of Medicine, Kermanshah University of Medical Sciences, Kermanshah, Iran.
Mahmoudi S; Cardiovascular Research Center, Health Institute, Kermanshah University of Medical Sciences, Kermanshah, Iran.
Jalilian N; Department of Clinical Biochemistry, School of Medicine, Kermanshah University of Medical Sciences, Kermanshah, Iran. .
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Źródło:
Biochemical genetics [Biochem Genet] 2023 Oct; Vol. 61 (5), pp. 2149-2158. Date of Electronic Publication: 2023 Mar 26.
Typ publikacji:
Journal Article
MeSH Terms:
Nitric Oxide Synthase Type III*/genetics
Hypertension*/genetics
Humans ; Iran ; Essential Hypertension/genetics ; Genetic Predisposition to Disease
Czasopismo naukowe

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