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Wyszukujesz frazę ""sickle cell"" wg kryterium: Temat


Tytuł:
Sickle cell trait in São Tomé e Príncipe: a population-based prevalence study in women of reproductive age.
Autorzy:
Queiroz G; Centro de Investigação em Antropologia e Saúde (CIAS), Universidade de Coimbra, Coimbra, Portugal. .; NOVA National School of Public Health, Public Health Research Centre, Comprehensive Health Research Center, CHRC, NOVA University Lisbon, Av. Padre Cruz, Lisboa, 1600 - 560, Portugal. .; Unidade de Saúde Pública, Unidade Local de Saúde da Região de Aveiro, Aveiro, Portugal. .
Monteiro C; Hospital Dr. Ayres de Menezes, São Tomé, São Tomé and Príncipe.
Manco L; Centro de Investigação em Antropologia e Saúde (CIAS), Universidade de Coimbra, Coimbra, Portugal.; Departamento de Ciências da Vida, Universidade de Coimbra, Coimbra, Portugal.
Relvas L; Unidade Funcional Hematologia Molecular, Unidade Local de Saúde de Coimbra, Coimbra, Portugal.
Trovoada MJ; Centro Nacional de Endemias, São Tomé, São Tomé and Príncipe.
Leite A; NOVA National School of Public Health, Public Health Research Centre, Comprehensive Health Research Center, CHRC, NOVA University Lisbon, Av. Padre Cruz, Lisboa, 1600 - 560, Portugal.; Department of Epidemiology, Instituto Nacional de Saúde Doutor Ricardo Jorge (INSA), Lisbon, Portugal.
Bento C; Centro de Investigação em Antropologia e Saúde (CIAS), Universidade de Coimbra, Coimbra, Portugal.; Unidade Funcional Hematologia Molecular, Unidade Local de Saúde de Coimbra, Coimbra, Portugal.
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Źródło:
BMC public health [BMC Public Health] 2024 Mar 19; Vol. 24 (1), pp. 850. Date of Electronic Publication: 2024 Mar 19.
Typ publikacji:
Journal Article
MeSH Terms:
Sickle Cell Trait*/epidemiology
Sickle Cell Trait*/genetics
Anemia, Sickle Cell*/epidemiology
Anemia, Sickle Cell*/genetics
Infant, Newborn ; Humans ; Female ; Prevalence ; Cross-Sectional Studies ; Hemoglobins
Czasopismo naukowe
Tytuł:
Assessment of hypoxemia among young adults with sickle cell anaemia in steady state in southwestern Nigeria: a crosssectional study.
Autorzy:
M A A; Department of Physiological Sciences, Faculty of Basic Medical Sciences, College of Health Sciences, Obafemi Awolowo University, Ile-Ife, Nigeria. .
O AI; Department of Haematology and Blood Transfusion, Obafemi Awolowo University Teaching Hospital Complex, Ile-Ife, Nigeria.
M S A; Respiratory Unit, Department of Internal Medicine, Obafemi Awolowo University Teaching Hospital Complex, Ile-Ife, Nigeria.
A BR; Department of Haematology and Blood Transfusion, Obafemi Awolowo University Teaching Hospital Complex, Ile-Ife, Nigeria.; Department of Haematology and Immunology, Faculty of Basic Medical Sciences, College of Health Sciences, Obafemi Awolowo University, Ile-Ife, Nigeria.
O O; Department of Physiological Sciences, Faculty of Basic Medical Sciences, College of Health Sciences, Obafemi Awolowo University, Ile-Ife, Nigeria.
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Źródło:
BMC research notes [BMC Res Notes] 2024 Apr 08; Vol. 17 (1), pp. 100. Date of Electronic Publication: 2024 Apr 08.
Typ publikacji:
Journal Article
MeSH Terms:
Anemia, Sickle Cell*/complications
Anemia, Sickle Cell*/epidemiology
Male ; Female ; Humans ; Young Adult ; Nigeria/epidemiology ; Hypoxia/epidemiology ; Cross-Sectional Studies
Czasopismo naukowe
Tytuł:
Role of hydroxyurea therapy in the prevention of organ damage in sickle cell disease: a systematic review and meta-analysis.
Autorzy:
Khargekar N; Department of Haematogenetics, ICMR-National Institute of Immunohaematology, 13th Floor, New MS Building, KEM Hospital Campus, Mumbai, Parel, 400 012, India. .
Banerjee A; Department of Transfusion Transmitted Disease, ICMR-National Institute of Immunohaematology, 13th Floor, New MS Building, KEM Hospital Campus, Mumbai, Parel, 400 012, India.
Athalye S; Department of Transfusion Transmitted Disease, ICMR-National Institute of Immunohaematology, 13th Floor, New MS Building, KEM Hospital Campus, Mumbai, Parel, 400 012, India.
Mahajan N; Department of Haematogenetics, ICMR-National Institute of Immunohaematology, 13th Floor, New MS Building, KEM Hospital Campus, Mumbai, Parel, 400 012, India.
Kargutkar N; Department of Haematogenetics, ICMR-National Institute of Immunohaematology, 13th Floor, New MS Building, KEM Hospital Campus, Mumbai, Parel, 400 012, India.
Tapase P; Department of Paediatric Immunology & Leukocyte Biology, ICMR-National Institute of Immunohaematology, 13th Floor, New MS Building, KEM Hospital Campus, Parel, Mumbai, 400 012, India.
Madkaikar M; Department of Paediatric Immunology & Leukocyte Biology, ICMR-National Institute of Immunohaematology, 13th Floor, New MS Building, KEM Hospital Campus, Parel, Mumbai, 400 012, India.
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Źródło:
Systematic reviews [Syst Rev] 2024 Feb 08; Vol. 13 (1), pp. 60. Date of Electronic Publication: 2024 Feb 08.
Typ publikacji:
Meta-Analysis; Systematic Review; Journal Article
MeSH Terms:
Hydroxyurea*/therapeutic use
Anemia, Sickle Cell*/complications
Anemia, Sickle Cell*/drug therapy
Humans ; Antisickling Agents/therapeutic use ; Albuminuria/drug therapy ; Blood Transfusion
Czasopismo naukowe
Tytuł:
Acute care utilization among individuals with sickle cell disease and related cardiopulmonary and renal complications.
Autorzy:
Singh A; Department of Pediatrics, Medical College of Wisconsin, Milwaukee, Wisconsin, United States of America.
Brousseau DC; Department of Pediatrics, Nemours Children's Health System, Wilmington, Delaware, United States of America.
Dasgupta M; Department of Pediatrics, Medical College of Wisconsin, Milwaukee, Wisconsin, United States of America.
Shet AS; Laboratory of Sickle Thrombosis and Vascular Biology, Sickle Cell Branch, National Heart, Lung, and Blood Institute, National Institutes of Health, Bethesda, Maryland, United States of America.
Field JJ; Department of Medicine, Medical College of Wisconsin, Milwaukee, Wisconsin, United States of America.; Versiti Blood Center of Wisconsin, Milwaukee, Wisconsin, United States of America.
Brandow AM; Department of Pediatrics, Medical College of Wisconsin, Milwaukee, Wisconsin, United States of America.
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Źródło:
PloS one [PLoS One] 2024 Apr 16; Vol. 19 (4), pp. e0297469. Date of Electronic Publication: 2024 Apr 16 (Print Publication: 2024).
Typ publikacji:
Journal Article
MeSH Terms:
Anemia, Sickle Cell*/complications
Anemia, Sickle Cell*/therapy
Anemia, Sickle Cell*/epidemiology
Adult ; Female ; Humans ; Child ; Male ; Kidney ; Disease Management ; Wisconsin ; Critical Care
Czasopismo naukowe
Tytuł:
A Novel Mechanistic Model for Future Research in the Elements of the ERAS Program in Patients With Sickle Cell Disease.
Autorzy:
Purnell M; is a Graduate Program Chair and Associate Professor, Baptist Health Sciences University, Memphis, Tennessee. Email: .
Rayborn M; is an Associate Professor, Nurse Anesthesia Program, School of Leadership and Advanced Nursing Practice, The University of Southern Mississippi, Hattiesburg, Mississippi.
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Źródło:
AANA journal [AANA J] 2024 Apr; Vol. 92 (2), pp. 87-92.
Typ publikacji:
Journal Article
MeSH Terms:
Enhanced Recovery After Surgery*
Anemia, Sickle Cell*
Humans ; Administration, Intravenous
Czasopismo naukowe
Tytuł:
Birth Prevalence of Sickle Cell Disease and County-Level Social Vulnerability - Sickle Cell Data Collection Program, 11 States, 2016-2020.
Autorzy:
Kayle M
Blewer AL
Pan W
Rothman JA
Polick CS
Rivenbark J
Fisher E
Reyes C
Strouse JJ
Weeks S
Desai JR
Snyder AB
Zhou M
Sutaria A
Valle J
Horiuchi SS
Sontag MK
Miller JI
Singh A
Dasgupta M
Janson IA
Galadanci N
Reeves SL
Latta K
Hurden I
Cromartie SJ
Plaxco AP
Mukhopadhyay A
Smeltzer MP
Hulihan M
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Źródło:
MMWR. Morbidity and mortality weekly report [MMWR Morb Mortal Wkly Rep] 2024 Mar 28; Vol. 73 (12), pp. 248-254. Date of Electronic Publication: 2024 Mar 28.
Typ publikacji:
Journal Article
MeSH Terms:
Ethnicity*
Anemia, Sickle Cell*/epidemiology
Anemia, Sickle Cell*/diagnosis
Female ; Child ; Humans ; Infant, Newborn ; United States/epidemiology ; Prevalence ; Cross-Sectional Studies ; Social Vulnerability ; Minority Groups
Czasopismo naukowe
Tytuł:
Substance use disorder of equimolar oxygen-nitrous oxide mixture in French sickle-cell patients: results of the PHEDRE study.
Autorzy:
Gérardin M; CHU Nantes, Centre d'Evaluation et d'Information sur la Pharmacodépendance-Addictovigilance (CEIP-A), Service de Pharmacologie Clinique, Nantes Université, 9 Quai Moncousu, 44 093, Nantes Cedex 1, France.
Rousselet M; CHU Nantes, Centre d'Evaluation et d'Information sur la Pharmacodépendance-Addictovigilance (CEIP-A), Service de Pharmacologie Clinique, Nantes Université, 9 Quai Moncousu, 44 093, Nantes Cedex 1, France.; CHU Nantes, UIC Psychiatrie et Santé Mentale, Nantes Université, Nantes, France.; CHU Nantes, CHU Tours, INSERM, MethodS in Patients Centered Outcomes and HEalth ResEarch, SPHERE, Nantes Université, Tours Université, Nantes, France.
Couec ML; CHU Nantes, Service de Pédiatrie et d'Oncologie Pédiatrique, Nantes Université, Nantes, France.
Masseau A; CHU Nantes, Service de Médecine Interne, Nantes Université, Nantes, France.
Aquizerate A; CHU Nantes, Centre d'Evaluation et d'Information sur la Pharmacodépendance-Addictovigilance (CEIP-A), Service de Pharmacologie Clinique, Nantes Université, 9 Quai Moncousu, 44 093, Nantes Cedex 1, France.
Authier N; CHU Clermont-Ferrand, Service de Pharmacologie Médicale, Clermont Auvergne Université, Clermont-Ferrand, France.
Deheul S; CHU Lille, Service de Pharmacologie, Lille Université, Lille, France.
Roussin A; CHU Toulouse, Service de Pharmacologie Médicale et Clinique, Toulouse Université, Toulouse, France.
Micallef J; APHM, Service de Pharmacologie Clinique, Hôpital de La Timone, Institut de Neurosciences Des Systèmes, Aix-Marseille Université, Marseille, France.
Djezzar S; APHP Paris, Centre d'Evaluation et d'Information sur la Pharmacodependence-Addictovigilance de Paris, Hôpital Fernand Widal, APHP Paris, Paris, France.
Feuillet F; CHU Nantes, CHU Tours, INSERM, MethodS in Patients Centered Outcomes and HEalth ResEarch, SPHERE, Nantes Université, Tours Université, Nantes, France.; CHU Nantes, DRI, Plateforme de Méthodologie et Biostatistique, Nantes Université, Nantes, France.
Jolliet P; CHU Nantes, Centre d'Evaluation et d'Information sur la Pharmacodépendance-Addictovigilance (CEIP-A), Service de Pharmacologie Clinique, Nantes Université, 9 Quai Moncousu, 44 093, Nantes Cedex 1, France.; CHU Nantes, CHU Tours, INSERM, MethodS in Patients Centered Outcomes and HEalth ResEarch, SPHERE, Nantes Université, Tours Université, Nantes, France.
Grall-Bronnec M; CHU Nantes, UIC Psychiatrie et Santé Mentale, Nantes Université, Nantes, France.; CHU Nantes, CHU Tours, INSERM, MethodS in Patients Centered Outcomes and HEalth ResEarch, SPHERE, Nantes Université, Tours Université, Nantes, France.
Victorri-Vigneau C; CHU Nantes, Centre d'Evaluation et d'Information sur la Pharmacodépendance-Addictovigilance (CEIP-A), Service de Pharmacologie Clinique, Nantes Université, 9 Quai Moncousu, 44 093, Nantes Cedex 1, France. .; CHU Nantes, CHU Tours, INSERM, MethodS in Patients Centered Outcomes and HEalth ResEarch, SPHERE, Nantes Université, Tours Université, Nantes, France. .
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Corporate Authors:
PHEDRE Group
French Addictovigilance Network (FAN)
Źródło:
Orphanet journal of rare diseases [Orphanet J Rare Dis] 2024 Mar 18; Vol. 19 (1), pp. 124. Date of Electronic Publication: 2024 Mar 18.
Typ publikacji:
Clinical Study; Journal Article
MeSH Terms:
Anemia, Sickle Cell*/drug therapy
Substance-Related Disorders*/epidemiology
Substance-Related Disorders*/complications
Substance-Related Disorders*/drug therapy
Humans ; Analgesics/therapeutic use ; Nitrous Oxide/therapeutic use ; Nitrous Oxide/adverse effects ; Oxygen ; Pain/drug therapy
Czasopismo naukowe
Tytuł:
On the feasibility of malaria hypothesis.
Autorzy:
Habibzadeh F; Global Virus Network (GVN), Middle East Region, Shiraz, Iran. .
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Źródło:
Scientific reports [Sci Rep] 2024 Mar 09; Vol. 14 (1), pp. 5800. Date of Electronic Publication: 2024 Mar 09.
Typ publikacji:
Journal Article
MeSH Terms:
Malaria*/genetics
Anemia, Sickle Cell*/genetics
Child ; Female ; Humans ; Feasibility Studies ; Hemoglobin, Sickle/genetics ; Gene Frequency
Czasopismo naukowe
Tytuł:
Bone Health Impairment in Patients with Hemoglobinopathies: From Biological Bases to New Possible Therapeutic Strategies.
Autorzy:
Di Paola A; Department of Woman, Child and General and Specialist Surgery, University of Campania 'Luigi Vanvitelli', 80138 Naples, Italy.
Marrapodi MM; Department of Woman, Child and General and Specialist Surgery, University of Campania 'Luigi Vanvitelli', 80138 Naples, Italy.
Di Martino M; Department of Woman, Child and General and Specialist Surgery, University of Campania 'Luigi Vanvitelli', 80138 Naples, Italy.
Giliberti G; Department of Experimental Medicine, University of Campania 'Luigi Vanvitelli', 80138 Naples, Italy.
Di Feo G; Department of Woman, Child and General and Specialist Surgery, University of Campania 'Luigi Vanvitelli', 80138 Naples, Italy.
Rana D; Department of Experimental Medicine, University of Campania 'Luigi Vanvitelli', 80138 Naples, Italy.
Ahmed S; Department of Experimental Medicine, University of Campania 'Luigi Vanvitelli', 80138 Naples, Italy.
Argenziano M; Department of Woman, Child and General and Specialist Surgery, University of Campania 'Luigi Vanvitelli', 80138 Naples, Italy.
Rossi F; Department of Woman, Child and General and Specialist Surgery, University of Campania 'Luigi Vanvitelli', 80138 Naples, Italy.
Roberti D; Department of Woman, Child and General and Specialist Surgery, University of Campania 'Luigi Vanvitelli', 80138 Naples, Italy.
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Źródło:
International journal of molecular sciences [Int J Mol Sci] 2024 Mar 01; Vol. 25 (5). Date of Electronic Publication: 2024 Mar 01.
Typ publikacji:
Journal Article; Review
MeSH Terms:
Hemoglobinopathies*/genetics
Anemia, Sickle Cell*/genetics
Thalassemia*
beta-Thalassemia*/genetics
Humans ; Bone Density ; Hemoglobin, Sickle
Czasopismo naukowe
Tytuł:
Reticulocyte Antioxidant Enzymes mRNA Levels versus Reticulocyte Maturity Indices in Hereditary Spherocytosis, β-Thalassemia and Sickle Cell Disease.
Autorzy:
Melo D; UCIBIO-Applied Molecular Biosciences Unit, Laboratory of Biochemistry, Department of Biological Sciences, Faculty of Pharmacy, University of Porto, 4051-401 Porto, Portugal.; Associate Laboratory i4HB-Institute for Health and Bioeconomy, Faculty of Pharmacy, University of Porto, 4051-401 Porto, Portugal.
Ferreira F; Hematology Service, Centro Hospitalar e Universitário de São João, 4051-401 Porto, Portugal.
Teles MJ; Clinical Pathology, Centro Hospitalar e Universitário de São João, 4051-401 Porto, Portugal.; Imuno-Hemotherapy Service, Centro Hospitalar Universitário de Santo António, 4051-401 Porto, Portugal.
Porto G; Imuno-Hemotherapy Service, Centro Hospitalar Universitário de Santo António, 4051-401 Porto, Portugal.; Center for Predictive and Preventive Genetics (CGPP)/Institute for Molecular and Cellular Biology (IBMC), 4051-401 Porto, Portugal.; Abel Salazar Institute of Biomedical Sciences (ICBAS), University of Porto, 4051-401 Porto, Portugal.
Coimbra S; UCIBIO-Applied Molecular Biosciences Unit, Laboratory of Biochemistry, Department of Biological Sciences, Faculty of Pharmacy, University of Porto, 4051-401 Porto, Portugal.; Associate Laboratory i4HB-Institute for Health and Bioeconomy, Faculty of Pharmacy, University of Porto, 4051-401 Porto, Portugal.; 1H-TOXRUN-One Health Toxicology Research Unit, University Institute of Health Sciences, CESPU, CRL, 4585-116 Gandra, Portugal.
Rocha S; UCIBIO-Applied Molecular Biosciences Unit, Laboratory of Biochemistry, Department of Biological Sciences, Faculty of Pharmacy, University of Porto, 4051-401 Porto, Portugal.; Associate Laboratory i4HB-Institute for Health and Bioeconomy, Faculty of Pharmacy, University of Porto, 4051-401 Porto, Portugal.
Santos-Silva A; UCIBIO-Applied Molecular Biosciences Unit, Laboratory of Biochemistry, Department of Biological Sciences, Faculty of Pharmacy, University of Porto, 4051-401 Porto, Portugal.; Associate Laboratory i4HB-Institute for Health and Bioeconomy, Faculty of Pharmacy, University of Porto, 4051-401 Porto, Portugal.
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Źródło:
International journal of molecular sciences [Int J Mol Sci] 2024 Feb 10; Vol. 25 (4). Date of Electronic Publication: 2024 Feb 10.
Typ publikacji:
Journal Article
MeSH Terms:
beta-Thalassemia*/genetics
Spherocytosis, Hereditary*/genetics
Anemia, Sickle Cell*/genetics
Humans ; Reticulocytes ; Antioxidants ; RNA, Messenger/genetics ; Superoxide Dismutase-1
Czasopismo naukowe
Tytuł:
Predictors of Developing a Complex Course of Osteomyelitis in Patients with Sickle Cell Anaemia.
Autorzy:
Hashmi AZA; College of Medicine, Sultan Qaboos University, Muscat, Oman.
Fazari EA; College of Medicine, Sultan Qaboos University, Muscat, Oman.
Ward MA; Department of Surgery, Sultan Qaboos University Hospital.
Masruri RA; College of Medicine, Sultan Qaboos University, Muscat, Oman.
Balushi SA; College of Medicine, Sultan Qaboos University, Muscat, Oman.
Mutani MA; Department of Surgery, Sultan Qaboos University Hospital.
Ghaithi AA; Department of Surgery, Sultan Qaboos University Hospital.
Baluki WA; Department of Surgery, Sultan Qaboos University Hospital.
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Źródło:
Sultan Qaboos University medical journal [Sultan Qaboos Univ Med J] 2024 Feb; Vol. 24 (1), pp. 58-62. Date of Electronic Publication: 2024 Feb 28.
Typ publikacji:
Journal Article
MeSH Terms:
Anemia, Sickle Cell*/complications
Bacteremia*
Osteomyelitis*
Humans ; Area Under Curve ; Lower Extremity
Czasopismo naukowe
Tytuł:
The value-based price of transformative gene therapy for sickle cell disease: a modeling analysis.
Autorzy:
Morgan G; Prime HCD, Mere House, Brook St, Knutsford, WA16 8GP, UK. .
Back E; Prime HCD, Mere House, Brook St, Knutsford, WA16 8GP, UK.
Besser M; Departments of Haematology, Addenbrooke's Hospital, Cambridge, UK.
Hallett TB; MRC Centre for Global Infectious Disease Analysis, Imperial College London, London, UK.
Guzauskas GF; Prime HCD, Mere House, Brook St, Knutsford, WA16 8GP, UK.; The Comparative Health Outcomes, Policy, and Economics Institute, University of Washington, Seattle, WA, USA.
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Źródło:
Scientific reports [Sci Rep] 2024 Feb 01; Vol. 14 (1), pp. 2739. Date of Electronic Publication: 2024 Feb 01.
Typ publikacji:
Journal Article
MeSH Terms:
Anemia, Sickle Cell*/genetics
Anemia, Sickle Cell*/therapy
Humans ; Disability-Adjusted Life Years ; Markov Chains ; Income ; Developing Countries ; Cost-Benefit Analysis
Czasopismo naukowe
Tytuł:
Brain network hypersensitivity underlies pain crises in sickle cell disease.
Autorzy:
Joo P; Department of Anesthesiology, Center for Consciousness Science, Center for the Study of Complex Systems, Michigan Psychedelic Center, University of Michigan, Arbor Lakes Building 1 Suite 2200, 4251 Plymouth Road, Ann Arbor, MI, 48105, USA.
Kim M; Department of Anesthesiology, Center for Consciousness Science, Center for the Study of Complex Systems, Michigan Psychedelic Center, University of Michigan, Arbor Lakes Building 1 Suite 2200, 4251 Plymouth Road, Ann Arbor, MI, 48105, USA.
Kish B; Weldon School of Biomedical Engineering, Purdue University, West Lafayette, IN, USA.
Nair VV; Weldon School of Biomedical Engineering, Purdue University, West Lafayette, IN, USA.
Tong Y; Weldon School of Biomedical Engineering, Purdue University, West Lafayette, IN, USA.
Liu Z; Indiana Center for Musculoskeletal Health, Indiana University, Indianapolis, IN, USA.; Department of Biostatistics, Indiana University School of Medicine, Indianapolis, IN, USA.
O'Brien ARW; Division of Hematology/Oncology, Department of Medicine, Indiana University School of Medicine, Indianapolis, IN, USA.
Harte SE; Department of Anesthesiology, Chronic Pain and Fatigue Research Center, University of Michigan, Ann Arbor, MI, USA.
Harris RE; Department of Anesthesiology, Chronic Pain and Fatigue Research Center, University of Michigan, Ann Arbor, MI, USA.; Susan Samueli Integrative Health Institute, and Department of Anesthesiology and Perioperative Care, School of Medicine, University of California at Irvine, Irvine, CA, USA.
Lee U; Department of Anesthesiology, Center for Consciousness Science, Center for the Study of Complex Systems, Michigan Psychedelic Center, University of Michigan, Arbor Lakes Building 1 Suite 2200, 4251 Plymouth Road, Ann Arbor, MI, 48105, USA. .
Wang Y; Division of Hematology/Oncology, Department of Medicine, Indiana University School of Medicine, Indianapolis, IN, USA. .; Department of Anesthesia, Stark Neurosciences Research Institute, Indiana University School of Medicine, Stark Neuroscience Building, Rm# 514E, 320 West 15th Street, Indianapolis, IN, 46202, USA. .
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Źródło:
Scientific reports [Sci Rep] 2024 Mar 27; Vol. 14 (1), pp. 7315. Date of Electronic Publication: 2024 Mar 27.
Typ publikacji:
Journal Article
MeSH Terms:
Pain*/etiology
Anemia, Sickle Cell*/complications
Humans ; Pain Management/adverse effects ; Brain
Czasopismo naukowe
Tytuł:
The RoxyScan is a novel measurement of red blood cell deformability under oxidative and shear stress.
Autorzy:
Larkin SK; Department of Pediatrics, University of California San Francisco, UCSF RBClab, 5700 MLK Jr. Way, Oakland, CA, 94609, USA. .
Hernández C; Department Central Diagnostic Laboratory - Research, University Medical Center Utrecht, Utrecht University, 3584 CX, Utrecht, The Netherlands.
van Beers EJ; Center for Benign Hematology, Thrombosis and Hemostasis - Van Creveldkliniek, University Medical Center Utrecht, Utrecht University, 3584 CX, Utrecht, The Netherlands.
van Wijk R; Department Central Diagnostic Laboratory - Research, University Medical Center Utrecht, Utrecht University, 3584 CX, Utrecht, The Netherlands.
Kuypers FA; Department of Pediatrics, University of California San Francisco, UCSF RBClab, 5700 MLK Jr. Way, Oakland, CA, 94609, USA.
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Źródło:
Scientific reports [Sci Rep] 2024 Mar 15; Vol. 14 (1), pp. 6344. Date of Electronic Publication: 2024 Mar 15.
Typ publikacji:
Journal Article
MeSH Terms:
Erythrocyte Deformability*
Anemia, Sickle Cell*
Humans ; Erythrocytes/metabolism ; Oxidative Stress ; Oxidation-Reduction
Czasopismo naukowe
Tytuł:
A Need for Daycare Unit for Sickle Cell Disease Patients in Oman.
Autorzy:
Al-Majarfi WK; Professional Development and Career Guidance Department, Ibri Hospital, Ibri, Oman.
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Źródło:
Sultan Qaboos University medical journal [Sultan Qaboos Univ Med J] 2024 Feb; Vol. 24 (1), pp. 4-6. Date of Electronic Publication: 2024 Feb 28.
Typ publikacji:
Editorial
MeSH Terms:
Anemia, Sickle Cell*/therapy
Humans ; Oman/epidemiology
Opinia redakcyjna
Tytuł:
Safety and efficacy of ketorolac continuous infusion for multimodal analgesia of vaso-occlusive crisis in patients with sickle cell disease.
Autorzy:
Pinto VM; EO Ospedali Galliera, Centro della Microcitemia, delle Anemie Congenite e dei Disordini del Metabolismo del Ferro, Genoa, Italy.
Gianesin B; EO Ospedali Galliera, Centro della Microcitemia, delle Anemie Congenite e dei Disordini del Metabolismo del Ferro, Genoa, Italy.; For Anemia Foundation, Genoa, Italy.
Sardo S; Department of Medical Science and Public Health, University of Cagliari, Cagliari, Italy.
Mazzi F; Department of Medicine, University of Verona and AOUI Verona, Verona, Italy.
Baiardi G; Department of Internal Medicine, Pharmacology & Toxicology Unit, University of Genoa, Genoa, Italy.; Clinical Pharmacology Unit, EO Ospedali Galliera, Genoa, Italy.
Menotti S; Department of Medicine, University of Verona and AOUI Verona, Verona, Italy.
Piras F; Department of Internal Medicine, Pharmacology & Toxicology Unit, University of Genoa, Genoa, Italy.
Quintino S; EO Ospedali Galliera, Centro della Microcitemia, delle Anemie Congenite e dei Disordini del Metabolismo del Ferro, Genoa, Italy.
Robello G; EO Ospedali Galliera, Centro della Microcitemia, delle Anemie Congenite e dei Disordini del Metabolismo del Ferro, Genoa, Italy.
Mattioli F; Department of Internal Medicine, Pharmacology & Toxicology Unit, University of Genoa, Genoa, Italy.; Clinical Pharmacology Unit, EO Ospedali Galliera, Genoa, Italy.
Finco G; Department of Medical Science and Public Health, University of Cagliari, Cagliari, Italy.
Forni GL; EO Ospedali Galliera, Centro della Microcitemia, delle Anemie Congenite e dei Disordini del Metabolismo del Ferro, Genoa, Italy. .
De Franceschi L; Department of Medicine, University of Verona and AOUI Verona, Verona, Italy.
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Źródło:
Orphanet journal of rare diseases [Orphanet J Rare Dis] 2024 Jan 22; Vol. 19 (1), pp. 22. Date of Electronic Publication: 2024 Jan 22.
Typ publikacji:
Letter
MeSH Terms:
Acute Pain*/drug therapy
Tramadol*
Anemia, Sickle Cell*/complications
Anemia, Sickle Cell*/drug therapy
Hemoglobinopathies*
Analgesia*
Adult ; Child ; Humans ; Ketorolac/therapeutic use
Opinia redakcyjna
Tytuł:
Prevalence of sickle cell trait and needs assessment for uptake of sickle cell screening among secondary school students in Kampala City, Uganda.
Autorzy:
Namukasa S; School of Nursing and Midwifery, Aga Khan University, Kampala, Uganda.
Maina R; School of Nursing and Midwifery, Aga Khan University, Nairobi, Kenya.
Nakaziba S; School of Nursing and Midwifery, Aga Khan University, Kampala, Uganda.
Among G; School of Nursing and Midwifery, Aga Khan University, Kampala, Uganda.
Asasira L; School of Nursing and Midwifery, Aga Khan University, Kampala, Uganda.
Mayambala P; Mengo Hospital Blood Bank, Kampala, Uganda.
Atukwatse J; School of Nursing and Midwifery, Aga Khan University, Kampala, Uganda.
Namuguzi M; School of Nursing and Midwifery, Aga Khan University, Kampala, Uganda.
Sarki AM; School of Nursing and Midwifery, Aga Khan University, Kampala, Uganda.; Family and Youth Health Initiative (FAYOHI), Duste, Jigawa State, Nigeria.
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Źródło:
PloS one [PLoS One] 2024 Jan 19; Vol. 19 (1), pp. e0296119. Date of Electronic Publication: 2024 Jan 19 (Print Publication: 2024).
Typ publikacji:
Journal Article
MeSH Terms:
Sickle Cell Trait*/diagnosis
Sickle Cell Trait*/epidemiology
Sickle Cell Trait*/genetics
Anemia, Sickle Cell*/diagnosis
Anemia, Sickle Cell*/epidemiology
Anemia, Sickle Cell*/genetics
Adolescent ; Humans ; Prevalence ; Uganda/epidemiology ; Cross-Sectional Studies ; Needs Assessment ; Schools ; Students
Czasopismo naukowe
Tytuł:
CHOICES for sickle cell reproductive health: A protocol of a randomized preconception intervention model for a single gene disorder.
Autorzy:
Wilkie DJ; College of Nursing, University of Florida, Gainesville, Florida, United States of America.
Telisnor G; College of Nursing, University of Florida, Gainesville, Florida, United States of America.
Powell-Roach K; College of Nursing, University of Tennessee Health Science Center, Memphis, Tennessee, United States of America.
Rangel AP; College of Nursing, University of Florida, Gainesville, Florida, United States of America.
Greenlee AL; College of Nursing, University of Florida, Gainesville, Florida, United States of America.
Ezenwa MO; College of Nursing, University of Florida, Gainesville, Florida, United States of America.
Gallo AM; College of Nursing, University of Florida, Gainesville, Florida, United States of America.
Black LV; College of Nursing, University of Florida, Gainesville, Florida, United States of America.
Gomes de Siqueira A; College of Engineering, University of Florida, Gainesville, Florida, United States of America.
Dyal BW; College of Nursing, University of Florida, Gainesville, Florida, United States of America.
Kalyanaraman S; College of Journalism and Communications, University of Florida, Gainesville, Florida, United States of America.
Yao Y; College of Nursing, University of Florida, Gainesville, Florida, United States of America.
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Źródło:
PloS one [PLoS One] 2023 Dec 07; Vol. 18 (12), pp. e0294907. Date of Electronic Publication: 2023 Dec 07 (Print Publication: 2023).
Typ publikacji:
Clinical Trial Protocol; Journal Article
MeSH Terms:
Anemia, Sickle Cell*/genetics
Sickle Cell Trait*/genetics
Child ; Humans ; Young Adult ; Reproduction ; Reproductive Health ; Research Design ; Randomized Controlled Trials as Topic
Czasopismo naukowe
Tytuł:
Newborn screening for sickle cell disease in Kisangani, Democratic Republic of the Congo: an update.
Autorzy:
Kasai ET; Department of Pediatrics, Faculty of Medicine and Pharmacy, University of Kisangani, Kisangani, Democratic Republic of the Congo.
Gulbis B; Department of Clinical Chemistry, Erasmus Hospital, Université Libre de Bruxelles, Brussels, Belgium.
Ntukamunda JK; Department of Pharmacy, Faculty of Medicine and Pharmacy, University of Kisangani, Kisangani, Democratic Republic of the Congo.
Bours V; Biochemical Genetics Laboratory, Human Genetics, CHU of Liège, University of Liège, Liège, Belgium.
Batina Agasa S; Department of Internal Medicine, Faculty of Medicine and Pharmacy, University of Kisangani, Kisangani, Democratic Republic of the Congo.
Marini Djang'eing'a R; Department of Clinical Chemistry, Erasmus Hospital, Université Libre de Bruxelles, Brussels, Belgium.; Laboratory of Analytical Pharmaceutical Chemistry, Faculty of Medicine, University of Liège, Liège, Belgium.
Boemer F; Biochemical Genetics Laboratory, Human Genetics, CHU of Liège, University of Liège, Liège, Belgium.
Katenga Bosunga G; Department of Obstetrics and Gynecology, Kisangani University Clinics, University of Kisangani, Kisangani, The Democratic Republic of the Congo.
Ngbonda Dauly N; Department of Pediatrics, Faculty of Medicine and Pharmacy, University of Kisangani, Kisangani, Democratic Republic of the Congo.
Sokoni Vutseme J; Department of Anthropology, Faculty of Social, Administrative and Political Sciences, University of Kisangani, Kisangani, Democratic Republic of the Congo.
Boso Mokili B; Faculty of Medicine and Pharmacy, University of Kisangani, Kisangani, Democratic Republic of the Congo.
Alworong'a Opara JP; Department of Pediatrics, Faculty of Medicine and Pharmacy, University of Kisangani, Kisangani, Democratic Republic of the Congo.
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Źródło:
Hematology (Amsterdam, Netherlands) [Hematology] 2023 Dec; Vol. 28 (1), pp. 2213043.
Typ publikacji:
Journal Article
MeSH Terms:
Neonatal Screening*
Anemia, Sickle Cell*/diagnosis
Anemia, Sickle Cell*/epidemiology
Anemia, Sickle Cell*/genetics
Infant ; Infant, Newborn ; Child ; Humans ; Democratic Republic of the Congo/epidemiology ; Hemoglobin, Sickle/genetics ; Point-of-Care Testing ; Hemoglobin A
Czasopismo naukowe
Tytuł:
An innovative intervention for the prevention of vaso-occlusive episodes in sickle cell disease.
Autorzy:
Jeon WJ; Department of Internal Medicine, School of Medicine, Loma Linda University, Loma Linda, CA, USA.
Joung B; Department of Internal Medicine, School of Medicine, Loma Linda University, Loma Linda, CA, USA.
Moon JH; Department of Internal Medicine, School of Medicine, Loma Linda University, Loma Linda, CA, USA.
Hino C; Department of Internal Medicine, School of Medicine, Loma Linda University, Loma Linda, CA, USA.
Park D; Department of Internal Medicine, School of Medicine, University of California San Francisco-Fresno, Fresno, CA, USA.
Pham B; Department of Internal Medicine, School of Medicine, University of California San Francisco-Fresno, Fresno, CA, USA.
Castillo DR; Division of Medical Oncology/ Hematology, Department of Internal Medicine, Loma Linda University Medical Center, Loma Linda, CA, USA.
Chong E; Division of Medical Oncology/ Hematology, Department of Internal Medicine, Loma Linda University Medical Center, Loma Linda, CA, USA.
Kaur S; Division of Medical Oncology/ Hematology, Department of Internal Medicine, Loma Linda University Medical Center, Loma Linda, CA, USA.
Grismore C; Director of Sickle Cell Servies, Loma Linda University Medical Center, Loma Linda, CA, USA.
Cao H; Division of Medical Oncology/ Hematology, Department of Internal Medicine, Loma Linda University Medical Center, Loma Linda, CA, USA.
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Źródło:
Hematology (Amsterdam, Netherlands) [Hematology] 2023 Dec; Vol. 28 (1), pp. 2215575.
Typ publikacji:
Journal Article
MeSH Terms:
Anemia, Sickle Cell*/complications
Anemia, Sickle Cell*/therapy
Humans ; Pain/etiology ; Pain/prevention & control ; Pain/drug therapy ; Hemoglobin, Sickle ; Pain Management/adverse effects ; Hydroxyurea/therapeutic use
Czasopismo naukowe

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