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Wyszukujesz frazę ""Kuehn EW"" wg kryterium: Autor


Wyświetlanie 1-8 z 8
Tytuł:
Identification of pathological transcription in autosomal dominant polycystic kidney disease epithelia.
Autorzy:
Friedrich S; Renal Division, Department of Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Hugstetterstrasse 55, 79106, Freiburg, Germany.; Department of General Pediatrics, Adolescent Medicine and Neonatology, Center for Pediatrics, Medical Center, Faculty of Medicine, University of Freiburg, Mathildenstrasse 1, 79106, Freiburg, Germany.
Müller H; Renal Division, Department of Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Hugstetterstrasse 55, 79106, Freiburg, Germany.
Riesterer C; Renal Division, Department of Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Hugstetterstrasse 55, 79106, Freiburg, Germany.
Schüller H; Renal Division, Department of Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Hugstetterstrasse 55, 79106, Freiburg, Germany.
Friedrich K; Renal Division, Department of Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Hugstetterstrasse 55, 79106, Freiburg, Germany.
Wörner CL; Renal Division, Department of Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Hugstetterstrasse 55, 79106, Freiburg, Germany.
Busch T; Renal Division, Department of Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Hugstetterstrasse 55, 79106, Freiburg, Germany.
Viau A; Imagine Institute, Laboratory of Hereditary Kidney Diseases, INSERM UMR 1163, Université de Paris, 75015, Paris, France.
Kuehn EW; Renal Division, Department of Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Hugstetterstrasse 55, 79106, Freiburg, Germany.; CIBSS - Centre for Integrative Biological Signalling Studies, Freiburg, Germany.
Köttgen M; Renal Division, Department of Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Hugstetterstrasse 55, 79106, Freiburg, Germany. .; CIBSS - Centre for Integrative Biological Signalling Studies, Freiburg, Germany. .
Hofherr A; Renal Division, Department of Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Hugstetterstrasse 55, 79106, Freiburg, Germany. .
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Źródło:
Scientific reports [Sci Rep] 2021 Jul 23; Vol. 11 (1), pp. 15139. Date of Electronic Publication: 2021 Jul 23.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Epithelial Cells/*pathology
Epithelium/*pathology
Polycystic Kidney, Autosomal Dominant/*genetics
Transcription, Genetic/*genetics
Animals ; Cells, Cultured ; Gene Expression Profiling/methods ; Gene Expression Regulation/genetics ; Mice ; Mice, Inbred C57BL ; Mutation/genetics ; Polycystic Kidney Diseases/genetics ; Polycystic Kidney Diseases/pathology ; Polycystic Kidney, Autosomal Dominant/pathology ; Signal Transduction/genetics ; TRPP Cation Channels/genetics
SCR Disease Name:
Potter Type III Polycystic Kidney Disease
Czasopismo naukowe
Tytuł:
A COL4A5 mutation with glomerular disease and signs of chronic thrombotic microangiopathy.
Autorzy:
Wuttke M; Renal Division, Department of Internal Medicine , Medical Center - University of Freiburg , Freiburg , Germany.
Seidl M; Institute for Surgical Pathology , Medical Center - University of Freiburg , Freiburg , Germany ; Center for Chronic Immunodeficiency (CCI) , Medical Center - University of Freiburg , Freiburg , Germany.
Malinoc A; Renal Division, Department of Internal Medicine , Medical Center - University of Freiburg , Freiburg , Germany.
Prischl FC; Nephrology, 4th Department of Internal Medicine , Klinikum Wels-Grieskirchen , Wels , Austria.
Kuehn EW; Renal Division, Department of Internal Medicine , Medical Center - University of Freiburg , Freiburg , Germany.
Walz G; Renal Division, Department of Internal Medicine , Medical Center - University of Freiburg , Freiburg , Germany.
Köttgen A; Renal Division, Department of Internal Medicine , Medical Center - University of Freiburg , Freiburg , Germany.
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Źródło:
Clinical kidney journal [Clin Kidney J] 2015 Dec; Vol. 8 (6), pp. 690-4. Date of Electronic Publication: 2015 Sep 29.
Typ publikacji:
Journal Article
Czasopismo naukowe
Tytuł:
A Cilia Independent Role of Ift88/Polaris during Cell Migration.
Autorzy:
Boehlke C; Department of Nephrology, University Hospital, Freiburg, Germany.
Janusch H; Department of Nephrology, University Hospital, Freiburg, Germany.
Hamann C; Department of Nephrology, University Hospital, Freiburg, Germany.
Powelske C; Department of Nephrology, University Hospital, Freiburg, Germany.
Mergen M; Department of Nephrology, University Hospital, Freiburg, Germany.
Herbst H; Department of Nephrology, University Hospital, Freiburg, Germany.
Kotsis F; Department of Nephrology, University Hospital, Freiburg, Germany.
Nitschke R; Life Imaging Center, Center for Biosystems Analysis, Albert-Ludwig-University, Freiburg, Germany; Center for Biological Signaling Studies (bioss), Albert-Ludwig-University, Freiburg, Germany.
Kuehn EW; Department of Nephrology, University Hospital, Freiburg, Germany; Center for Biological Signaling Studies (bioss), Albert-Ludwig-University, Freiburg, Germany.
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Źródło:
PloS one [PLoS One] 2015 Oct 14; Vol. 10 (10), pp. e0140378. Date of Electronic Publication: 2015 Oct 14 (Print Publication: 2015).
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Cell Movement*
Carrier Proteins/*metabolism
Animals ; Cell Polarity ; Cilia ; Dogs ; Flagella/metabolism ; Kinesins/metabolism ; Madin Darby Canine Kidney Cells
Czasopismo naukowe
Tytuł:
Kinesin-2 mediates apical endosome transport during epithelial lumen formation.
Autorzy:
Li D; Department of Cell and Developmental Biology; School of Medicine; Anschutz Medical Campus; University of Colorado Denver; Aurora, CO USA.
Kuehn EW; Department of Nephrology; University Hospital; Freiburg, Germany ; BIOSS Centre for Biological Signaling Studies; Albert-Ludwigs-Universität Freiburg; Freiburg, Germany.
Prekeris R; Department of Cell and Developmental Biology; School of Medicine; Anschutz Medical Campus; University of Colorado Denver; Aurora, CO USA.
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Źródło:
Cellular logistics [Cell Logist] 2014 Jan 01; Vol. 4 (1), pp. e28928. Date of Electronic Publication: 2014 May 06.
Typ publikacji:
Journal Article
Czasopismo naukowe
Tytuł:
ANKS6 is a central component of a nephronophthisis module linking NEK8 to INVS and NPHP3.
Autorzy:
Hoff S; Department of Medicine, Renal Division, University of Freiburg Medical Center, Freiburg, Germany.
Halbritter J
Epting D
Frank V
Nguyen TM
van Reeuwijk J
Boehlke C
Schell C
Yasunaga T
Helmstädter M
Mergen M
Filhol E
Boldt K
Horn N
Ueffing M
Otto EA
Eisenberger T
Elting MW
van Wijk JA
Bockenhauer D
Sebire NJ
Rittig S
Vyberg M
Ring T
Pohl M
Pape L
Neuhaus TJ
Elshakhs NA
Koon SJ
Harris PC
Grahammer F
Huber TB
Kuehn EW
Kramer-Zucker A
Bolz HJ
Roepman R
Saunier S
Walz G
Hildebrandt F
Bergmann C
Lienkamp SS
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Źródło:
Nature genetics [Nat Genet] 2013 Aug; Vol. 45 (8), pp. 951-6. Date of Electronic Publication: 2013 Jun 23.
Typ publikacji:
Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
MeSH Terms:
Kidney Diseases, Cystic/*genetics
Kinesins/*genetics
Nuclear Proteins/*genetics
Protein Kinases/*genetics
Transcription Factors/*genetics
Animals ; Cilia/metabolism ; Consanguinity ; Exons ; Gene Knockdown Techniques ; Humans ; Introns ; Kidney Diseases, Cystic/metabolism ; Kinesins/metabolism ; Mice ; Mutation ; NIMA-Related Kinases ; Nuclear Proteins/metabolism ; Phenotype ; Polycystic Kidney Diseases/genetics ; Protein Binding ; Protein Interaction Maps ; Protein Kinases/metabolism ; Protein Transport ; Transcription Factors/metabolism ; Xenopus/embryology ; Xenopus/metabolism ; Zebrafish/genetics ; Zebrafish/metabolism ; Zebrafish Proteins/genetics ; Zebrafish Proteins/metabolism
Czasopismo naukowe
Tytuł:
Kif3a guides microtubular dynamics, migration and lumen formation of MDCK cells.
Autorzy:
Boehlke C; Department of Nephrology, University Hospital, Freiburg, Germany.
Kotsis F
Buchholz B
Powelske C
Eckardt KU
Walz G
Nitschke R
Kuehn EW
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Źródło:
PloS one [PLoS One] 2013 May 01; Vol. 8 (5), pp. e62165. Date of Electronic Publication: 2013 May 01 (Print Publication: 2013).
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Kinesins/*physiology
Microtubules/*metabolism
Animals ; Cell Movement ; Cilia/physiology ; Dogs ; Madin Darby Canine Kidney Cells ; Morphogenesis ; Protein Multimerization ; Protein Processing, Post-Translational ; Spheroids, Cellular/cytology ; Spheroids, Cellular/metabolism ; Tight Junctions/metabolism
Czasopismo naukowe
Tytuł:
Primary cilia regulate mTORC1 activity and cell size through Lkb1.
Autorzy:
Boehlke C; Renal Unit, Department of Medicine, University Medical Center, Albert-Ludwig-University of Freiburg, Hugstetter Strasse 55, D-79106 Freiburg, Germany.
Kotsis F
Patel V
Braeg S
Voelker H
Bredt S
Beyer T
Janusch H
Hamann C
Gödel M
Müller K
Herbst M
Hornung M
Doerken M
Köttgen M
Nitschke R
Igarashi P
Walz G
Kuehn EW
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Źródło:
Nature cell biology [Nat Cell Biol] 2010 Nov; Vol. 12 (11), pp. 1115-22. Date of Electronic Publication: 2010 Oct 24.
Typ publikacji:
Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
MeSH Terms:
Cell Size*
Cilia/*metabolism
Protein Serine-Threonine Kinases/*metabolism
Proteins/*metabolism
AMP-Activated Protein Kinases ; Animals ; Calcium/metabolism ; Cell Line ; Cilia/chemistry ; Dogs ; Kinesins/deficiency ; Kinesins/metabolism ; Mechanistic Target of Rapamycin Complex 1 ; Mice ; Mice, Transgenic ; Multiprotein Complexes ; Phosphorylation ; Signal Transduction ; TOR Serine-Threonine Kinases
Czasopismo naukowe
    Wyświetlanie 1-8 z 8

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