- Tytuł:
- Stimulating VAPB-PTPIP51 ER-mitochondria tethering corrects FTD/ALS mutant TDP43 linked Ca and synaptic defects.
- Autorzy:
- Źródło:
- Acta neuropathologica communications [Acta Neuropathol Commun] 2024 Feb 23; Vol. 12 (1), pp. 32. Date of Electronic Publication: 2024 Feb 23.
- Typ publikacji:
- Journal Article
- MeSH Terms:
-
Amyotrophic Lateral Sclerosis*/pathology
Frontotemporal Dementia*/genetics
Frontotemporal Dementia*/metabolism
Neurodegenerative Diseases*/metabolism
Vesicular Transport Proteins*/genetics
Humans ; Calcium/metabolism ; Endoplasmic Reticulum/metabolism ; Glycogen Synthase Kinase 3 beta/metabolism ; Mitochondria/metabolism ; Protein Tyrosine Phosphatases/metabolism ; Synapses/pathology ; TDP-43 Proteinopathies/metabolism - SCR Disease Name:
- Frontotemporal Dementia With Motor Neuron Disease
Czasopismo naukowe