- Tytuł:
- Plectin Deficiency in Fibroblasts Deranges Intermediate Filament and Organelle Morphology, Migration, and Adhesion.
- Autorzy:
- Źródło:
- The Journal of investigative dermatology [J Invest Dermatol] 2024 Mar; Vol. 144 (3), pp. 547-562.e9. Date of Electronic Publication: 2023 Sep 15.
- Typ publikacji:
- Journal Article
- MeSH Terms:
-
Epidermolysis Bullosa Simplex*/pathology
Muscular Dystrophies */complicationsMuscular Dystrophies */geneticsMuscular Dystrophies */metabolismMuscular Dystrophies , Limb-Girdle*
Humans ; Intermediate Filaments/metabolism ; Plectin/genetics ; Mitochondria/metabolism ; Fibroblasts/metabolism ; Intermediate Filament Proteins/metabolism - SCR Disease Name:
-
Epidermolysa bullosa simplex and limb girdle
muscular dystrophy
Czasopismo naukowe