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Wyszukujesz frazę ""Mice, Inbred mdx"" wg kryterium: Temat


Tytuł:
Running improves muscle mass by activating autophagic flux and inhibiting ubiquitination degradation in mdx mice.
Autorzy:
Zhou S; Guangdong Traditional Medical and Sports Injury Rehabilitation Research Institute, Guangdong Second Provincial General Hospital, 466 Xin Gang Zhong Road, Guangzhou 510317, China.
Lei S; Guangdong Traditional Medical and Sports Injury Rehabilitation Research Institute, Guangdong Second Provincial General Hospital, 466 Xin Gang Zhong Road, Guangzhou 510317, China.
She Y; Guangdong Traditional Medical and Sports Injury Rehabilitation Research Institute, Guangdong Second Provincial General Hospital, 466 Xin Gang Zhong Road, Guangzhou 510317, China.
Shi H; Guangdong Traditional Medical and Sports Injury Rehabilitation Research Institute, Guangdong Second Provincial General Hospital, 466 Xin Gang Zhong Road, Guangzhou 510317, China.
Li Y; Guangdong Traditional Medical and Sports Injury Rehabilitation Research Institute, Guangdong Second Provincial General Hospital, 466 Xin Gang Zhong Road, Guangzhou 510317, China.
Zhou X; Guangdong Traditional Medical and Sports Injury Rehabilitation Research Institute, Guangdong Second Provincial General Hospital, 466 Xin Gang Zhong Road, Guangzhou 510317, China.
Chen R; Guangdong Traditional Medical and Sports Injury Rehabilitation Research Institute, Guangdong Second Provincial General Hospital, 466 Xin Gang Zhong Road, Guangzhou 510317, China. Electronic address: .
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Źródło:
Gene [Gene] 2024 Mar 20; Vol. 899, pp. 148136. Date of Electronic Publication: 2024 Jan 05.
Typ publikacji:
Journal Article
MeSH Terms:
Muscular Dystrophy, Duchenne*
Running*/physiology
Animals ; Mice ; Mice, Inbred mdx ; Mice, Inbred C57BL ; Muscle, Skeletal/metabolism ; Muscle Proteins/metabolism ; Autophagy ; Disease Models, Animal
Czasopismo naukowe
Tytuł:
Beneficial effects of resistance training on both mild and severe mouse dystrophic muscle function as a preclinical option for Duchenne muscular dystrophy.
Autorzy:
Hassani M; Sorbonne Université, Institut de Biologie Paris-Seine, UMR CNRS 8256, INSERM ERL U1164, Biological Adaptation and Ageing, Paris, F-75013 France.
Moutachi D; Sorbonne Université, INSERM, Institut de Myologie, Centre de Recherche en Myologie, F-75013 Paris, France.
Lemaitre M; Sorbonne Université, UMS28, Paris, F-75013 France.
Boulinguiez A; Department of Biological Sciences, Royal Holloway University of London, Surrey, United Kingdom.
Furling D; Sorbonne Université, INSERM, Institut de Myologie, Centre de Recherche en Myologie, F-75013 Paris, France.
Agbulut O; Sorbonne Université, Institut de Biologie Paris-Seine, UMR CNRS 8256, INSERM ERL U1164, Biological Adaptation and Ageing, Paris, F-75013 France.
Ferry A; Sorbonne Université, INSERM, Institut de Myologie, Centre de Recherche en Myologie, F-75013 Paris, France.; Université Paris Cité, F-75006 Paris, France.
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Źródło:
PloS one [PLoS One] 2024 Mar 08; Vol. 19 (3), pp. e0295700. Date of Electronic Publication: 2024 Mar 08 (Print Publication: 2024).
Typ publikacji:
Journal Article
MeSH Terms:
Muscular Dystrophy, Duchenne*/pathology
Resistance Training*
Cyclosporins*/pharmacology
Humans ; Animals ; Mice ; Mice, Inbred mdx ; Calcineurin/metabolism ; Quality of Life ; Muscle, Skeletal/metabolism ; Disease Models, Animal
Czasopismo naukowe
Tytuł:
Enhanced Diaphragm Muscle Function upon Satellite Cell Transplantation in Dystrophic Mice.
Autorzy:
Azzag K; Lillehei Heart Institute, Department of Medicine, University of Minnesota, Minneapolis, MN 55455, USA.
Gransee HM; Department of Anesthesiology and Perioperative Medicine, Mayo Clinic, Rochester, MN 55905, USA.
Magli A; Lillehei Heart Institute, Department of Medicine, University of Minnesota, Minneapolis, MN 55455, USA.
Yamashita AMS; Lillehei Heart Institute, Department of Medicine, University of Minnesota, Minneapolis, MN 55455, USA.
Tungtur S; Lillehei Heart Institute, Department of Medicine, University of Minnesota, Minneapolis, MN 55455, USA.
Ahlquist A; Lillehei Heart Institute, Department of Medicine, University of Minnesota, Minneapolis, MN 55455, USA.
Zhan WZ; Department of Anesthesiology and Perioperative Medicine, Mayo Clinic, Rochester, MN 55905, USA.
Onyebu C; Lillehei Heart Institute, Department of Medicine, University of Minnesota, Minneapolis, MN 55455, USA.
Greising SM; School of Kinesiology, University of Minnesota, Minneapolis, MN 55455, USA.
Mantilla CB; Department of Anesthesiology and Perioperative Medicine, Mayo Clinic, Rochester, MN 55905, USA.; Department of Physiology and Biomedical Engineering, Mayo Clinic, Rochester, MN 55905, USA.
Perlingeiro RCR; Lillehei Heart Institute, Department of Medicine, University of Minnesota, Minneapolis, MN 55455, USA.; Stem Cell Institute, University of Minnesota, Minneapolis, MN 55455, USA.
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Źródło:
International journal of molecular sciences [Int J Mol Sci] 2024 Feb 21; Vol. 25 (5). Date of Electronic Publication: 2024 Feb 21.
Typ publikacji:
Journal Article
MeSH Terms:
Muscular Dystrophy, Duchenne*/genetics
Mice ; Animals ; Diaphragm ; Mice, Inbred mdx ; Muscle, Skeletal ; Cell Transplantation
Czasopismo naukowe
Tytuł:
Hematopoietic Prostaglandin D Synthase Is Increased in Mast Cells and Pericytes in Autopsy Myocardial Specimens from Patients with Duchenne Muscular Dystrophy.
Autorzy:
Hamamura K; Laboratory of Chemical Pharmacology, Faculty of Pharmaceutical Sciences, Daiichi University of Pharmacy, Fukuoka 815-8511, Japan.; Department of Clinical Pharmacokinetics, Faculty of Pharmaceutical Sciences, Kyushu University, 3-1-1 Maidashi Higashi-ku, Fukuoka 812-8582, Japan.
Yoshida Y; Department of Clinical Pharmacokinetics, Faculty of Pharmaceutical Sciences, Kyushu University, 3-1-1 Maidashi Higashi-ku, Fukuoka 812-8582, Japan.
Oyama K; Department of Pharmaceutics, Faculty of Pharmaceutical Sciences, Kyushu University, 3-1-1 Maidashi Higashi-ku, Fukuoka 812-8582, Japan.
Li J; Department of Clinical Pharmacokinetics, Faculty of Pharmaceutical Sciences, Kyushu University, 3-1-1 Maidashi Higashi-ku, Fukuoka 812-8582, Japan.
Kawano S; Department of Clinical Pharmacokinetics, Faculty of Pharmaceutical Sciences, Kyushu University, 3-1-1 Maidashi Higashi-ku, Fukuoka 812-8582, Japan.
Inoue K; Department of Neurology and Rehabilitation Medicine, National Hospital Organization Osaka Toneyama Medical Center, Toneyama 5-1-1, Toyonaka 560-8552, Japan.
Toyooka K; Department of Neurology, National Hospital Organization Osaka Toneyama Medical Center, Toneyama 5-1-1, Toyonaka 560-8552, Japan.
Yamadera M; Department of Clinical Research, National Hospital Organization Osaka Toneyama Medical Center, Toneyama 5-1-1, Toyonaka 560-8552, Japan.
Matsunaga N; Department of Clinical Pharmacokinetics, Faculty of Pharmaceutical Sciences, Kyushu University, 3-1-1 Maidashi Higashi-ku, Fukuoka 812-8582, Japan.
Matsumura T; Department of Neurology, National Hospital Organization Osaka Toneyama Medical Center, Toneyama 5-1-1, Toyonaka 560-8552, Japan.
Aritake K; Laboratory of Chemical Pharmacology, Faculty of Pharmaceutical Sciences, Daiichi University of Pharmacy, Fukuoka 815-8511, Japan.
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Źródło:
International journal of molecular sciences [Int J Mol Sci] 2024 Feb 03; Vol. 25 (3). Date of Electronic Publication: 2024 Feb 03.
Typ publikacji:
Journal Article
MeSH Terms:
Cardiomyopathies*/etiology
Cardiomyopathies*/metabolism
Intramolecular Oxidoreductases*
Lipocalins*
Muscular Dystrophy, Duchenne*/genetics
Animals ; Humans ; Mice ; Disease Models, Animal ; Mast Cells/metabolism ; Mice, Inbred mdx ; Muscle, Skeletal/metabolism ; Myocardium/metabolism ; Pericytes/metabolism
Czasopismo naukowe
Tytuł:
Chloroquine decreases cardiac fibrosis and improves cardiac function in a mouse model of Duchenne muscular dystrophy.
Autorzy:
Hirata T; Department of Pediatrics, Graduate School of Medicine, Kyoto University, Shogoin, Sakyo-ku, Kyoto City, Japan.
Baba S; Department of Pediatrics, Graduate School of Medicine, Kyoto University, Shogoin, Sakyo-ku, Kyoto City, Japan.
Akagi K; Department of Pediatrics, Graduate School of Medicine, Kyoto University, Shogoin, Sakyo-ku, Kyoto City, Japan.
Matsuda K; Department of Pediatrics, Graduate School of Medicine, Kyoto University, Shogoin, Sakyo-ku, Kyoto City, Japan.
Umeda K; Department of Pediatrics, Graduate School of Medicine, Kyoto University, Shogoin, Sakyo-ku, Kyoto City, Japan.
Adachi S; Department of Pediatrics, Graduate School of Medicine, Kyoto University, Shogoin, Sakyo-ku, Kyoto City, Japan.
Heike T; Department of Pediatrics, Graduate School of Medicine, Kyoto University, Shogoin, Sakyo-ku, Kyoto City, Japan.
Takita J; Department of Pediatrics, Graduate School of Medicine, Kyoto University, Shogoin, Sakyo-ku, Kyoto City, Japan.
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Źródło:
PloS one [PLoS One] 2024 Jan 31; Vol. 19 (1), pp. e0297083. Date of Electronic Publication: 2024 Jan 31 (Print Publication: 2024).
Typ publikacji:
Journal Article
MeSH Terms:
Muscular Dystrophy, Duchenne*/pathology
Cardiomyopathies*
Humans ; Mice ; Animals ; Mice, Inbred mdx ; Isoproterenol/pharmacology ; Muscle, Skeletal ; Myocytes, Cardiac/pathology ; Fibrosis ; Disease Models, Animal ; Dystrophin
Czasopismo naukowe
Tytuł:
A phase 2 open-label study of the safety and efficacy of weekly dosing of ATL1102 in patients with non-ambulatory Duchenne muscular dystrophy and pharmacology in mdx mice.
Autorzy:
Woodcock IR; Department of Neurology, The Royal Children's Hospital, Melbourne, Australia.; The Murdoch Children's Research Institute, Melbourne, Australia.; Department of Paediatrics, University of Melbourne, Melbourne, Australia.
Tachas G; Antisense Therapeutics Ltd, Melbourne, Australia.
Desem N; Antisense Therapeutics Ltd, Melbourne, Australia.
Houweling PJ; The Murdoch Children's Research Institute, Melbourne, Australia.; Department of Paediatrics, University of Melbourne, Melbourne, Australia.
Kean M; Department of Medical Imaging, The Royal Children's Hospital, Melbourne, Australia.
Emmanuel J; Department of Medical Imaging, The Royal Children's Hospital, Melbourne, Australia.
Kennedy R; Department of Neurology, The Royal Children's Hospital, Melbourne, Australia.; The Murdoch Children's Research Institute, Melbourne, Australia.; Department of Physiotherapy, University of Melbourne, Melbourne, Australia.
Carroll K; Department of Neurology, The Royal Children's Hospital, Melbourne, Australia.; The Murdoch Children's Research Institute, Melbourne, Australia.
de Valle K; Department of Neurology, The Royal Children's Hospital, Melbourne, Australia.; The Murdoch Children's Research Institute, Melbourne, Australia.; Department of Physiotherapy, University of Melbourne, Melbourne, Australia.
Adams J; The Murdoch Children's Research Institute, Melbourne, Australia.
Lamandé SR; The Murdoch Children's Research Institute, Melbourne, Australia.; Department of Paediatrics, University of Melbourne, Melbourne, Australia.
Coles C; The Murdoch Children's Research Institute, Melbourne, Australia.
Tiong C; The Murdoch Children's Research Institute, Melbourne, Australia.
Burton M; The Murdoch Children's Research Institute, Melbourne, Australia.
Villano D; Department of Neurology, The Royal Children's Hospital, Melbourne, Australia.
Button P; McCloud Consulting Group, Sydney, Australia.
Hogrel JY; Institut de Myologie, GH Pitié-Salpêtrière, Paris, France.
Catling-Seyffer S; Department of Neurology, The Royal Children's Hospital, Melbourne, Australia.; The Murdoch Children's Research Institute, Melbourne, Australia.
Ryan MM; Department of Neurology, The Royal Children's Hospital, Melbourne, Australia.; The Murdoch Children's Research Institute, Melbourne, Australia.; Department of Paediatrics, University of Melbourne, Melbourne, Australia.
Delatycki MB; Victorian Clinical Genetics Service, Melbourne, Australia.; Murdoch Children's Research Institute, Bruce Lefroy Centre for Genetic Health Research, Melbourne, Australia.
Yiu EM; Department of Neurology, The Royal Children's Hospital, Melbourne, Australia.; The Murdoch Children's Research Institute, Melbourne, Australia.; Department of Paediatrics, University of Melbourne, Melbourne, Australia.
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Źródło:
PloS one [PLoS One] 2024 Jan 25; Vol. 19 (1), pp. e0294847. Date of Electronic Publication: 2024 Jan 25 (Print Publication: 2024).
Typ publikacji:
Clinical Trial, Phase II; Journal Article
MeSH Terms:
Muscular Dystrophy, Duchenne*/drug therapy
Muscular Dystrophy, Duchenne*/genetics
Muscular Dystrophy, Duchenne*/complications
Male ; Child ; Animals ; Mice ; Humans ; Mice, Inbred mdx ; Australia ; Muscle, Skeletal/metabolism ; Adrenal Cortex Hormones/adverse effects ; Adrenal Cortex Hormones/metabolism ; Inflammation/metabolism
Czasopismo naukowe
Tytuł:
N-terminal titin fragment: a non-invasive, pharmacodynamic biomarker for microdystrophin efficacy.
Autorzy:
Boehler JF; Solid Biosciences, 500 Rutherford Avenue 3rd Floor, Boston, MA, 02129, USA. .
Brown KJ; Rejuvenate Bio, 11425 Sorrento Valley Road, San Diego, CA, 92121, USA.
Ricotti V; National Institute for Health and Care Research Great Ormond Street Hospital Biomedical Research Centre/University College London Great Ormond Street Institute of Child Health, London, UK.
Morris CA; PHDL Consulting LLC, 43 Sylvanus Wood Lane, Woburn, MA, 01801, USA.
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Źródło:
Skeletal muscle [Skelet Muscle] 2024 Jan 16; Vol. 14 (1), pp. 2. Date of Electronic Publication: 2024 Jan 16.
Typ publikacji:
Journal Article
MeSH Terms:
Proteomics*
Muscular Dystrophy, Duchenne*/genetics
Muscular Dystrophy, Duchenne*/therapy
Humans ; Mice ; Animals ; Dogs ; Connectin/genetics ; Mice, Inbred mdx ; Biomarkers ; Creatine Kinase ; Muscle, Skeletal/metabolism ; Protein Kinases/metabolism
Czasopismo naukowe
Tytuł:
Transcriptional dysregulation of autophagy in the muscle of a mouse model of Duchenne muscular dystrophy.
Autorzy:
Nakashima R; Department of Pharmacology, Sapporo Medical University School of Medicine, South-1, West-17, Chuo-ku, Sapporo, 060-8556, Japan.
Hosoda R; Department of Pharmacology, Sapporo Medical University School of Medicine, South-1, West-17, Chuo-ku, Sapporo, 060-8556, Japan.
Tatekoshi Y; Department of Pharmacology, Sapporo Medical University School of Medicine, South-1, West-17, Chuo-ku, Sapporo, 060-8556, Japan.
Iwahara N; Department of Pharmacology, Sapporo Medical University School of Medicine, South-1, West-17, Chuo-ku, Sapporo, 060-8556, Japan.; Department of Neurology, Sapporo Medical University School of Medicine, Sapporo, Japan.
Saga Y; Department of Pharmacology, Sapporo Medical University School of Medicine, South-1, West-17, Chuo-ku, Sapporo, 060-8556, Japan.
Kuno A; Department of Pharmacology, Sapporo Medical University School of Medicine, South-1, West-17, Chuo-ku, Sapporo, 060-8556, Japan. .
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Źródło:
Scientific reports [Sci Rep] 2024 Jan 16; Vol. 14 (1), pp. 1365. Date of Electronic Publication: 2024 Jan 16.
Typ publikacji:
Journal Article
MeSH Terms:
Muscular Dystrophy, Duchenne*/genetics
Muscular Dystrophy, Duchenne*/metabolism
Humans ; Animals ; Mice ; Dystrophin/genetics ; Mice, Inbred mdx ; Muscle, Skeletal/metabolism ; Autophagy/genetics ; Disease Models, Animal
Czasopismo naukowe
Tytuł:
Evaluation of pro-regenerative and anti-inflammatory effects of isolecanoric acid in the muscle: Potential treatment of Duchenne Muscular Dystrophy.
Autorzy:
Matias-Valiente L; Cardiovascular Development Group, Department of Experimental Biology, Faculty of Experimental Sciences, University of Jaen, Jaen, Spain; Fundación MEDINA, Technology Park of Health Sciences, Granada, Spain.
Sanchez-Fernandez C; Cardiovascular Development Group, Department of Experimental Biology, Faculty of Experimental Sciences, University of Jaen, Jaen, Spain; Fundación MEDINA, Technology Park of Health Sciences, Granada, Spain.
Rodriguez-Outeiriño L; Cardiovascular Development Group, Department of Experimental Biology, Faculty of Experimental Sciences, University of Jaen, Jaen, Spain; Fundación MEDINA, Technology Park of Health Sciences, Granada, Spain.
Ramos MC; Fundación MEDINA, Technology Park of Health Sciences, Granada, Spain.
Díaz C; Fundación MEDINA, Technology Park of Health Sciences, Granada, Spain.
Crespo G; Fundación MEDINA, Technology Park of Health Sciences, Granada, Spain.
González-Menéndez V; Fundación MEDINA, Technology Park of Health Sciences, Granada, Spain.
Genilloud O; Fundación MEDINA, Technology Park of Health Sciences, Granada, Spain.
Reyes F; Fundación MEDINA, Technology Park of Health Sciences, Granada, Spain.
Montolio M; Department of Cell Biology, Physiology and Immunology, Faculty of Biology, University of Barcelona, Spain; Duchenne Parent Project Spain Madrid, Spain.
Hernandez-Torres F; Fundación MEDINA, Technology Park of Health Sciences, Granada, Spain; Department of Biochemistry and Molecular Biology III and Immunology, Faculty of Medicine, University of Granada, Granada, Spain. Electronic address: .
Aranega AE; Cardiovascular Development Group, Department of Experimental Biology, Faculty of Experimental Sciences, University of Jaen, Jaen, Spain; Fundación MEDINA, Technology Park of Health Sciences, Granada, Spain. Electronic address: .
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Źródło:
Biomedicine & pharmacotherapy = Biomedecine & pharmacotherapie [Biomed Pharmacother] 2024 Jan; Vol. 170, pp. 116056. Date of Electronic Publication: 2023 Dec 29.
Typ publikacji:
Journal Article
MeSH Terms:
Muscular Dystrophy, Duchenne*/drug therapy
Muscular Dystrophy, Duchenne*/metabolism
Animals ; Mice ; Humans ; beta Catenin/metabolism ; Glycogen Synthase Kinase 3 beta/metabolism ; Mice, Inbred mdx ; Muscle, Skeletal ; Inflammation/metabolism ; Disease Models, Animal
Czasopismo naukowe
Tytuł:
Astaxanthin Ameliorates Worsened Muscle Dysfunction of MDX Mice Fed with a High-Fat Diet through Reducing Lipotoxicity and Regulating Gut Microbiota.
Autorzy:
Chen Y; Department of Neurology, The First Affiliated Hospital of Soochow University, Suzhou 215006, China.
Ling C; Department of Clinical Nutrition, Dushu Lake Hospital Affiliated to Soochow University, Suzhou 215124, China.
Chen M; Department of Endocrinology and Metabolism, The First Affiliated Hospital of Soochow University, Suzhou 215006, China.
Yu L; Department of Neurology, The First Affiliated Hospital of Soochow University, Suzhou 215006, China.
Yang J; Department of Clinical Nutrition, The First Affiliated Hospital of Soochow University, Suzhou 215031, China.
Fang Q; Department of Neurology, The First Affiliated Hospital of Soochow University, Suzhou 215006, China.; Department of Clinical Nutrition, Dushu Lake Hospital Affiliated to Soochow University, Suzhou 215124, China.
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Źródło:
Nutrients [Nutrients] 2023 Dec 21; Vol. 16 (1). Date of Electronic Publication: 2023 Dec 21.
Typ publikacji:
Journal Article
MeSH Terms:
Gastrointestinal Microbiome*
Humans ; Mice ; Animals ; Male ; Mice, Inbred mdx ; Diet, High-Fat/adverse effects ; Quality of Life ; Mice, Inbred C57BL ; Muscles ; Disease Progression ; Obesity ; Triglycerides ; Xanthophylls
Czasopismo naukowe
Tytuł:
mCherry on Top: A Positive Read-Out Cellular Platform for Screening DMD Exon Skipping Xenopeptide-PMO Conjugates.
Autorzy:
Lessl AL; Pharmaceutical Biotechnology, Department of Pharmacy, LMU Munich, Butenandtstrasse 5-13, 81377 Munich, Germany.
Pöhmerer J; Pharmaceutical Biotechnology, Department of Pharmacy, LMU Munich, Butenandtstrasse 5-13, 81377 Munich, Germany.
Lin Y; Pharmaceutical Biotechnology, Department of Pharmacy, LMU Munich, Butenandtstrasse 5-13, 81377 Munich, Germany.
Wilk U; Pharmaceutical Biotechnology, Department of Pharmacy, LMU Munich, Butenandtstrasse 5-13, 81377 Munich, Germany.
Höhn M; Pharmaceutical Biotechnology, Department of Pharmacy, LMU Munich, Butenandtstrasse 5-13, 81377 Munich, Germany.
Hörterer E; Pharmaceutical Biotechnology, Department of Pharmacy, LMU Munich, Butenandtstrasse 5-13, 81377 Munich, Germany.
Wagner E; Pharmaceutical Biotechnology, Department of Pharmacy, LMU Munich, Butenandtstrasse 5-13, 81377 Munich, Germany.; Center for NanoScience (CeNS), LMU Munich, 80799 Munich, Germany.
Lächelt U; Pharmaceutical Biotechnology, Department of Pharmacy, LMU Munich, Butenandtstrasse 5-13, 81377 Munich, Germany.; Center for NanoScience (CeNS), LMU Munich, 80799 Munich, Germany.; Department of Pharmaceutical Sciences, University of Vienna, Josef-Holaubek-Platz 2, 1090 Vienna, Austria.
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Źródło:
Bioconjugate chemistry [Bioconjug Chem] 2023 Dec 20; Vol. 34 (12), pp. 2263-2274. Date of Electronic Publication: 2023 Nov 22.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Dystrophin*/genetics
Muscular Dystrophy, Duchenne*/genetics
Muscular Dystrophy, Duchenne*/therapy
Mice ; Humans ; Animals ; Mice, Inbred mdx ; HeLa Cells ; Morpholinos ; Exons
Czasopismo naukowe
Tytuł:
Combinatorial activation of the WNT-dependent fibrogenic program by distinct complement subunits in dystrophic muscle.
Autorzy:
Florio F; Department of Cellular, Computational and Integrative Biology (CIBIO), University of Trento, Trento, Italy.; Dulbecco Telethon Institute at University of Trento, Trento, Italy.; Neurology Unit, Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Milan, Italy.
Vencato S; Department of Cellular, Computational and Integrative Biology (CIBIO), University of Trento, Trento, Italy.; Dulbecco Telethon Institute at University of Trento, Trento, Italy.
Papa FT; Department of Cellular, Computational and Integrative Biology (CIBIO), University of Trento, Trento, Italy.; Dulbecco Telethon Institute at University of Trento, Trento, Italy.
Libergoli M; Department of Cellular, Computational and Integrative Biology (CIBIO), University of Trento, Trento, Italy.; Dulbecco Telethon Institute at University of Trento, Trento, Italy.
Kheir E; Department of Cellular, Computational and Integrative Biology (CIBIO), University of Trento, Trento, Italy.; Dulbecco Telethon Institute at University of Trento, Trento, Italy.
Ghzaiel I; Department of Cellular, Computational and Integrative Biology (CIBIO), University of Trento, Trento, Italy.; Dulbecco Telethon Institute at University of Trento, Trento, Italy.
Rando TA; Broad Stem Cell Research Center, University of California Los Angeles, Los Angeles, CA, USA.
Torrente Y; Neurology Unit, Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Milan, Italy.; Stem Cell Laboratory, Dino Ferrari Center, Department of Pathophysiology and Transplantation, University of Milan, Milan, Italy.
Biressi S; Department of Cellular, Computational and Integrative Biology (CIBIO), University of Trento, Trento, Italy.; Dulbecco Telethon Institute at University of Trento, Trento, Italy.
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Źródło:
EMBO molecular medicine [EMBO Mol Med] 2023 Dec 07; Vol. 15 (12), pp. e17405. Date of Electronic Publication: 2023 Nov 06.
Typ publikacji:
Journal Article
MeSH Terms:
Muscle, Skeletal*/metabolism
Muscular Dystrophy, Duchenne*/genetics
Humans ; Mice ; Animals ; Wnt Signaling Pathway ; Fibrosis ; Mice, Inbred mdx
Czasopismo naukowe
Tytuł:
Hypochlorous acid exposure impairs skeletal muscle function and Ca signalling: implications for Duchenne muscular dystrophy pathology.
Autorzy:
Lea TA; School of Human Sciences, University of Western Australia, Perth, Western Australia, Australia.
Panizza PM; School of Human Sciences, University of Western Australia, Perth, Western Australia, Australia.
Arthur PG; School of Molecular Sciences, University of Western Australia, Perth, Western Australia, Australia.
Bakker AJ; School of Human Sciences, University of Western Australia, Perth, Western Australia, Australia.
Pinniger GJ; School of Human Sciences, University of Western Australia, Perth, Western Australia, Australia.
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Źródło:
The Journal of physiology [J Physiol] 2023 Dec; Vol. 601 (23), pp. 5257-5275. Date of Electronic Publication: 2023 Oct 21.
Typ publikacji:
Journal Article
MeSH Terms:
Muscular Dystrophy, Duchenne*
Animals ; Mice ; Hypochlorous Acid/pharmacology ; Hypochlorous Acid/metabolism ; Hypochlorous Acid/therapeutic use ; Peroxidase/metabolism ; Mice, Inbred mdx ; Mice, Inbred C57BL ; Muscle, Skeletal/metabolism ; Inflammation/metabolism ; Disease Models, Animal
Czasopismo naukowe
Tytuł:
Receptor interacting protein kinase-3 mediates both myopathy and cardiomyopathy in preclinical animal models of Duchenne muscular dystrophy.
Autorzy:
Bencze M; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
Periou B; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
Punzón I; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
Barthélémy I; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
Taglietti V; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
Hou C; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
Zaidan L; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
Kefi K; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
Blot S; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
Agbulut O; Institut de Biologie Paris-Seine (IBPS), CNRS UMR 8256, Inserm ERL U1164, Biological Adaptation and Ageing, Sorbonne Université, Paris, France.
Gervais M; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
Derumeaux G; Team Derumeaux, Department of Physiology, Henri Mondor Hospital, FHU-SENEC, AP-HP, U955-IMRB, Université Paris-Est Créteil (UPEC), Créteil, France.
Authier FJ; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
Tiret L; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
Relaix F; Team Relaix, Biology of the Neuromuscular System, U955-IMRB, Inserm, UPEC, ENVA, EFS, Créteil, France.
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Źródło:
Journal of cachexia, sarcopenia and muscle [J Cachexia Sarcopenia Muscle] 2023 Dec; Vol. 14 (6), pp. 2520-2531. Date of Electronic Publication: 2023 Nov 01.
Typ publikacji:
Journal Article
MeSH Terms:
Muscular Dystrophy, Duchenne*/genetics
Cardiomyopathies*/etiology
Animals ; Dogs ; Mice ; Rats ; Mice, Inbred mdx ; Disease Models, Animal ; Protein Kinases
Czasopismo naukowe
Tytuł:
Naringenin improves muscle endurance via activation of the Sp1-ERRγ transcriptional axis.
Autorzy:
Lv Z; National Laboratory of Biomacromolecules, CAS Center for Excellence in Biomacromolecules, Institute of Biophysics, Chinese Academy of Sciences, Beijing 100101, China; University of Chinese Academy of Sciences, Beijing 100049, China.
Meng J; National Laboratory of Biomacromolecules, CAS Center for Excellence in Biomacromolecules, Institute of Biophysics, Chinese Academy of Sciences, Beijing 100101, China.
Yao S; State Key Laboratory of Drug Research and Natural Products Chemistry Department, Shanghai Institute of Materia Medica, Chinese Academy of Sciences, Shanghai 201203, China; University of Chinese Academy of Sciences, Beijing 100049, China; Zhongshan Institute for Drug Discovery, Shanghai Institute of Materia Medica, Chinese Academy of Sciences, Zhongshan 528400, China.
Xiao F; School of Chinese Materia Medica, Nanjing University of Chinese Medicine, Nanjing 210023, China; Drug and Design Center, State Key Laboratory of Drug Research, Shanghai Institute of Materia Medica, Chinese Academy of Sciences, Shanghai 201203, China.
Li S; National Laboratory of Biomacromolecules, CAS Center for Excellence in Biomacromolecules, Institute of Biophysics, Chinese Academy of Sciences, Beijing 100101, China; University of Chinese Academy of Sciences, Beijing 100049, China.
Shi H; National Laboratory of Biomacromolecules, CAS Center for Excellence in Biomacromolecules, Institute of Biophysics, Chinese Academy of Sciences, Beijing 100101, China; University of Chinese Academy of Sciences, Beijing 100049, China.
Cui C; University of Chinese Academy of Sciences, Beijing 100049, China; Drug and Design Center, State Key Laboratory of Drug Research, Shanghai Institute of Materia Medica, Chinese Academy of Sciences, Shanghai 201203, China.
Chen K; University of Chinese Academy of Sciences, Beijing 100049, China; School of Chinese Materia Medica, Nanjing University of Chinese Medicine, Nanjing 210023, China; Drug and Design Center, State Key Laboratory of Drug Research, Shanghai Institute of Materia Medica, Chinese Academy of Sciences, Shanghai 201203, China.
Luo X; University of Chinese Academy of Sciences, Beijing 100049, China; School of Chinese Materia Medica, Nanjing University of Chinese Medicine, Nanjing 210023, China; Drug and Design Center, State Key Laboratory of Drug Research, Shanghai Institute of Materia Medica, Chinese Academy of Sciences, Shanghai 201203, China. Electronic address: .
Ye Y; State Key Laboratory of Drug Research and Natural Products Chemistry Department, Shanghai Institute of Materia Medica, Chinese Academy of Sciences, Shanghai 201203, China; University of Chinese Academy of Sciences, Beijing 100049, China; School of Chinese Materia Medica, Nanjing University of Chinese Medicine, Nanjing 210023, China; School of Life Science and Technology, ShanghaiTech University, Shanghai 201203, China. Electronic address: .
Chen C; National Laboratory of Biomacromolecules, CAS Center for Excellence in Biomacromolecules, Institute of Biophysics, Chinese Academy of Sciences, Beijing 100101, China; University of Chinese Academy of Sciences, Beijing 100049, China; Beijing Institute for Brain Disorders, Capital Medical University, Beijing 100069, China. Electronic address: .
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Źródło:
Cell reports [Cell Rep] 2023 Nov 28; Vol. 42 (11), pp. 113288. Date of Electronic Publication: 2023 Oct 23.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Muscular Dystrophy, Duchenne*/metabolism
Mice ; Animals ; Mice, Inbred mdx ; Muscle, Skeletal/metabolism ; Promoter Regions, Genetic/genetics
Czasopismo naukowe
Tytuł:
Electrical impedance myography detects dystrophin-related muscle changes in mdx mice.
Autorzy:
Hiyoshi T; Neuroscience Translational Medicine, Neuroscience Drug Discovery Unit, Takeda Pharmaceutical Company Limited, 26-1, Muraoka-Higashi 2-Chome, Fujisawa, Kanagawa, 251-8555, Japan.
Zhao F; Center of Excellence for Imaging, Preclinical and Translational Sciences, Takeda Development Center Americas, Inc., 95 Hayden Avenue, Lexington, MA, 02141, USA.
Baba R; Muscular Disease and Neuropathy Unit, Neuroscience Drug Discovery Unit, Takeda Pharmaceutical Company Limited, 26-1, Muraoka-Higashi 2-Chome, Fujisawa, Kanagawa, 251-8555, Japan.
Hirakawa T; Muscular Disease and Neuropathy Unit, Neuroscience Drug Discovery Unit, Takeda Pharmaceutical Company Limited, 26-1, Muraoka-Higashi 2-Chome, Fujisawa, Kanagawa, 251-8555, Japan.
Kuboki R; Muscular Disease and Neuropathy Unit, Neuroscience Drug Discovery Unit, Takeda Pharmaceutical Company Limited, 26-1, Muraoka-Higashi 2-Chome, Fujisawa, Kanagawa, 251-8555, Japan.
Suzuki K; Muscular Disease and Neuropathy Unit, Neuroscience Drug Discovery Unit, Takeda Pharmaceutical Company Limited, 26-1, Muraoka-Higashi 2-Chome, Fujisawa, Kanagawa, 251-8555, Japan.
Tomimatsu Y; Neuroscience Translational Medicine, Neuroscience Drug Discovery Unit, Takeda Pharmaceutical Company Limited, 26-1, Muraoka-Higashi 2-Chome, Fujisawa, Kanagawa, 251-8555, Japan.
O'Donnell P; Neuroscience Translational Medicine, Neuroscience Drug Discovery Unit, Takeda Development Center Americas, Inc., 95 Hayden Avenue, Lexington, MA, 02141, USA.
Han S; Neuroscience Therapeutic Area Unit, Takeda Development Center Americas, Inc., 95 Hayden Avenue, Lexington, MA, 02141, USA.
Zach N; Neuroscience Translational Medicine, Neuroscience Drug Discovery Unit, Takeda Development Center Americas, Inc., 95 Hayden Avenue, Lexington, MA, 02141, USA.
Nakashima M; Neuroscience Translational Medicine, Neuroscience Drug Discovery Unit, Takeda Pharmaceutical Company Limited, 26-1, Muraoka-Higashi 2-Chome, Fujisawa, Kanagawa, 251-8555, Japan. .
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Źródło:
Skeletal muscle [Skelet Muscle] 2023 Nov 18; Vol. 13 (1), pp. 19. Date of Electronic Publication: 2023 Nov 18.
Typ publikacji:
Journal Article
MeSH Terms:
Dystrophin*/genetics
Dystrophin*/metabolism
Muscular Dystrophy, Duchenne*/diagnostic imaging
Muscular Dystrophy, Duchenne*/genetics
Muscular Dystrophy, Duchenne*/pathology
Mice ; Animals ; Mice, Inbred mdx ; Electric Impedance ; Mice, Inbred C57BL ; Muscle, Skeletal/metabolism ; Morpholinos/pharmacology ; Morpholinos/therapeutic use ; Myography ; Biomarkers
Czasopismo naukowe
Tytuł:
Proteome Profiling of the Dystrophic mdx Mice Diaphragm.
Autorzy:
Mucha O; Department of Medical Biotechnology, Faculty of Biochemistry, Biophysics and Biotechnology, Jagiellonian University in Krakow, Gronostajowa 7 Street, 30-387 Kraków, Poland.
Myszka M; Department of Medical Biotechnology, Faculty of Biochemistry, Biophysics and Biotechnology, Jagiellonian University in Krakow, Gronostajowa 7 Street, 30-387 Kraków, Poland.; Doctoral School of Exact and Natural Sciences, Łojasiewicza 11 Street, 30-348 Kraków, Poland.
Podkalicka P; Department of Medical Biotechnology, Faculty of Biochemistry, Biophysics and Biotechnology, Jagiellonian University in Krakow, Gronostajowa 7 Street, 30-387 Kraków, Poland.
Świderska B; Mass Spectrometry Laboratory, Institute of Biochemistry and Biophysics, Polish Academy of Sciences, Pawińskiego 5a Street, 02-106 Warsaw, Poland.
Malinowska A; Mass Spectrometry Laboratory, Institute of Biochemistry and Biophysics, Polish Academy of Sciences, Pawińskiego 5a Street, 02-106 Warsaw, Poland.
Dulak J; Department of Medical Biotechnology, Faculty of Biochemistry, Biophysics and Biotechnology, Jagiellonian University in Krakow, Gronostajowa 7 Street, 30-387 Kraków, Poland.
Łoboda A; Department of Medical Biotechnology, Faculty of Biochemistry, Biophysics and Biotechnology, Jagiellonian University in Krakow, Gronostajowa 7 Street, 30-387 Kraków, Poland.
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Źródło:
Biomolecules [Biomolecules] 2023 Nov 13; Vol. 13 (11). Date of Electronic Publication: 2023 Nov 13.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Diaphragm*/metabolism
Muscular Dystrophy, Duchenne*/genetics
Muscular Dystrophy, Duchenne*/metabolism
Animals ; Mice ; Mice, Inbred mdx ; Proteome/metabolism ; Muscle, Skeletal/metabolism ; Mice, Inbred C57BL
Czasopismo naukowe
Tytuł:
Dimethyl fumarate modulates the dystrophic disease program following short-term treatment.
Autorzy:
Timpani CA; Institute for Health and Sport (IHeS), Victoria University, Melbourne, Victoria, Australia.; Australian Institute for Musculoskeletal Science (AIMSS), St Albans, Victoria, Australia.; Department of Medicine - Western Health, Melbourne Medical School, The University of Melbourne, St Albans, Victoria, Australia.
Kourakis S; Institute for Health and Sport (IHeS), Victoria University, Melbourne, Victoria, Australia.; Australian Institute for Musculoskeletal Science (AIMSS), St Albans, Victoria, Australia.
Debruin DA; Institute for Health and Sport (IHeS), Victoria University, Melbourne, Victoria, Australia.; Australian Institute for Musculoskeletal Science (AIMSS), St Albans, Victoria, Australia.
Campelj DG; Institute for Health and Sport (IHeS), Victoria University, Melbourne, Victoria, Australia.
Pompeani N; Institute for Health and Sport (IHeS), Victoria University, Melbourne, Victoria, Australia.; Florey Institute of Neuroscience and Mental Health, Heidelberg, Victoria, Australia.
Dargahi N; Institute for Health and Sport (IHeS), Victoria University, Melbourne, Victoria, Australia.
Bautista AP; School of Molecular Sciences, The University of Western Australia, Perth, Western Australia, Australia.
Bagaric RM; Institute for Health and Sport (IHeS), Victoria University, Melbourne, Victoria, Australia.; Australian Institute for Musculoskeletal Science (AIMSS), St Albans, Victoria, Australia.
Ritenis EJ; College of Health and Biomedicine, Victoria University, Melbourne, Victoria, Australia.
Sahakian L; Institute for Health and Sport (IHeS), Victoria University, Melbourne, Victoria, Australia.; Department of Medicine - Western Health, Melbourne Medical School, The University of Melbourne, St Albans, Victoria, Australia.
Debrincat D; College of Health and Biomedicine, Victoria University, Melbourne, Victoria, Australia.
Stupka N; Institute for Health and Sport (IHeS), Victoria University, Melbourne, Victoria, Australia.; Australian Institute for Musculoskeletal Science (AIMSS), St Albans, Victoria, Australia.; Department of Medicine - Western Health, Melbourne Medical School, The University of Melbourne, St Albans, Victoria, Australia.
Hafner P; Division of Neuropaediatrics and Developmental Medicine, University Children's Hospital of Basel (UKBB), Basel, Switzerland.
Arthur PG; School of Molecular Sciences, The University of Western Australia, Perth, Western Australia, Australia.
Terrill JR; School of Molecular Sciences, The University of Western Australia, Perth, Western Australia, Australia.
Apostolopoulos V; Institute for Health and Sport (IHeS), Victoria University, Melbourne, Victoria, Australia.; Australian Institute for Musculoskeletal Science (AIMSS), St Albans, Victoria, Australia.
de Haan JB; Basic Science Domain, Oxidative Stress Laboratory, Baker Heart and Diabetes Institute, Melbourne, Victoria, Australia.; Department of Immunology and Pathology, Central Clinical School, Monash University, Melbourne, Victoria, Australia.; Department of Physiology, Anatomy and Microbiology, La Trobe University, Melbourne, Victoria, Australia.; Faculty of Science, Engineering and Technology, Swinburne University, Melbourne, Victoria, Australia.; Baker Department of Cardiometabolic Health, University of Melbourne, Parkville, Victoria, Australia.
Guven N; Department of Medicine - Western Health, Melbourne Medical School, The University of Melbourne, St Albans, Victoria, Australia.
Fischer D; Division of Neuropaediatrics and Developmental Medicine, University Children's Hospital of Basel (UKBB), Basel, Switzerland.
Rybalka E; Institute for Health and Sport (IHeS), Victoria University, Melbourne, Victoria, Australia.; Australian Institute for Musculoskeletal Science (AIMSS), St Albans, Victoria, Australia.; Department of Medicine - Western Health, Melbourne Medical School, The University of Melbourne, St Albans, Victoria, Australia.; Division of Neuropaediatrics and Developmental Medicine, University Children's Hospital of Basel (UKBB), Basel, Switzerland.
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Źródło:
JCI insight [JCI Insight] 2023 Nov 08; Vol. 8 (21). Date of Electronic Publication: 2023 Nov 08.
Typ publikacji:
Journal Article
MeSH Terms:
Dimethyl Fumarate*/pharmacology
Dimethyl Fumarate*/therapeutic use
Muscular Dystrophy, Duchenne*/drug therapy
Muscular Dystrophy, Duchenne*/genetics
Muscular Dystrophy, Duchenne*/pathology
Animals ; Mice ; Mice, Inbred mdx ; Prednisone ; Muscles/pathology
Czasopismo naukowe
Tytuł:
Uridine Administration Promotes Normalization of Heart Mitochondrial Function in Dystrophin-Deficient Mice and Decreases Tissue Fibrosis.
Autorzy:
Dubinin MV; Mari State University, Yoshkar-Ola, Mari El Republic, Russia. .
Belosludtseva NV; Institute of Theoretical and Experimental Biophysics, Russian Academy of Sciences, Pushchino, Moscow region, Russia.
Mikheeva IB; Institute of Theoretical and Experimental Biophysics, Russian Academy of Sciences, Pushchino, Moscow region, Russia.
Chelyadnikova YA; Mari State University, Yoshkar-Ola, Mari El Republic, Russia.
Penkina DK; Mari State University, Yoshkar-Ola, Mari El Republic, Russia.
Vafina AB; Mari State University, Yoshkar-Ola, Mari El Republic, Russia.
Starinets VS; Institute of Theoretical and Experimental Biophysics, Russian Academy of Sciences, Pushchino, Moscow region, Russia.
Kireev II; A. N. Belozersky Institute of Physico-Chemical Biology, M. V. Lomonosov Moscow State University, Moscow, Russia.
Belosludtsev KN; Mari State University, Yoshkar-Ola, Mari El Republic, Russia.; Institute of Theoretical and Experimental Biophysics, Russian Academy of Sciences, Pushchino, Moscow region, Russia.
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Źródło:
Bulletin of experimental biology and medicine [Bull Exp Biol Med] 2023 Nov; Vol. 176 (1), pp. 54-59. Date of Electronic Publication: 2023 Dec 13.
Typ publikacji:
Journal Article
MeSH Terms:
Dystrophin*/genetics
Dystrophin*/metabolism
Muscular Dystrophy, Duchenne*/metabolism
Animals ; Mice ; Mice, Inbred mdx ; Mitochondria, Heart/metabolism ; Fibrosis ; Muscle, Skeletal/metabolism ; Disease Models, Animal
Czasopismo naukowe
Tytuł:
LED therapy plus idebenone treatment targeting calcium and mitochondrial signaling pathways in dystrophic muscle cells.
Autorzy:
da Silva HNM; Department of Structural and Functional Biology, Institute of Biology, University of Campinas, Campinas, Brazil.
Mizobuti DS; Department of Structural and Functional Biology, Institute of Biology, University of Campinas, Campinas, Brazil.
Pereira VA; Department of Structural and Functional Biology, Institute of Biology, University of Campinas, Campinas, Brazil.
da Rocha GL; Department of Structural and Functional Biology, Institute of Biology, University of Campinas, Campinas, Brazil.
da Cruz MV; Department of Structural and Functional Biology, Institute of Biology, University of Campinas, Campinas, Brazil.; Obesity and Comorbidities Research Center (OCRC), Campinas, Brazil.
de Oliveira AG; Department of Structural and Functional Biology, Institute of Biology, University of Campinas, Campinas, Brazil.; Obesity and Comorbidities Research Center (OCRC), Campinas, Brazil.
Silveira LR; Department of Structural and Functional Biology, Institute of Biology, University of Campinas, Campinas, Brazil.; Obesity and Comorbidities Research Center (OCRC), Campinas, Brazil.
Minatel E; Department of Structural and Functional Biology, Institute of Biology, University of Campinas, Campinas, Brazil. .
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Źródło:
Cell stress & chaperones [Cell Stress Chaperones] 2023 Nov; Vol. 28 (6), pp. 773-785. Date of Electronic Publication: 2023 Aug 14.
Typ publikacji:
Journal Article; Research Support, Non-U.S. Gov't
MeSH Terms:
Muscle, Skeletal*/metabolism
Calcium*/metabolism
Mice ; Animals ; Mice, Inbred mdx ; Mice, Inbred C57BL ; Hydrogen Peroxide/metabolism ; Signal Transduction ; Muscle Cells/metabolism ; Disease Models, Animal
Czasopismo naukowe

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