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Wyszukujesz frazę ""Mariani, G."" wg kryterium: Autor


Wyświetlanie 1-12 z 12
Tytuł:
Women with congenital factor VII deficiency: clinical phenotype and treatment options from two international studies.
Autorzy:
Napolitano M; Haematology Unit, Thrombosis and Hemostasis Reference Regional Center, University of Palermo, Palermo, Italy. .
Di Minno MN; Division of Cardiology, Department of Advanced Biomedical Sciences, Federico II University, Naples, Italy.
Batorova A; The National Haemophilia Centre, Institute of Haematology and Blood Transfusion, School of Medicine of Comenius University, University Hospital, Bratislava, Slovakia.
Dolce A; National Institute of Statistics, Palermo, Italy.
Giansily-Blaizot M; Laboratory of Haematology, University Hospital, Montpellier, France.
Ingerslev J; Centre for Haemophilia & Thrombosis, University Hospital Skejby, Aarhus, Denmark.
Schved JF; Laboratory of Haematology, University Hospital, Montpellier, France.
Auerswald G; Klinikum Bremen-Mitte, Prof.-Hess Kinderklinik, Bremen, Germany.
Kenet G; National Hemophilia Center, Chaim Sheba Medical Center, Tel Hashomer, Israel.; Sackler School of Medicine, Tel Aviv University, Tel Aviv, Israel.
Karimi M; Haematology Research Center, Shiraz University of Medical Sciences, Shiraz, Iran.
Shamsi T; National Institute of Blood Diseases & Bone Marrow Transplantation, Karachi, Pakistan.
Ruiz de Sáez A; Centro Nacional de Hemophilia, Banco Municipal de Sangre, Caracas, Venezuela.
Dolatkhah R; Haematology and Oncology Research Center, Tabriz University of Medical Sciences, Tabriz, Iran.
Chuansumrit A; Faculty of Medicine Ramathibodi Hospital, Mahidol University, Bangkok, Thailand.
Bertrand MA; CRTH de Besançon, Besançon, France.
Mariani G; Westminster University, London, UK.
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Źródło:
Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2016 Sep; Vol. 22 (5), pp. 752-9. Date of Electronic Publication: 2016 Jun 24.
Typ publikacji:
Journal Article
MeSH Terms:
Coagulants/*therapeutic use
Factor VII Deficiency/*drug therapy
Factor VIIa/*therapeutic use
Adolescent ; Adult ; Aged ; Aged, 80 and over ; Antifibrinolytic Agents/therapeutic use ; Child ; Child, Preschool ; Cohort Studies ; Factor VII/analysis ; Female ; Hemorrhage/epidemiology ; Hemorrhage/prevention & control ; Humans ; Infant ; Male ; Menorrhagia/epidemiology ; Middle Aged ; Phenotype ; Proportional Hazards Models ; ROC Curve ; Recombinant Proteins/therapeutic use ; Registries ; Treatment Outcome ; Young Adult
Czasopismo naukowe
Tytuł:
Replacement therapy in inherited factor VII deficiency: occurrence of adverse events and relation with surgery.
Autorzy:
Napolitano M; Haematology Unit, Thrombosis and Hemostasis Reference Regional Center, Università di Palermo, Palermo, Italy.
Dolce A; National Institute of Statistics, Palermo, Italy.
Batorova A; The National Haemophilia Centre, Institute of Haematology and Blood Transfusion, University Hospital, Bratislava, Slovakia.
Giansily-Blaizot M; Laboratory of Haematology, University Hospital, Montpellier, France.
Ingerslev J; Centre for Haemophilia & Thrombosis, University Hospital Skejby, Aarhus, Denmark.
Mirbehbahani N; Hematology and Oncology Research Center, Golestan University of Medical Sciences, Gorgan, Iran.
Di Minno MN; Department of Clinical Medicine and Surgery, Federico II University, Naples, Italy.
Lopez Fernandez MF; Complejo Hospitalario Universitario A Coruña, A Coruña, Spain.
Karimi M; Haematology Research Center, Shiraz University of Medical Sciences, Shiraz, Iran.
Charoenkwan P; Division of Hematology, Chiang Mai University, Chiang Mai, Thailand.
Kavakli K; Children's Hospital, Ege University Faculty of Medicine, Izmir, Turkey.
Mariani G; Università di Ferrara Medical School, Ferrara, Italy.
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Źródło:
Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2015 Nov; Vol. 21 (6), pp. e513-7. Date of Electronic Publication: 2015 Aug 07.
Typ publikacji:
Letter; Research Support, Non-U.S. Gov't
MeSH Terms:
Factor VII Deficiency/*therapy
Child ; Child, Preschool ; Factor VII Deficiency/complications ; Factor VII Deficiency/surgery ; Female ; Humans ; Infant ; Infant, Newborn ; Male ; Middle Aged ; Young Adult
Raport
Tytuł:
Inhibitors to factor VII in congenital factor VII deficiency.
Autorzy:
Batorova A; The National Haemophilia Centre, University Hospital, Bratislava, Slovakia.
Mariani G
Kavakli K
de Saez AR
Caliskan U
Karimi M
Pinotti M
Napolitano M
Dolce A
Sørensen B
Ingerslev J
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Corporate Authors:
STER Study Group
Źródło:
Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2014 Mar; Vol. 20 (2), pp. e188-91.
Typ publikacji:
Letter; Research Support, Non-U.S. Gov't
MeSH Terms:
Antibodies/*immunology
Factor VII/*immunology
Factor VII Deficiency/*immunology
Antibodies/blood ; Humans
Raport
Tytuł:
Factor VII deficiency: defining the clinical picture and optimizing therapeutic options.
Autorzy:
Lapecorella M; Centro Emofilia e Trombosi, Unità Operativa Medicina Interna 2-Ematologia, Università de L'Aquila, Ospedale San Salvatore, Coppito, L'Aquila, Italy. />Mariani G
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Corporate Authors:
International Registry on Congenital Factor VII Deficiency
Źródło:
Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2008 Nov; Vol. 14 (6), pp. 1170-5.
Typ publikacji:
Journal Article; Review
MeSH Terms:
Mutation*
Registries*
Factor VII/*physiology
Factor VII Deficiency/*genetics
Hemorrhage/*etiology
Age Factors ; Blood Coagulation/physiology ; Coagulants/therapeutic use ; Factor VII Deficiency/diagnosis ; Factor VII Deficiency/drug therapy ; Factor VIIa/therapeutic use ; Female ; Hemorrhage/drug therapy ; Humans ; Infant ; Infant, Newborn ; Male ; Pregnancy ; Prothrombin Time ; Randomized Controlled Trials as Topic ; Rare Diseases ; Recombinant Proteins/therapeutic use ; Severity of Illness Index
Czasopismo naukowe
Tytuł:
Genetic aspects and research development in haemostasis.
Autorzy:
Tuddenham EG; Haemophilia Centre and Haemostasis Unit, Royal Free Hospital, London, United Kingdom.
Ingerslev J
Sørensen LN
Christiansen K
Mariani G
Peyvandi F
Waddington SN
Buckley SM
Kochanek S
Chuah MK
Vandendriessche T
Berntorp E
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Źródło:
Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2008 Jul; Vol. 14 Suppl 3, pp. 113-8.
Typ publikacji:
Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Review
MeSH Terms:
Blood Coagulation Factor Inhibitors/*genetics
Factor VII Deficiency/*complications
Hemostasis/*physiology
Polymorphism, Single Nucleotide/*physiology
Cohort Studies ; Factor VII/genetics ; Factor VII Deficiency/genetics ; Genetic Therapy/trends ; Hemostasis/genetics ; Humans ; Polymorphism, Single Nucleotide/genetics
Czasopismo naukowe
Tytuł:
Congenital factor VII deficiency: therapy with recombinant activated factor VII -- a critical appraisal.
Autorzy:
Mariani G; Department of Internal Medicine and Public Health, University of L'Aquila, L'Aquila, Italy. />Konkle BA
Ingerslev J
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Źródło:
Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2006 Jan; Vol. 12 (1), pp. 19-27.
Typ publikacji:
Journal Article; Review
MeSH Terms:
Factor VII/*therapeutic use
Factor VII Deficiency/*congenital
Acute Disease ; Adolescent ; Adult ; Aged ; Aged, 80 and over ; Child ; Child, Preschool ; Emergencies ; Factor VII Deficiency/therapy ; Factor VIIa ; Female ; Hemorrhage/prevention & control ; Hemostasis/physiology ; Humans ; Infant ; Intraoperative Complications/prevention & control ; Male ; Middle Aged ; Recombinant Proteins/therapeutic use ; Treatment Outcome
Czasopismo naukowe
Tytuł:
How to evaluate phenotype-genotype relationship in rare coagulation haemorrhagic disorders: examples from FVII deficiency.
Autorzy:
Bernardi F; Department of Biochemistry and Molecular Biology, University of Ferrara, 44100 Ferrara, Italy. />Marchetti G
Dolce A
Mariani G
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Źródło:
Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2004 Oct; Vol. 10 Suppl 4, pp. 177-9.
Typ publikacji:
Journal Article; Review
MeSH Terms:
Blood Coagulation Disorders/*genetics
Factor VII Deficiency/*genetics
Hemorrhage/*genetics
Blood Coagulation Disorders/complications ; Blood Coagulation Disorders/congenital ; Blood Coagulation Factors/genetics ; Factor VII Deficiency/complications ; Genotype ; Hemorrhage/etiology ; Humans ; Mutation ; Phenotype ; Polymorphism, Genetic
Czasopismo naukowe
Tytuł:
Clinical picture and management of congenital factor VII deficiency.
Autorzy:
Mariani G; Department of Internal Medicine and Public Health, University of L'Aquila, L'Aquila I-6F100, Italy. />Dolce A
Marchetti G
Bernardi F
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Źródło:
Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2004 Oct; Vol. 10 Suppl 4, pp. 180-3.
Typ publikacji:
Journal Article
MeSH Terms:
Factor VII Deficiency/*diagnosis
Blood Coagulation Factors/therapeutic use ; Factor VII/antagonists & inhibitors ; Factor VII/therapeutic use ; Factor VII Deficiency/congenital ; Female ; Hemorrhage/etiology ; Hemorrhage/prevention & control ; Humans ; Male ; Plasma ; Postoperative Hemorrhage/prevention & control ; Sex Factors
Czasopismo naukowe
    Wyświetlanie 1-12 z 12

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